340 related articles for article (PubMed ID: 32776106)
1. Assembly of the [4Fe-4S] cluster of NFU1 requires the coordinated donation of two [2Fe-2S] clusters from the scaffold proteins, ISCU2 and ISCA1.
Jain A; Singh A; Maio N; Rouault TA
Hum Mol Genet; 2020 Nov; 29(19):3165-3182. PubMed ID: 32776106
[TBL] [Abstract][Full Text] [Related]
2. ISCA1 Orchestrates ISCA2 and NFU1 in the Maturation of Human Mitochondrial [4Fe-4S] Proteins.
Suraci D; Saudino G; Nasta V; Ciofi-Baffoni S; Banci L
J Mol Biol; 2021 May; 433(10):166924. PubMed ID: 33711344
[TBL] [Abstract][Full Text] [Related]
3. Structural Plasticity of NFU1 Upon Interaction with Binding Partners: Insights into the Mitochondrial [4Fe-4S] Cluster Pathway.
Da Vela S; Saudino G; Lucarelli F; Banci L; Svergun DI; Ciofi-Baffoni S
J Mol Biol; 2023 Aug; 435(15):168154. PubMed ID: 37211204
[TBL] [Abstract][Full Text] [Related]
4. A pathway for assembling [4Fe-4S]
Nasta V; Suraci D; Gourdoupis S; Ciofi-Baffoni S; Banci L
FEBS J; 2020 Jun; 287(11):2312-2327. PubMed ID: 31724821
[TBL] [Abstract][Full Text] [Related]
5. Mitochondrial [4Fe-4S] protein assembly involves reductive [2Fe-2S] cluster fusion on ISCA1-ISCA2 by electron flow from ferredoxin FDX2.
Weiler BD; Brück MC; Kothe I; Bill E; Lill R; Mühlenhoff U
Proc Natl Acad Sci U S A; 2020 Aug; 117(34):20555-20565. PubMed ID: 32817474
[TBL] [Abstract][Full Text] [Related]
6. A fatal mitochondrial disease is associated with defective NFU1 function in the maturation of a subset of mitochondrial Fe-S proteins.
Navarro-Sastre A; Tort F; Stehling O; Uzarska MA; Arranz JA; Del Toro M; Labayru MT; Landa J; Font A; Garcia-Villoria J; Merinero B; Ugarte M; Gutierrez-Solana LG; Campistol J; Garcia-Cazorla A; Vaquerizo J; Riudor E; Briones P; Elpeleg O; Ribes A; Lill R
Am J Hum Genet; 2011 Nov; 89(5):656-67. PubMed ID: 22077971
[TBL] [Abstract][Full Text] [Related]
7. The Human Iron-Sulfur Assembly Complex Catalyzes the Synthesis of [2Fe-2S] Clusters on ISCU2 That Can Be Transferred to Acceptor Molecules.
Fox NG; Chakrabarti M; McCormick SP; Lindahl PA; Barondeau DP
Biochemistry; 2015 Jun; 54(25):3871-9. PubMed ID: 26016389
[TBL] [Abstract][Full Text] [Related]
8. Formation of [4Fe-4S] clusters in the mitochondrial iron-sulfur cluster assembly machinery.
Brancaccio D; Gallo A; Mikolajczyk M; Zovo K; Palumaa P; Novellino E; Piccioli M; Ciofi-Baffoni S; Banci L
J Am Chem Soc; 2014 Nov; 136(46):16240-50. PubMed ID: 25347204
[TBL] [Abstract][Full Text] [Related]
9. BOLA3 and NFU1 link mitoribosome iron-sulfur cluster assembly to multiple mitochondrial dysfunctions syndrome.
Zhong H; Janer A; Khalimonchuk O; Antonicka H; Shoubridge EA; Barrientos A
Nucleic Acids Res; 2023 Nov; 51(21):11797-11812. PubMed ID: 37823603
[TBL] [Abstract][Full Text] [Related]
10. Understanding the molecular basis for multiple mitochondrial dysfunctions syndrome 1 (MMDS1): impact of a disease-causing Gly189Arg substitution on NFU1.
Wesley NA; Wachnowsky C; Fidai I; Cowan JA
FEBS J; 2017 Nov; 284(22):3838-3848. PubMed ID: 28906594
[TBL] [Abstract][Full Text] [Related]
11. ISCU interacts with NFU1, and ISCU[4Fe-4S] transfers its Fe-S cluster to NFU1 leading to the production of holo-NFU1.
Cai K; Frederick RO; Markley JL
J Struct Biol; 2020 May; 210(2):107491. PubMed ID: 32151725
[TBL] [Abstract][Full Text] [Related]
12. Analysis of NFU-1 metallocofactor binding-site substitutions-impacts on iron-sulfur cluster coordination and protein structure and function.
Wesley NA; Wachnowsky C; Fidai I; Cowan JA
FEBS J; 2017 Nov; 284(22):3817-3837. PubMed ID: 28906593
[TBL] [Abstract][Full Text] [Related]
13. Mechanisms of Mitochondrial Iron-Sulfur Protein Biogenesis.
Lill R; Freibert SA
Annu Rev Biochem; 2020 Jun; 89():471-499. PubMed ID: 31935115
[TBL] [Abstract][Full Text] [Related]
14. Molecular Basis of Rare Diseases Associated to the Maturation of Mitochondrial [4Fe-4S]-Containing Proteins.
Camponeschi F; Ciofi-Baffoni S; Calderone V; Banci L
Biomolecules; 2022 Jul; 12(7):. PubMed ID: 35883565
[TBL] [Abstract][Full Text] [Related]
15. Understanding the Molecular Basis of Multiple Mitochondrial Dysfunctions Syndrome 1 (MMDS1)-Impact of a Disease-Causing Gly208Cys Substitution on Structure and Activity of NFU1 in the Fe/S Cluster Biosynthetic Pathway.
Wachnowsky C; Wesley NA; Fidai I; Cowan JA
J Mol Biol; 2017 Mar; 429(6):790-807. PubMed ID: 28161430
[TBL] [Abstract][Full Text] [Related]
16. Role of Nfu1 and Bol3 in iron-sulfur cluster transfer to mitochondrial clients.
Melber A; Na U; Vashisht A; Weiler BD; Lill R; Wohlschlegel JA; Winge DR
Elife; 2016 Aug; 5():. PubMed ID: 27532773
[TBL] [Abstract][Full Text] [Related]
17. Structural/Functional Properties of Human NFU1, an Intermediate [4Fe-4S] Carrier in Human Mitochondrial Iron-Sulfur Cluster Biogenesis.
Cai K; Liu G; Frederick RO; Xiao R; Montelione GT; Markley JL
Structure; 2016 Dec; 24(12):2080-2091. PubMed ID: 27818104
[TBL] [Abstract][Full Text] [Related]
18. Impact of mutations within the [Fe-S] cluster or the lipoic acid biosynthesis pathways on mitochondrial protein expression profiles in fibroblasts from patients.
Lebigot E; Gaignard P; Dorboz I; Slama A; Rio M; de Lonlay P; Héron B; Sabourdy F; Boespflug-Tanguy O; Cardoso A; Habarou F; Ottolenghi C; Thérond P; Bouton C; Golinelli-Cohen MP; Boutron A
Mol Genet Metab; 2017 Nov; 122(3):85-94. PubMed ID: 28803783
[TBL] [Abstract][Full Text] [Related]
19. The plastidial
Roland M; Przybyla-Toscano J; Vignols F; Berger N; Azam T; Christ L; Santoni V; Wu HC; Dhalleine T; Johnson MK; Dubos C; Couturier J; Rouhier N
J Biol Chem; 2020 Feb; 295(6):1727-1742. PubMed ID: 31911438
[TBL] [Abstract][Full Text] [Related]
20. ISCA1 mutation in a patient with infantile-onset leukodystrophy causes defects in mitochondrial [4Fe-4S] proteins.
Torraco A; Stehling O; Stümpfig C; Rösser R; De Rasmo D; Fiermonte G; Verrigni D; Rizza T; Vozza A; Di Nottia M; Diodato D; Martinelli D; Piemonte F; Dionisi-Vici C; Bertini E; Lill R; Carrozzo R
Hum Mol Genet; 2018 Aug; 27(15):2739-2754. PubMed ID: 29767723
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
