These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
3. A case of carbamylphosphate synthetase-I deficiency associated with secondary carnitine deficiency--L-carnitine treatment of CPS-I deficiency. Mori T; Tsuchiyama A; Nagai K; Nagao M; Oyanagi K; Tsugawa S Eur J Pediatr; 1990 Jan; 149(4):272-4. PubMed ID: 2303075 [TBL] [Abstract][Full Text] [Related]
4. Hyperammonemia related to carnitine metabolism with particular emphasis on ornithine transcarbamylase deficiency. Matsuda I; Ohtani Y; Ohyanagi K; Yamamoto S Enzyme; 1987; 38(1-4):251-5. PubMed ID: 3440448 [TBL] [Abstract][Full Text] [Related]
5. Carnitine palmitoyltransferase 2 deficiency: the time-course of blood and urinary acylcarnitine levels during initial L-carnitine supplementation. Hori T; Fukao T; Kobayashi H; Teramoto T; Takayanagi M; Hasegawa Y; Yasuno T; Yamaguchi S; Kondo N Tohoku J Exp Med; 2010 Jul; 221(3):191-5. PubMed ID: 20543534 [TBL] [Abstract][Full Text] [Related]
6. Alteration of urinary carnitine profile induced by benzoate administration. Sakuma T Arch Dis Child; 1991 Jul; 66(7):873-5. PubMed ID: 1863104 [TBL] [Abstract][Full Text] [Related]
7. Characteristics of NO cycle coupling with urea cycle in non-hyperammonemic carriers of ornithine transcarbamylase deficiency. Nagasaka H; Yorifuji T; Egawa H; Inui A; Fujisawa T; Komatsu H; Tsukahara H; Uemoto S; Inomata Y Mol Genet Metab; 2013 Jul; 109(3):251-4. PubMed ID: 23669167 [TBL] [Abstract][Full Text] [Related]
8. Tissue acylcarnitine and acyl-coenzyme A profiles in chronically hyperammonemic mice treated with sodium benzoate and supplementary L-carnitine. Michalak A; Qureshi IA Biomed Pharmacother; 1995; 49(7-8):350-7. PubMed ID: 8562862 [TBL] [Abstract][Full Text] [Related]
9. Renal handling of carnitine in children with carnitine deficiency and hyperammonemia associated with valproate therapy. Matsuda I; Ohtani Y; Ninomiya N J Pediatr; 1986 Jul; 109(1):131-4. PubMed ID: 3088240 [TBL] [Abstract][Full Text] [Related]
10. Secondary carnitine deficiency in the newborn period in twins of a mother with partial ornithine transcarbamylase deficiency. Nagao M; Tsuchiyama A; Aoyama T; Mori T; Oyanagi K J Pediatr; 1989 Oct; 115(4):611-4. PubMed ID: 2795359 [No Abstract] [Full Text] [Related]
11. Renal handling of free and acylcarnitine in secondary carnitine deficiency. Ohtani Y; Nishiyama S; Matsuda I Neurology; 1984 Jul; 34(7):977-9. PubMed ID: 6539878 [TBL] [Abstract][Full Text] [Related]
12. Quantitation of urinary carnitine esters in a patient with medium-chain acyl-coenzyme A dehydrogenase deficiency: effect of metabolic state and L-carnitine therapy. Schmidt-Sommerfeld E; Penn D; Kerner J; Bieber LL; Rossi TM; Lebenthal E J Pediatr; 1989 Oct; 115(4):577-82. PubMed ID: 2795349 [TBL] [Abstract][Full Text] [Related]
13. Restoration of hepatic cytochrome c oxidase activity and expression with acetyl-L-carnitine treatment in spf mice with an ornithine transcarbamylase deficiency. Mawal YR; Rama Rao KV; Qureshi IA Biochem Pharmacol; 1998 Jun; 55(11):1853-60. PubMed ID: 9714304 [TBL] [Abstract][Full Text] [Related]
14. The role of orthotopic liver transplantation in the treatment of ornithine transcarbamylase deficiency. Busuttil AA; Goss JA; Seu P; Dulkanchainun TS; Yanni GS; McDiarmid SV; Busuttil RW Liver Transpl Surg; 1998 Sep; 4(5):350-4. PubMed ID: 9724471 [TBL] [Abstract][Full Text] [Related]
15. Propionylcarnitine excretion in propionic and methylmalonic acidurias: a cause of carnitine deficiency. Di Donato S; Rimoldi M; Garavaglia B; Uziel G Clin Chim Acta; 1984 May; 139(1):13-21. PubMed ID: 6723070 [TBL] [Abstract][Full Text] [Related]
16. Hyperammonemic coma due to parenteral nutrition in a woman with heterozygous ornithine transcarbamylase deficiency. Felig DM; Brusilow SW; Boyer JL Gastroenterology; 1995 Jul; 109(1):282-4. PubMed ID: 7797025 [TBL] [Abstract][Full Text] [Related]
17. Long-term treatment of girls with ornithine transcarbamylase deficiency. Maestri NE; Brusilow SW; Clissold DB; Bassett SS N Engl J Med; 1996 Sep; 335(12):855-9. PubMed ID: 8778603 [TBL] [Abstract][Full Text] [Related]
18. An unusual presentation of medium-chain acyl coenzyme A dehydrogenase deficiency. Marsden D; Sege-Petersen K; Nyhan WL; Roschinger W; Sweetman L Am J Dis Child; 1992 Dec; 146(12):1459-62. PubMed ID: 1456259 [TBL] [Abstract][Full Text] [Related]
19. Neonatal hyperammonemia associated with carnitine deficiency. Nagao M; Tsuchiyama A; Mori T; Agatsuma Y; Oyanagi K Tohoku J Exp Med; 1989 Aug; 158(4):317-23. PubMed ID: 2588261 [TBL] [Abstract][Full Text] [Related]
20. Ornithine transcarbamylase deficiency in females: an often overlooked cause of treatable encephalopathy. Pridmore CL; Clarke JT; Blaser S J Child Neurol; 1995 Sep; 10(5):369-74. PubMed ID: 7499756 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]