157 related articles for article (PubMed ID: 3349094)
1. The Zellweger syndrome: deficient chain-shortening of erucic acid (22:1 (n-9)) and adrenic acid (22:4 (n-6)) in cultured skin fibroblasts.
Christensen E; Hagve TA; Christophersen BO
Biochim Biophys Acta; 1988 Mar; 959(2):134-42. PubMed ID: 3349094
[TBL] [Abstract][Full Text] [Related]
2. Adrenoleukodystrophy. The chain shortening of erucic acid (22:1(n-9)) and adrenic acid (22:4(n-6)) is deficient in neonatal adrenoleukodystrophy and normal in X-linked adrenoleukodistrophy skin fibroblasts.
Christensen E; Grønn M; Hagve TA; Kase BF; Christophersen BO
Biochim Biophys Acta; 1989 Mar; 1002(1):79-83. PubMed ID: 2538146
[TBL] [Abstract][Full Text] [Related]
3. Peroxisomal beta-oxidation of polyunsaturated long chain fatty acids in human fibroblasts. The polyunsaturated and the saturated long chain fatty acids are retroconverted by the same acyl-CoA oxidase.
Christensen E; Woldseth B; Hagve TA; Poll-The BT; Wanders RJ; Sprecher H; Stokke O; Christophersen BO
Scand J Clin Lab Invest Suppl; 1993; 215():61-74. PubMed ID: 8327852
[TBL] [Abstract][Full Text] [Related]
4. Peroxisomal very long-chain fatty acid beta-oxidation in human skin fibroblasts: activity in Zellweger syndrome and other peroxisomal disorders.
Wanders RJ; van Roermund CW; van Wijland MJ; Heikoop J; Schutgens RB; Schram AW; Tager JM; van den Bosch H; Poll-Thé BT; Saudubray JM
Clin Chim Acta; 1987 Jul; 166(2-3):255-63. PubMed ID: 2441904
[TBL] [Abstract][Full Text] [Related]
5. Localization of nervonic acid beta-oxidation in human and rodent peroxisomes: impaired oxidation in Zellweger syndrome and X-linked adrenoleukodystrophy.
Sandhir R; Khan M; Chahal A; Singh I
J Lipid Res; 1998 Nov; 39(11):2161-71. PubMed ID: 9799802
[TBL] [Abstract][Full Text] [Related]
6. Regulation of the metabolism of polyunsaturated fatty acids.
Hagve TA; Christensen E; Grønn M; Christophersen BO
Scand J Clin Lab Invest Suppl; 1988; 191():33-46. PubMed ID: 3073521
[TBL] [Abstract][Full Text] [Related]
7. Chain-shortening of erucic acid and microperoxisomal beta-oxidation in rat small intestine.
Thomassen MS; Helgerud P; Norum KR
Biochem J; 1985 Jan; 225(2):301-6. PubMed ID: 3977835
[TBL] [Abstract][Full Text] [Related]
8. Fatty acid synthesis from [2-14C]acetate in normal and peroxisome-deficient (Zellweger) fibroblasts.
Poulos A; Usher S; Paton BC
Lipids; 1993 Feb; 28(2):97-102. PubMed ID: 8441343
[TBL] [Abstract][Full Text] [Related]
9. Peroxisomal fatty acid beta-oxidation in relation to the accumulation of very long chain fatty acids in cultured skin fibroblasts from patients with Zellweger syndrome and other peroxisomal disorders.
Wanders RJ; van Roermund CW; van Wijland MJ; Schutgens RB; Heikoop J; van den Bosch H; Schram AW; Tager JM
J Clin Invest; 1987 Dec; 80(6):1778-83. PubMed ID: 3680527
[TBL] [Abstract][Full Text] [Related]
10. Very long-chain fatty acids in peroxisomal disease.
Poulos A; Beckman K; Johnson DW; Paton BC; Robinson BS; Sharp P; Usher S; Singh H
Adv Exp Med Biol; 1992; 318():331-40. PubMed ID: 1378993
[TBL] [Abstract][Full Text] [Related]
11. The Zellweger syndrome: deficient conversion of docosahexaenoic acid (22:6(n-3)) to eicosapentaenoic acid (20:5(n-3)) and normal delta 4-desaturase activity in cultured skin fibroblasts.
Grønn M; Christensen E; Hagve TA; Christophersen BO
Biochim Biophys Acta; 1990 May; 1044(2):249-54. PubMed ID: 2140517
[TBL] [Abstract][Full Text] [Related]
12. Very-long-chain polyunsaturated fatty acids accumulate in phosphatidylcholine of fibroblasts from patients with Zellweger syndrome and acyl-CoA oxidase1 deficiency.
Abe Y; Honsho M; Nakanishi H; Taguchi R; Fujiki Y
Biochim Biophys Acta; 2014 Apr; 1841(4):610-9. PubMed ID: 24418004
[TBL] [Abstract][Full Text] [Related]
13. Evidence for peroxisomal retroconversion of adrenic acid (22:4(n-6)) and docosahexaenoic acids (22:6(n-3)) in isolated liver cells.
Hagve TA; Christophersen BO
Biochim Biophys Acta; 1986 Feb; 875(2):165-73. PubMed ID: 2935195
[TBL] [Abstract][Full Text] [Related]
14. Hydroxyeicosatetraenoic acid metabolism in cultured human skin fibroblasts. Evidence for peroxisomal beta-oxidation.
Gordon JA; Figard PH; Spector AA
J Clin Invest; 1990 Apr; 85(4):1173-81. PubMed ID: 2318972
[TBL] [Abstract][Full Text] [Related]
15. Formation of a novel arachidonic acid metabolite in peroxisomes.
Gordon JA; Heller SK; Rhead WJ; Watkins PA; Spector AA
Prostaglandins Leukot Essent Fatty Acids; 1995; 52(2-3):77-81. PubMed ID: 7540307
[TBL] [Abstract][Full Text] [Related]
16. Conversion of arachidonic acid to tetradecadienoic acid by peroxisomal oxidation.
Spector AA; Williard DE; Kaduce TL; Gordon JA
Prostaglandins Leukot Essent Fatty Acids; 1997 Jul; 57(1):101-5. PubMed ID: 9250615
[TBL] [Abstract][Full Text] [Related]
17. The cerebrohepatorenal (Zellweger) syndrome. Increased levels and impaired degradation of very-long-chain fatty acids and their use in prenatal diagnosis.
Moser AE; Singh I; Brown FR; Solish GI; Kelley RI; Benke PJ; Moser HW
N Engl J Med; 1984 May; 310(18):1141-6. PubMed ID: 6709009
[TBL] [Abstract][Full Text] [Related]
18. Peroxisomes contribute to the acylcarnitine production when the carnitine shuttle is deficient.
Violante S; Ijlst L; Te Brinke H; Koster J; Tavares de Almeida I; Wanders RJ; Ventura FV; Houten SM
Biochim Biophys Acta; 2013 Sep; 1831(9):1467-74. PubMed ID: 23850792
[TBL] [Abstract][Full Text] [Related]
19. Peroxisomal beta-oxidation of branched chain fatty acids in human skin fibroblasts.
Singh H; Brogan M; Johnson D; Poulos A
J Lipid Res; 1992 Nov; 33(11):1597-605. PubMed ID: 1464743
[TBL] [Abstract][Full Text] [Related]
20. A comparative study of straight chain and branched chain fatty acid oxidation in skin fibroblasts from patients with peroxisomal disorders.
Singh H; Usher S; Johnson D; Poulos A
J Lipid Res; 1990 Feb; 31(2):217-25. PubMed ID: 1691260
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]