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4. Peroxisomes contribute to the acylcarnitine production when the carnitine shuttle is deficient. Violante S; Ijlst L; Te Brinke H; Koster J; Tavares de Almeida I; Wanders RJ; Ventura FV; Houten SM Biochim Biophys Acta; 2013 Sep; 1831(9):1467-74. PubMed ID: 23850792 [TBL] [Abstract][Full Text] [Related]
5. Lipid storage myopathy, ichthyosis, and steatorrhea. Miranda A; DiMauro S; Eastwood A; Hays A; Johnson WG; Olarte M; Whitlock R; Mayeux R; Rowland LP Muscle Nerve; 1979; 2(1):1-13. PubMed ID: 545139 [TBL] [Abstract][Full Text] [Related]
6. Mitochondrial carnitine-acylcarnitine translocase deficiency presenting as sudden neonatal death. Chalmers RA; Stanley CA; English N; Wigglesworth JS J Pediatr; 1997 Aug; 131(2):220-5. PubMed ID: 9290607 [TBL] [Abstract][Full Text] [Related]
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8. Carnitine and carnitine palmitoyltransferase in fatty acid oxidation and ketosis. Hoppel CL Fed Proc; 1982 Oct; 41(12):2853-7. PubMed ID: 7128831 [TBL] [Abstract][Full Text] [Related]
9. Defects of fatty-acid oxidation in muscle. Angelini C Baillieres Clin Endocrinol Metab; 1990 Sep; 4(3):561-82. PubMed ID: 2268228 [TBL] [Abstract][Full Text] [Related]
10. [Alterations of mitochondria in metabolic diseases. Carnitine deficiency, carnitine palmitoyltransferase deficiency and beta oxidation]. Angelini C Acta Neurol (Napoli); 1989 Oct; 11(5):330-4. PubMed ID: 2603779 [TBL] [Abstract][Full Text] [Related]
11. Analysis of fatty acid oxidation intermediates in cultured fibroblasts to detect mitochondrial oxidation disorders. Pourfarzam M; Schaefer J; Turnbull DM; Bartlett K Clin Chem; 1994 Dec; 40(12):2267-75. PubMed ID: 7988014 [TBL] [Abstract][Full Text] [Related]
12. Effect of methylglyoxal bis(guanylhydrazone) on hepatic, heart and skeletal muscle mitochondrial carnitine palmitoyltransferase and beta-oxidation of fatty acids. Brady LJ; Brady PS; Gandour RD Biochem Pharmacol; 1987 Feb; 36(4):447-52. PubMed ID: 3827937 [TBL] [Abstract][Full Text] [Related]
13. Characterisation of carnitine palmitoyltransferases in patients with a carnitine palmitoyltransferase deficiency: implications for diagnosis and therapy. Schaefer J; Jackson S; Taroni F; Swift P; Turnbull DM J Neurol Neurosurg Psychiatry; 1997 Feb; 62(2):169-76. PubMed ID: 9048718 [TBL] [Abstract][Full Text] [Related]
14. Fatty acid beta-oxidation in peroxisomes and mitochondria: the first, unequivocal evidence for the involvement of carnitine in shuttling propionyl-CoA from peroxisomes to mitochondria. Jakobs BS; Wanders RJ Biochem Biophys Res Commun; 1995 Aug; 213(3):1035-41. PubMed ID: 7654220 [TBL] [Abstract][Full Text] [Related]
15. Paradoxical effects of clofibrate on liver and muscle metabolism in rats. Induction of myotonia and alteration of fatty acid and glucose oxidation. Paul HS; Adibi SA J Clin Invest; 1979 Aug; 64(2):405-12. PubMed ID: 457859 [TBL] [Abstract][Full Text] [Related]
16. Multisystem triglyceride storage disorder without ichthyosis in two siblings. Wessalowski R; Schroten H; Neuen-Jacob E; Reichmann H; Melnik BC; Lenard HG; Voit T Acta Paediatr; 1994 Jan; 83(1):93-8. PubMed ID: 8193482 [TBL] [Abstract][Full Text] [Related]
17. Carnitine-acylcarnitine translocase deficiency with severe hypoglycemia and auriculo ventricular block. Translocase assay in permeabilized fibroblasts. Pande SV; Brivet M; Slama A; Demaugre F; Aufrant C; Saudubray JM J Clin Invest; 1993 Mar; 91(3):1247-52. PubMed ID: 8450053 [TBL] [Abstract][Full Text] [Related]
18. Disorders of lipid metabolism in muscle. Di Mauro S; Trevisan C; Hays A Muscle Nerve; 1980; 3(5):369-88. PubMed ID: 7421873 [TBL] [Abstract][Full Text] [Related]
19. Analysis of carnitine esters by radio-high performance liquid chromatography in cultured skin fibroblasts from patients with mitochondrial fatty acid oxidation disorders. Schmidt-Sommerfeld E; Bobrowski PJ; Penn D; Rhead WJ; Wanders RJ; Bennett MJ Pediatr Res; 1998 Aug; 44(2):210-4. PubMed ID: 9702916 [TBL] [Abstract][Full Text] [Related]
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