These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
3. Nonsense pathogenic variants in exon 1 of PHOX2B lead to translational reinitiation in congenital central hypoventilation syndrome. Cain JT; Kim DI; Quast M; Shivega WG; Patrick RJ; Moser C; Reuter S; Perez M; Myers A; Weimer JM; Roux KJ; Landsverk M Am J Med Genet A; 2017 May; 173(5):1200-1207. PubMed ID: 28371199 [TBL] [Abstract][Full Text] [Related]
4. Congenital central hypoventilation syndrome: PHOX2B mutations and phenotype. Berry-Kravis EM; Zhou L; Rand CM; Weese-Mayer DE Am J Respir Crit Care Med; 2006 Nov; 174(10):1139-44. PubMed ID: 16888290 [TBL] [Abstract][Full Text] [Related]
5. Transcriptional dysregulation and impairment of PHOX2B auto-regulatory mechanism induced by polyalanine expansion mutations associated with congenital central hypoventilation syndrome. Di Lascio S; Bachetti T; Saba E; Ceccherini I; Benfante R; Fornasari D Neurobiol Dis; 2013 Feb; 50():187-200. PubMed ID: 23103552 [TBL] [Abstract][Full Text] [Related]
6. Causative and common PHOX2B variants define a broad phenotypic spectrum. Bachetti T; Ceccherini I Clin Genet; 2020 Jan; 97(1):103-113. PubMed ID: 31444792 [TBL] [Abstract][Full Text] [Related]
8. Expression of Ret-, p75(NTR)-, Phox2a-, Phox2b-, and tyrosine hydroxylase-immunoreactivity by undifferentiated neural crest-derived cells and different classes of enteric neurons in the embryonic mouse gut. Young HM; Ciampoli D; Hsuan J; Canty AJ Dev Dyn; 1999 Oct; 216(2):137-52. PubMed ID: 10536054 [TBL] [Abstract][Full Text] [Related]
9. Congenital central hypoventilation syndrome from past to future: model for translational and transitional autonomic medicine. Weese-Mayer DE; Rand CM; Berry-Kravis EM; Jennings LJ; Loghmanee DA; Patwari PP; Ceccherini I Pediatr Pulmonol; 2009 Jun; 44(6):521-35. PubMed ID: 19422034 [TBL] [Abstract][Full Text] [Related]
10. Germline mosaicism of PHOX2B mutation accounts for familial recurrence of congenital central hypoventilation syndrome (CCHS). Rand CM; Yu M; Jennings LJ; Panesar K; Berry-Kravis EM; Zhou L; Weese-Mayer DE Am J Med Genet A; 2012 Sep; 158A(9):2297-301. PubMed ID: 22821709 [TBL] [Abstract][Full Text] [Related]
11. Adult With Kasi AS; Kun SS; Keens TG; Perez IA J Clin Sleep Med; 2018 Dec; 14(12):2079-2081. PubMed ID: 30518452 [No Abstract] [Full Text] [Related]
12. Mutations that disrupt PHOXB interaction with the neuronal calcium sensor HPCAL1 impede cellular differentiation in neuroblastoma. Wang W; Zhong Q; Teng L; Bhatnagar N; Sharma B; Zhang X; Luther W; Haynes LP; Burgoyne RD; Vidal M; Volchenboum S; Hill DE; George RE Oncogene; 2014 Jun; 33(25):3316-24. PubMed ID: 23873030 [TBL] [Abstract][Full Text] [Related]
13. A respiratory/Hirschsprung phenotype in a three-generation family associated with a novel pathogenic PHOX2B splice donor mutation. Pace NP; Pace Bardon M; Borg I Mol Genet Genomic Med; 2020 Dec; 8(12):e1528. PubMed ID: 33047879 [TBL] [Abstract][Full Text] [Related]
14. Carbamazepine Improves Apneic Episodes in Congenital Central Hypoventilation Syndrome (CCHS) With a Novel Schirwani S; Pysden K; Chetcuti P; Blyth M J Clin Sleep Med; 2017 Nov; 13(11):1359-1362. PubMed ID: 28992836 [TBL] [Abstract][Full Text] [Related]
15. Organoid models of breathing disorders reveal patterning defect of hindbrain neurons caused by PHOX2B-PARMs. Lui KN; Li Z; Lai FP; Lau ST; Ngan ES Stem Cell Reports; 2023 Jul; 18(7):1500-1515. PubMed ID: 37352849 [TBL] [Abstract][Full Text] [Related]
16. Altered enteric expression of the homeobox transcription factor Phox2b in patients with diverticular disease. Cossais F; Lange C; Barrenschee M; Möding M; Ebsen M; Vogel I; Böttner M; Wedel T United European Gastroenterol J; 2019 Apr; 7(3):349-357. PubMed ID: 31019703 [TBL] [Abstract][Full Text] [Related]
17. Haploinsufficiency for Phox2b in mice causes dilated pupils and atrophy of the ciliary ganglion: mechanistic insights into human congenital central hypoventilation syndrome. Cross SH; Morgan JE; Pattyn A; West K; McKie L; Hart A; Thaung C; Brunet JF; Jackson IJ Hum Mol Genet; 2004 Jul; 13(14):1433-9. PubMed ID: 15150159 [TBL] [Abstract][Full Text] [Related]
18. Treatment of neuroblastoma in congenital central hypoventilation syndrome with a PHOX2B polyalanine repeat expansion mutation: New twist on a neurocristopathy syndrome. Armstrong AE; Weese-Mayer DE; Mian A; Maris JM; Batra V; Gosiengfiao Y; Reichek J; Madonna MB; Bush JW; Shore RM; Walterhouse DO Pediatr Blood Cancer; 2015 Nov; 62(11):2007-10. PubMed ID: 26011159 [TBL] [Abstract][Full Text] [Related]
19. Generation and characterization of iPSC lines (BGUi004-A, BGUi005-A) from two identical twins with polyalanine expansion in the paired-like homeobox 2B (PHOX2B) gene. Falik D; Rabinski T; Zlotnik D; Eshel R; Zorsky M; Garin-Shkolnik T; Ofir R; Adato A; Ashkenazi A; Vatine GD Stem Cell Res; 2020 Oct; 48():101955. PubMed ID: 32822965 [TBL] [Abstract][Full Text] [Related]
20. A Novel c.676_677insG Ye G; Han D; Jiang Y; Wang Z; Zhou Y; Lin X; Chen W; Chen M; Xu J; Yang Y; Guo Q J Clin Sleep Med; 2019 Mar; 15(3):509-513. PubMed ID: 30853048 [No Abstract] [Full Text] [Related] [Next] [New Search]