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2. Molecular analysis of T-B-NK+ severe combined immunodeficiency and Omenn syndrome cases in Saudi Arabia. Alsmadi O; Al-Ghonaium A; Al-Muhsen S; Arnaout R; Al-Dhekri H; Al-Saud B; Al-Kayal F; Al-Saud H; Al-Mousa H BMC Med Genet; 2009 Nov; 10():116. PubMed ID: 19912631 [TBL] [Abstract][Full Text] [Related]
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4. Whole-exome sequencing identified a homozygous novel Wang W; Wang J; Wang J; Liu J; Pei J; Li W; Wang Y; Banerjee S; Xu R; Meng Z; Yi B Allergol Immunopathol (Madr); 2022; 50(6):32-46. PubMed ID: 36335443 [TBL] [Abstract][Full Text] [Related]
5. Characterization of immune function and analysis of RAG gene mutations in Omenn syndrome and related disorders. Wada T; Takei K; Kudo M; Shimura S; Kasahara Y; Koizumi S; Kawa-Ha K; Ishida Y; Imashuku S; Seki H; Yachie A Clin Exp Immunol; 2000 Jan; 119(1):148-55. PubMed ID: 10606976 [TBL] [Abstract][Full Text] [Related]
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9. Identical mutations in RAG1 or RAG2 genes leading to defective V(D)J recombinase activity can cause either T-B-severe combined immune deficiency or Omenn syndrome. Corneo B; Moshous D; Güngör T; Wulffraat N; Philippet P; Le Deist FL; Fischer A; de Villartay JP Blood; 2001 May; 97(9):2772-6. PubMed ID: 11313270 [TBL] [Abstract][Full Text] [Related]
10. Omenn Syndrome due to RAG1 Mutation Presenting With Nonimmune Hydrops Fetalis in Two Siblings. Valeri L; Lugli L; Iughetti L; Soresina A; Giliani S; Porta F; Berardi A Pediatrics; 2022 Jan; 149(1):. PubMed ID: 34889447 [TBL] [Abstract][Full Text] [Related]
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20. Oligoclonal expansion of T lymphocytes with multiple second-site mutations leads to Omenn syndrome in a patient with RAG1-deficient severe combined immunodeficiency. Wada T; Toma T; Okamoto H; Kasahara Y; Koizumi S; Agematsu K; Kimura H; Shimada A; Hayashi Y; Kato M; Yachie A Blood; 2005 Sep; 106(6):2099-101. PubMed ID: 15845893 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]