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3. LONP1 Is Required for Maturation of a Subset of Mitochondrial Proteins, and Its Loss Elicits an Integrated Stress Response. Zurita Rendón O; Shoubridge EA Mol Cell Biol; 2018 Oct; 38(20):. PubMed ID: 30061372 [TBL] [Abstract][Full Text] [Related]
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5. CODAS syndrome is associated with mutations of LONP1, encoding mitochondrial AAA+ Lon protease. Strauss KA; Jinks RN; Puffenberger EG; Venkatesh S; Singh K; Cheng I; Mikita N; Thilagavathi J; Lee J; Sarafianos S; Benkert A; Koehler A; Zhu A; Trovillion V; McGlincy M; Morlet T; Deardorff M; Innes AM; Prasad C; Chudley AE; Lee IN; Suzuki CK Am J Hum Genet; 2015 Jan; 96(1):121-35. PubMed ID: 25574826 [TBL] [Abstract][Full Text] [Related]
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9. Proteomic analysis demonstrates the role of the quality control protease LONP1 in mitochondrial protein aggregation. Pollecker K; Sylvester M; Voos W J Biol Chem; 2021 Oct; 297(4):101134. PubMed ID: 34461102 [TBL] [Abstract][Full Text] [Related]
11. Structure-Based Design of Selective LONP1 Inhibitors for Probing Kingsley LJ; He X; McNeill M; Nelson J; Nikulin V; Ma Z; Lu W; Zhou VW; Manuia M; Kreusch A; Gao MY; Witmer D; Vaillancourt MT; Lu M; Greenblatt S; Lee C; Vashisht A; Bender S; Spraggon G; Michellys PY; Jia Y; Haling JR; Lelais G J Med Chem; 2021 Apr; 64(8):4857-4869. PubMed ID: 33821636 [TBL] [Abstract][Full Text] [Related]
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13. Mitochondrial Lon protease is a gatekeeper for proteins newly imported into the matrix. Matsushima Y; Takahashi K; Yue S; Fujiyoshi Y; Yoshioka H; Aihara M; Setoyama D; Uchiumi T; Fukuchi S; Kang D Commun Biol; 2021 Aug; 4(1):974. PubMed ID: 34400774 [TBL] [Abstract][Full Text] [Related]
14. Cell stress management by the mitochondrial LonP1 protease - Insights into mitigating developmental, oncogenic and cardiac stress. Venkatesh S; Suzuki CK Mitochondrion; 2020 Mar; 51():46-61. PubMed ID: 31756517 [TBL] [Abstract][Full Text] [Related]
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18. Structural Basis for the Magnesium-Dependent Activation and Hexamerization of the Lon AAA+ Protease. Su SC; Lin CC; Tai HC; Chang MY; Ho MR; Babu CS; Liao JH; Wu SH; Chang YC; Lim C; Chang CI Structure; 2016 May; 24(5):676-686. PubMed ID: 27041593 [TBL] [Abstract][Full Text] [Related]
19. Chronic hyperglycemia impairs mitochondrial unfolded protein response and precipitates proteotoxicity in experimental diabetic neuropathy: focus on LonP1 mediated mitochondrial regulation. Kalvala AK; Yerra VG; Sherkhane B; Gundu C; Arruri V; Kumar R; Kumar A Pharmacol Rep; 2020 Dec; 72(6):1627-1644. PubMed ID: 32720218 [TBL] [Abstract][Full Text] [Related]
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