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6. TMPyP4 porphyrin distorts RNA G-quadruplex structures of the disease-associated r(GGGGCC)n repeat of the C9orf72 gene and blocks interaction of RNA-binding proteins. Zamiri B; Reddy K; Macgregor RB; Pearson CE J Biol Chem; 2014 Feb; 289(8):4653-9. PubMed ID: 24371143 [TBL] [Abstract][Full Text] [Related]
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11. Relax, Don't RAN Translate It. Wilson KM; Muralidharan B; Isaacs AM Neuron; 2019 Dec; 104(5):827-829. PubMed ID: 31805259 [TBL] [Abstract][Full Text] [Related]
12. The porphyrin TMPyP4 inhibits elongation during the noncanonical translation of the FTLD/ALS-associated GGGGCC repeat in the C9orf72 gene. Mori K; Gotoh S; Yamashita T; Uozumi R; Kawabe Y; Tagami S; Kamp F; Nuscher B; Edbauer D; Haass C; Nagai Y; Ikeda M J Biol Chem; 2021 Oct; 297(4):101120. PubMed ID: 34450161 [TBL] [Abstract][Full Text] [Related]
13. Reduced autophagy upon C9ORF72 loss synergizes with dipeptide repeat protein toxicity in G4C2 repeat expansion disorders. Boivin M; Pfister V; Gaucherot A; Ruffenach F; Negroni L; Sellier C; Charlet-Berguerand N EMBO J; 2020 Feb; 39(4):e100574. PubMed ID: 31930538 [TBL] [Abstract][Full Text] [Related]
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17. The disease-associated r(GGGGCC)n repeat from the C9orf72 gene forms tract length-dependent uni- and multimolecular RNA G-quadruplex structures. Reddy K; Zamiri B; Stanley SYR; Macgregor RB; Pearson CE J Biol Chem; 2013 Apr; 288(14):9860-9866. PubMed ID: 23423380 [TBL] [Abstract][Full Text] [Related]
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