233 related articles for article (PubMed ID: 34199295)
1.
Lee JH; Lin SY; Liu JW; Lin SZ; Harn HJ; Chiou TW
Int J Mol Sci; 2021 Jun; 22(12):. PubMed ID: 34199295
[TBL] [Abstract][Full Text] [Related]
2. n-Butylidenephthalide exhibits protection against neurotoxicity through regulation of tryptophan 2, 3 dioxygenase in spinocerebellar ataxia type 3.
Rajamani K; Liu JW; Wu CH; Chiang IT; You DH; Lin SY; Hsieh DK; Lin SZ; Harn HJ; Chiou TW
Neuropharmacology; 2017 May; 117():434-446. PubMed ID: 28223212
[TBL] [Abstract][Full Text] [Related]
3. Anti-Excitotoxic Effects of N-Butylidenephthalide Revealed by Chemically Insulted Purkinje Progenitor Cells Derived from SCA3 iPSCs.
Yang HH; Chiang IT; Liu JW; Hsieh J; Lee JH; Lu HE; Tso HS; Deng YC; Kao JC; Wu JR; Harn HJ; Chiou TW
Int J Mol Sci; 2022 Jan; 23(3):. PubMed ID: 35163312
[TBL] [Abstract][Full Text] [Related]
4. Far-infrared Radiation Improves Motor Dysfunction and Neuropathology in Spinocerebellar Ataxia Type 3 Mice.
Liu SW; Chang JC; Chuang SF; Liu KH; Cheng WL; Chang HJ; Chang HS; Lin TT; Hsieh CL; Lin WY; Hsieh M; Kuo SJ; Liu CS
Cerebellum; 2019 Feb; 18(1):22-32. PubMed ID: 29725949
[TBL] [Abstract][Full Text] [Related]
5. Oligonucleotide therapy mitigates disease in spinocerebellar ataxia type 3 mice.
McLoughlin HS; Moore LR; Chopra R; Komlo R; McKenzie M; Blumenstein KG; Zhao H; Kordasiewicz HB; Shakkottai VG; Paulson HL
Ann Neurol; 2018 Jul; 84(1):64-77. PubMed ID: 29908063
[TBL] [Abstract][Full Text] [Related]
6. Inactivation of PNKP by mutant ATXN3 triggers apoptosis by activating the DNA damage-response pathway in SCA3.
Gao R; Liu Y; Silva-Fernandes A; Fang X; Paulucci-Holthauzen A; Chatterjee A; Zhang HL; Matsuura T; Choudhary S; Ashizawa T; Koeppen AH; Maciel P; Hazra TK; Sarkar PS
PLoS Genet; 2015 Jan; 11(1):e1004834. PubMed ID: 25590633
[TBL] [Abstract][Full Text] [Related]
7. Treatment with sodium butyrate induces autophagy resulting in therapeutic benefits for spinocerebellar ataxia type 3.
Watchon M; Robinson KJ; Luu L; An Y; Yuan KC; Plenderleith SK; Cheng F; Don EK; Nicholson GA; Lee A; Laird AS
FASEB J; 2024 Jan; 38(2):e23429. PubMed ID: 38258931
[TBL] [Abstract][Full Text] [Related]
8. Growth hormone rescue cerebellar degeneration in SCA3 transgenic mice.
Wu S; Liu K; Cheng W; Su S; Lin Y; Lin T; Cheng Y; Chang J; Wu Y; Liu C
Biochem Biophys Res Commun; 2020 Aug; 529(2):467-473. PubMed ID: 32703453
[TBL] [Abstract][Full Text] [Related]
9. Combined therapy with m-TOR-dependent and -independent autophagy inducers causes neurotoxicity in a mouse model of Machado-Joseph disease.
Duarte-Silva S; Silva-Fernandes A; Neves-Carvalho A; Soares-Cunha C; Teixeira-Castro A; Maciel P
Neuroscience; 2016 Jan; 313():162-73. PubMed ID: 26601773
[TBL] [Abstract][Full Text] [Related]
10. T1-11 and JMF1907 ameliorate polyglutamine-expanded ataxin-3-induced neurodegeneration, transcriptional dysregulation and ataxic symptom in the SCA3 transgenic mouse.
Chou AH; Chen YL; Chiu CC; Yuan SJ; Weng YH; Yeh TH; Lin YL; Fang JM; Wang HL
Neuropharmacology; 2015 Dec; 99():308-17. PubMed ID: 26254860
[TBL] [Abstract][Full Text] [Related]
11. Neurodegenerative phosphoprotein signaling landscape in models of SCA3.
Sowa AS; Popova TG; Harmuth T; Weber JJ; Pereira Sena P; Schmidt J; Hübener-Schmid J; Schmidt T
Mol Brain; 2021 Mar; 14(1):57. PubMed ID: 33741019
[TBL] [Abstract][Full Text] [Related]
12. Pharmacological enhancement of retinoid-related orphan receptor α function mitigates spinocerebellar ataxia type 3 pathology.
Watanave M; Hoshino C; Konno A; Fukuzaki Y; Matsuzaki Y; Ishitani T; Hirai H
Neurobiol Dis; 2019 Jan; 121():263-273. PubMed ID: 30343032
[TBL] [Abstract][Full Text] [Related]
13. Antisense Oligonucleotide Therapy Targeted Against ATXN3 Improves Potassium Channel-Mediated Purkinje Neuron Dysfunction in Spinocerebellar Ataxia Type 3.
Bushart DD; Zalon AJ; Zhang H; Morrison LM; Guan Y; Paulson HL; Shakkottai VG; McLoughlin HS
Cerebellum; 2021 Feb; 20(1):41-53. PubMed ID: 32789747
[TBL] [Abstract][Full Text] [Related]
14. In vivo assessment of riluzole as a potential therapeutic drug for spinocerebellar ataxia type 3.
Schmidt J; Schmidt T; Golla M; Lehmann L; Weber JJ; Hübener-Schmid J; Riess O
J Neurochem; 2016 Jul; 138(1):150-62. PubMed ID: 26990650
[TBL] [Abstract][Full Text] [Related]
15. Caffeic acid and resveratrol ameliorate cellular damage in cell and Drosophila models of spinocerebellar ataxia type 3 through upregulation of Nrf2 pathway.
Wu YL; Chang JC; Lin WY; Li CC; Hsieh M; Chen HW; Wang TS; Wu WT; Liu CS; Liu KL
Free Radic Biol Med; 2018 Feb; 115():309-317. PubMed ID: 29247688
[TBL] [Abstract][Full Text] [Related]
16. A fine balance between Prpf19 and Exoc7 in achieving degradation of aggregated protein and suppression of cell death in spinocerebellar ataxia type 3.
Chen ZS; Huang X; Talbot K; Chan HYE
Cell Death Dis; 2021 Feb; 12(2):136. PubMed ID: 33542212
[TBL] [Abstract][Full Text] [Related]
17. Autophagy Function and Benefits of Autophagy Induction in Models of Spinocerebellar Ataxia Type 3.
Watchon M; Luu L; Plenderleith SK; Yuan KC; Laird AS
Cells; 2023 Mar; 12(6):. PubMed ID: 36980234
[TBL] [Abstract][Full Text] [Related]
18. Silencing mutant ATXN3 expression resolves molecular phenotypes in SCA3 transgenic mice.
Rodríguez-Lebrón E; Costa Mdo C; Luna-Cancalon K; Peron TM; Fischer S; Boudreau RL; Davidson BL; Paulson HL
Mol Ther; 2013 Oct; 21(10):1909-18. PubMed ID: 23820820
[TBL] [Abstract][Full Text] [Related]
19. Druggable genome screen identifies new regulators of the abundance and toxicity of ATXN3, the Spinocerebellar Ataxia type 3 disease protein.
Ashraf NS; Sutton JR; Yang Y; Ranxhi B; Libohova K; Shaw ED; Barget AJ; Todi SV; Paulson HL; Costa MDC
Neurobiol Dis; 2020 Apr; 137():104697. PubMed ID: 31783119
[TBL] [Abstract][Full Text] [Related]
20. Flow cytometry allows rapid detection of protein aggregates in cellular and zebrafish models of spinocerebellar ataxia 3.
Robinson KJ; Tym MC; Hogan A; Watchon M; Yuan KC; Plenderleith SK; Don EK; Laird AS
Dis Model Mech; 2021 Oct; 14(10):. PubMed ID: 34473252
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
