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9. Quantitative Lipid Profiling Reveals Major Differences between Liver Organoids with Normal Pi*M and Deficient Pi*Z Variants of Alpha-1-antitrypsin. Pérez-Luz S; Lalchandani J; Matamala N; Barrero MJ; Gil-Martín S; Saz SR; Varona S; Monzón S; Cuesta I; Justo I; Marcacuzco A; Hierro L; Garfia C; Gomez-Mariano G; Janciauskiene S; Martínez-Delgado B Int J Mol Sci; 2023 Aug; 24(15):. PubMed ID: 37569847 [TBL] [Abstract][Full Text] [Related]
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12. Storage of alpha-1-antitrypsin in intrahepatic bile duct cells in alpha-1-antitrypsin deficiency (Pi Z phenotype). Callea F; Fevery J; Massi G; de Groote J; Desmet VJ Histopathology; 1985 Jan; 9(1):99-108. PubMed ID: 2984102 [TBL] [Abstract][Full Text] [Related]
13. The Mechanism of Mitochondrial Injury in Alpha-1 Antitrypsin Deficiency Mediated Liver Disease. Khodayari N; Wang RL; Oshins R; Lu Y; Millett M; Aranyos AM; Mostofizadeh S; Scindia Y; Flagg TO; Brantly M Int J Mol Sci; 2021 Dec; 22(24):. PubMed ID: 34948056 [TBL] [Abstract][Full Text] [Related]
14. The Autophagy Pathway: A Critical Route in the Disposal of Alpha 1-Antitrypsin Aggregates That Holds Many Mysteries. Leon C; Bouchecareilh M Int J Mol Sci; 2021 Feb; 22(4):. PubMed ID: 33668611 [TBL] [Abstract][Full Text] [Related]
16. Elevated synthesis of human alpha 1-antitrypsin hinders the secretion of murine alpha 1-antitrypsin from hepatocytes of transgenic mice. Sifers RN; Rogers BB; Hawkins HK; Finegold MJ; Woo SL J Biol Chem; 1989 Sep; 264(26):15696-700. PubMed ID: 2788654 [TBL] [Abstract][Full Text] [Related]
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19. Liver disease in alpha-1 antitrypsin deficiency: current understanding and future therapy. Teckman JH COPD; 2013 Mar; 10 Suppl 1():35-43. PubMed ID: 23527737 [TBL] [Abstract][Full Text] [Related]
20. Autophagic disposal of the aggregation-prone protein that causes liver inflammation and carcinogenesis in alpha-1-antitrypsin deficiency. Perlmutter DH Cell Death Differ; 2009 Jan; 16(1):39-45. PubMed ID: 18617899 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]