These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
25. FUS-immunoreactive inclusions are a common feature in sporadic and non-SOD1 familial amyotrophic lateral sclerosis. Deng HX; Zhai H; Bigio EH; Yan J; Fecto F; Ajroud K; Mishra M; Ajroud-Driss S; Heller S; Sufit R; Siddique N; Mugnaini E; Siddique T Ann Neurol; 2010 Jun; 67(6):739-48. PubMed ID: 20517935 [TBL] [Abstract][Full Text] [Related]
26. The Redox Activity of Protein Disulfide Isomerase Inhibits ALS Phenotypes in Cellular and Zebrafish Models. Parakh S; Shadfar S; Perri ER; Ragagnin AMG; Piattoni CV; Fogolín MB; Yuan KC; Shahheydari H; Don EK; Thomas CJ; Hong Y; Comini MA; Laird AS; Spencer DM; Atkin JD iScience; 2020 May; 23(5):101097. PubMed ID: 32446203 [TBL] [Abstract][Full Text] [Related]
27. Extensive splicing changes in an ALS/FTD transgenic mouse model overexpressing cytoplasmic fused in sarcoma. Ito D; Taguchi R; Deguchi M; Ogasawara H; Inoue E Sci Rep; 2020 Mar; 10(1):4857. PubMed ID: 32184412 [TBL] [Abstract][Full Text] [Related]
28. Dendritic Homeostasis Disruption in a Novel Frontotemporal Dementia Mouse Model Expressing Cytoplasmic Fused in Sarcoma. Shiihashi G; Ito D; Arai I; Kobayashi Y; Hayashi K; Otsuka S; Nakajima K; Yuzaki M; Itohara S; Suzuki N EBioMedicine; 2017 Oct; 24():102-115. PubMed ID: 28928015 [TBL] [Abstract][Full Text] [Related]
29. Protein disulfide isomerase in ALS mouse glia links protein misfolding with NADPH oxidase-catalyzed superoxide production. Jaronen M; Vehviläinen P; Malm T; Keksa-Goldsteine V; Pollari E; Valonen P; Koistinaho J; Goldsteins G Hum Mol Genet; 2013 Feb; 22(4):646-55. PubMed ID: 23118353 [TBL] [Abstract][Full Text] [Related]
30. Trichostatin A Relieves Growth Suppression and Restores Histone Acetylation at Specific Sites in a FUS ALS/FTD Yeast Model. Bennett SA; Cobos SN; Mirzakandova M; Fallah M; Son E; Angelakakis G; Rana N; Hugais M; Torrente MP Biochemistry; 2021 Dec; 60(48):3671-3675. PubMed ID: 34788013 [TBL] [Abstract][Full Text] [Related]
31. Targeting RACK1 to alleviate TDP-43 and FUS proteinopathy-mediated suppression of protein translation and neurodegeneration. Zhao B; Cowan CM; Coutts JA; Christy DD; Saraph A; Hsueh SCC; Plotkin SS; Mackenzie IR; Kaplan JM; Cashman NR Acta Neuropathol Commun; 2023 Dec; 11(1):200. PubMed ID: 38111057 [TBL] [Abstract][Full Text] [Related]
32. ALS/FTD-associated FUS activates GSK-3β to disrupt the VAPB-PTPIP51 interaction and ER-mitochondria associations. Stoica R; Paillusson S; Gomez-Suaga P; Mitchell JC; Lau DH; Gray EH; Sancho RM; Vizcay-Barrena G; De Vos KJ; Shaw CE; Hanger DP; Noble W; Miller CC EMBO Rep; 2016 Sep; 17(9):1326-42. PubMed ID: 27418313 [TBL] [Abstract][Full Text] [Related]
33. Mechanisms of FUS mutations in familial amyotrophic lateral sclerosis. Shang Y; Huang EJ Brain Res; 2016 Sep; 1647():65-78. PubMed ID: 27033831 [TBL] [Abstract][Full Text] [Related]
34. Amyotrophic lateral sclerosis-linked UBQLN2 mutants inhibit endoplasmic reticulum to Golgi transport, leading to Golgi fragmentation and ER stress. Halloran M; Ragagnin AMG; Vidal M; Parakh S; Yang S; Heng B; Grima N; Shahheydari H; Soo KY; Blair I; Guillemin GJ; Sundaramoorthy V; Atkin JD Cell Mol Life Sci; 2020 Oct; 77(19):3859-3873. PubMed ID: 31802140 [TBL] [Abstract][Full Text] [Related]
35. Lysine acetylation regulates the RNA binding, subcellular localization and inclusion formation of FUS. Arenas A; Chen J; Kuang L; Barnett KR; Kasarskis EJ; Gal J; Zhu H Hum Mol Genet; 2020 Sep; 29(16):2684-2697. PubMed ID: 32691043 [TBL] [Abstract][Full Text] [Related]
36. Mutation of the ALS-/FTD-Associated RNA-Binding Protein FUS Affects Axonal Development. van Tartwijk FW; Wunderlich LCS; Mela I; Makarchuk S; Jakobs MAH; Qamar S; Franze K; Kaminski Schierle GS; St George-Hyslop PH; Lin JQ; Holt CE; Kaminski CF J Neurosci; 2024 Jul; 44(27):. PubMed ID: 38692734 [TBL] [Abstract][Full Text] [Related]
37. Potential effect of S-nitrosylated protein disulfide isomerase on mutant SOD1 aggregation and neuronal cell death in amyotrophic lateral sclerosis. Jeon GS; Nakamura T; Lee JS; Choi WJ; Ahn SW; Lee KW; Sung JJ; Lipton SA Mol Neurobiol; 2014 Apr; 49(2):796-807. PubMed ID: 24091828 [TBL] [Abstract][Full Text] [Related]
38. ALS/FTD-associated mutation in cyclin F inhibits ER-Golgi trafficking, inducing ER stress, ERAD and Golgi fragmentation. Ragagnin AMG; Sundaramoorthy V; Farzana F; Gautam S; Saravanabavan S; Takalloo Z; Mehta P; Do-Ha D; Parakh S; Shadfar S; Hunter J; Vidal M; Jagaraj CJ; Brocardo M; Konopka A; Yang S; Rayner SL; Williams KL; Blair IP; Chung RS; Lee A; Ooi L; Atkin JD Sci Rep; 2023 Nov; 13(1):20467. PubMed ID: 37993492 [TBL] [Abstract][Full Text] [Related]
39. Stepwise acquirement of hallmark neuropathology in FUS-ALS iPSC models depends on mutation type and neuronal aging. Japtok J; Lojewski X; Naumann M; Klingenstein M; Reinhardt P; Sterneckert J; Putz S; Demestre M; Boeckers TM; Ludolph AC; Liebau S; Storch A; Hermann A Neurobiol Dis; 2015 Oct; 82():420-429. PubMed ID: 26253605 [TBL] [Abstract][Full Text] [Related]
40. Molecular pathology and genetic advances in amyotrophic lateral sclerosis: an emerging molecular pathway and the significance of glial pathology. Ince PG; Highley JR; Kirby J; Wharton SB; Takahashi H; Strong MJ; Shaw PJ Acta Neuropathol; 2011 Dec; 122(6):657-71. PubMed ID: 22105541 [TBL] [Abstract][Full Text] [Related] [Previous] [Next] [New Search]