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2. Cystine accumulation and clearance in normal and cystinotic fibroblasts exposed to cystine dimethyl ester. Steinherz R; Makov N; Narinsky R; Meidan B; Kohn G Clin Chim Acta; 1984 Aug; 141(2-3):119-25. PubMed ID: 6488551 [TBL] [Abstract][Full Text] [Related]
3. Comparative study of cystine clearance in cystinotic and I-cell fibroblasts upon exposure to cystine dimethyl ester. Steinherz R; Makov N; Narinsky R; Meidan B; Kohn G Enzyme; 1984; 32(2):126-30. PubMed ID: 6499825 [TBL] [Abstract][Full Text] [Related]
4. Cystine dimethylester model of cystinosis: still reliable? Wilmer MJ; Willems PH; Verkaart S; Visch HJ; de Graaf-Hess A; Blom HJ; Monnens LA; van den Heuvel LP; Levtchenko EN Pediatr Res; 2007 Aug; 62(2):151-5. PubMed ID: 17597653 [TBL] [Abstract][Full Text] [Related]
5. Cystine accumulation and loss in normal, heterozygous, and cystinotic fibroblasts. Jonas AJ; Greene AA; Smith ML; Schneider JA Proc Natl Acad Sci U S A; 1982 Jul; 79(14):4442-5. PubMed ID: 6956872 [TBL] [Abstract][Full Text] [Related]
6. Impaired clearance of free cystine from lysosome-enriched granular fractions of I-cell-disease fibroblasts. Tietze F; Rome LH; Butler JD; Harper GS; Gahl WA Biochem J; 1986 Jul; 237(1):9-15. PubMed ID: 3800891 [TBL] [Abstract][Full Text] [Related]
7. Lysosomal cystine transport in cystinosis variants and their parents. Gahl WA; Tietze F Pediatr Res; 1987 Feb; 21(2):193-6. PubMed ID: 3822600 [TBL] [Abstract][Full Text] [Related]
8. Cystine accumulation and clearance by normal and cystinotic leukocytes exposed to cystine dimethyl ester. Steinherz R; Tietze F; Gahl WA; Triche TJ; Chiang H; Modesti A; Schulman JD Proc Natl Acad Sci U S A; 1982 Jul; 79(14):4446-50. PubMed ID: 6956873 [TBL] [Abstract][Full Text] [Related]
9. Uptake and utilization of exogenous cystine by cystinotic and normal fibroblasts. States B; Harris D; Segal S J Clin Invest; 1974 Apr; 53(4):1003-16. PubMed ID: 4815074 [TBL] [Abstract][Full Text] [Related]
10. Heterozygote detection in cystinosis, using leukocytes exposed to cystine dimethyl ester. Steinherz R; Tietze F; Triche T; Modesti A; Gahl WA; Schulman JD N Engl J Med; 1982 Jun; 306(24):1468-70. PubMed ID: 7078591 [No Abstract] [Full Text] [Related]
11. Description of a selection method highly cytotoxic for cystinotic fibroblasts but not normal human fibroblasts. Pisoni RL; Lemons RM; Paelicke KM; Thoene JG Somat Cell Mol Genet; 1992 Jan; 18(1):1-6. PubMed ID: 1546366 [TBL] [Abstract][Full Text] [Related]
12. Lysosomal cystine storage in cystinosis and mucolipidosis type II. Greene AA; Jonas AJ; Harms E; Smith ML; Pellett OL; Bump EA; Miller AL; Schneider JA Pediatr Res; 1985 Nov; 19(11):1170-4. PubMed ID: 4069825 [TBL] [Abstract][Full Text] [Related]
13. Utilization of mercaptoethylgluconamide for depleting human cystinotic fibroblasts of their accumulated lysosomal cystine. Pisoni RL; Lisowski KM; Lemons RM; Thoene JG Pediatr Res; 1989 Jul; 26(1):73-6. PubMed ID: 2771512 [TBL] [Abstract][Full Text] [Related]
14. Lysosomal cystine storage augments apoptosis in cultured human fibroblasts and renal tubular epithelial cells. Park M; Helip-Wooley A; Thoene J J Am Soc Nephrol; 2002 Dec; 13(12):2878-87. PubMed ID: 12444206 [TBL] [Abstract][Full Text] [Related]
15. Cystine accumulation in cystinotic fibroblasts from free and protein-linked cystine but not cysteine. Thoene JG; Lemons RM Biochem J; 1982 Dec; 208(3):823-30. PubMed ID: 6762213 [TBL] [Abstract][Full Text] [Related]
16. Transport of L-cystine by cultivated skin fibroblasts of normal subjects and patients with cystinosis. Kaye CI; Nadler HL Pediatr Res; 1976 Jul; 10(7):637-41. PubMed ID: 934729 [TBL] [Abstract][Full Text] [Related]
17. Altered status of glutathione and its metabolites in cystinotic cells. Levtchenko E; de Graaf-Hess A; Wilmer M; van den Heuvel L; Monnens L; Blom H Nephrol Dial Transplant; 2005 Sep; 20(9):1828-32. PubMed ID: 15956064 [TBL] [Abstract][Full Text] [Related]
18. Handling of L-[35S]cystine by cysteamine-pretreated cystinotic and normal fibroblasts. States B; Lee J; Segal S Arch Biochem Biophys; 1983 Feb; 220(2):361-9. PubMed ID: 6824329 [TBL] [Abstract][Full Text] [Related]
19. The effect of chloroquine on the metabolism of [35S]cystine in normal and cystinotic human skin fibroblasts. Danpure CJ Biochem J; 1981 Dec; 200(3):555-63. PubMed ID: 7342970 [TBL] [Abstract][Full Text] [Related]