248 related articles for article (PubMed ID: 34573100)
1. Signaling Overlap between the Golgi Stress Response and Cysteine Metabolism in Huntington's Disease.
Paul BD
Antioxidants (Basel); 2021 Sep; 10(9):. PubMed ID: 34573100
[TBL] [Abstract][Full Text] [Related]
2. Cysteine metabolism and hydrogen sulfide signaling in Huntington's disease.
Paul BD
Free Radic Biol Med; 2022 Jun; 186():93-98. PubMed ID: 35550919
[TBL] [Abstract][Full Text] [Related]
3. Golgi stress response reprograms cysteine metabolism to confer cytoprotection in Huntington's disease.
Sbodio JI; Snyder SH; Paul BD
Proc Natl Acad Sci U S A; 2018 Jan; 115(4):780-785. PubMed ID: 29317536
[TBL] [Abstract][Full Text] [Related]
4. Mutant Huntingtin Derails Cysteine Metabolism in Huntington's Disease at Both Transcriptional and Post-Translational Levels.
Paul BD; Sbodio JI; Snyder SH
Antioxidants (Basel); 2022 Jul; 11(8):. PubMed ID: 36009188
[TBL] [Abstract][Full Text] [Related]
5. Small molecule modulator of protein disulfide isomerase attenuates mutant huntingtin toxicity and inhibits endoplasmic reticulum stress in a mouse model of Huntington's disease.
Zhou X; Li G; Kaplan A; Gaschler MM; Zhang X; Hou Z; Jiang M; Zott R; Cremers S; Stockwell BR; Duan W
Hum Mol Genet; 2018 May; 27(9):1545-1555. PubMed ID: 29462355
[TBL] [Abstract][Full Text] [Related]
6. Endoplasmic reticulum stress: The cause and solution to Huntington's disease?
Jiang Y; Chadwick SR; Lajoie P
Brain Res; 2016 Oct; 1648(Pt B):650-657. PubMed ID: 27040914
[TBL] [Abstract][Full Text] [Related]
7. Impaired Redox Signaling in Huntington's Disease: Therapeutic Implications.
Paul BD; Snyder SH
Front Mol Neurosci; 2019; 12():68. PubMed ID: 30941013
[TBL] [Abstract][Full Text] [Related]
8. Converging pathways in the occurrence of endoplasmic reticulum (ER) stress in Huntington's disease.
Vidal R; Caballero B; Couve A; Hetz C
Curr Mol Med; 2011 Feb; 11(1):1-12. PubMed ID: 21189122
[TBL] [Abstract][Full Text] [Related]
9. IRE1 plays an essential role in ER stress-mediated aggregation of mutant huntingtin via the inhibition of autophagy flux.
Lee H; Noh JY; Oh Y; Kim Y; Chang JW; Chung CW; Lee ST; Kim M; Ryu H; Jung YK
Hum Mol Genet; 2012 Jan; 21(1):101-14. PubMed ID: 21954231
[TBL] [Abstract][Full Text] [Related]
10. Cystathionine γ-lyase deficiency mediates neurodegeneration in Huntington's disease.
Paul BD; Sbodio JI; Xu R; Vandiver MS; Cha JY; Snowman AM; Snyder SH
Nature; 2014 May; 509(7498):96-100. PubMed ID: 24670645
[TBL] [Abstract][Full Text] [Related]
11. Inhibition of endoplasmic reticulum stress counteracts neuronal cell death and protein aggregation caused by N-terminal mutant huntingtin proteins.
Reijonen S; Putkonen N; Nørremølle A; Lindholm D; Korhonen L
Exp Cell Res; 2008 Mar; 314(5):950-60. PubMed ID: 18255062
[TBL] [Abstract][Full Text] [Related]
12. AAV-mediated delivery of the transcription factor XBP1s into the striatum reduces mutant Huntingtin aggregation in a mouse model of Huntington's disease.
Zuleta A; Vidal RL; Armentano D; Parsons G; Hetz C
Biochem Biophys Res Commun; 2012 Apr; 420(3):558-63. PubMed ID: 22445760
[TBL] [Abstract][Full Text] [Related]
13. Towards a comprehensive understanding of the contributions of mitochondrial dysfunction and oxidative stress in the pathogenesis and pathophysiology of Huntington's disease.
Tobore TO
J Neurosci Res; 2019 Nov; 97(11):1455-1468. PubMed ID: 31304621
[TBL] [Abstract][Full Text] [Related]
14. Nucleocytoplasmic trafficking and transcription effects of huntingtin in Huntington's disease.
Truant R; Atwal RS; Burtnik A
Prog Neurobiol; 2007 Nov; 83(4):211-27. PubMed ID: 17240517
[TBL] [Abstract][Full Text] [Related]
15. Herp Promotes Degradation of Mutant Huntingtin: Involvement of the Proteasome and Molecular Chaperones.
Luo H; Cao L; Liang X; Du A; Peng T; Li H
Mol Neurobiol; 2018 Oct; 55(10):7652-7668. PubMed ID: 29430620
[TBL] [Abstract][Full Text] [Related]
16. Transcriptional control of amino acid homeostasis is disrupted in Huntington's disease.
Sbodio JI; Snyder SH; Paul BD
Proc Natl Acad Sci U S A; 2016 Aug; 113(31):8843-8. PubMed ID: 27436896
[TBL] [Abstract][Full Text] [Related]
17. Huntingtin is required for ER-to-Golgi transport and for secretory vesicle fusion at the plasma membrane.
Brandstaetter H; Kruppa AJ; Buss F
Dis Model Mech; 2014 Dec; 7(12):1335-40. PubMed ID: 25368120
[TBL] [Abstract][Full Text] [Related]
18. Downregulation of glial genes involved in synaptic function mitigates Huntington's disease pathogenesis.
Onur TS; Laitman A; Zhao H; Keyho R; Kim H; Wang J; Mair M; Wang H; Li L; Perez A; de Haro M; Wan YW; Allen G; Lu B; Al-Ramahi I; Liu Z; Botas J
Elife; 2021 Apr; 10():. PubMed ID: 33871358
[TBL] [Abstract][Full Text] [Related]
19. Increased Steady-State Mutant Huntingtin mRNA in Huntington's Disease Brain.
Liu W; Chaurette J; Pfister EL; Kennington LA; Chase KO; Bullock J; Vonsattel JP; Faull RL; Macdonald D; DiFiglia M; Zamore PD; Aronin N
J Huntingtons Dis; 2013; 2(4):491-500. PubMed ID: 25062733
[TBL] [Abstract][Full Text] [Related]
20. Loss-of-Huntingtin in Medial and Lateral Ganglionic Lineages Differentially Disrupts Regional Interneuron and Projection Neuron Subtypes and Promotes Huntington's Disease-Associated Behavioral, Cellular, and Pathological Hallmarks.
Mehler MF; Petronglo JR; Arteaga-Bracho EE; Gulinello ME; Winchester ML; Pichamoorthy N; Young SK; DeJesus CD; Ishtiaq H; Gokhan S; Molero AE
J Neurosci; 2019 Mar; 39(10):1892-1909. PubMed ID: 30626701
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]