247 related articles for article (PubMed ID: 35468843)
1. Duchenne muscular dystrophy trajectory in R-DMDdel52 preclinical rat model identifies COMP as biomarker of fibrosis.
Taglietti V; Kefi K; Bronisz-Budzyńska I; Mirciloglu B; Rodrigues M; Cardone N; Coulpier F; Periou B; Gentil C; Goddard M; Authier FJ; Pietri-Rouxel F; Malfatti E; Lafuste P; Tiret L; Relaix F
Acta Neuropathol Commun; 2022 Apr; 10(1):60. PubMed ID: 35468843
[TBL] [Abstract][Full Text] [Related]
2. Long-Term Protective Effect of Human Dystrophin Expressing Chimeric (DEC) Cell Therapy on Amelioration of Function of Cardiac, Respiratory and Skeletal Muscles in Duchenne Muscular Dystrophy.
Siemionow M; Langa P; Brodowska S; Kozlowska K; Zalants K; Budzynska K; Heydemann A
Stem Cell Rev Rep; 2022 Dec; 18(8):2872-2892. PubMed ID: 35590083
[TBL] [Abstract][Full Text] [Related]
3. Human dystrophin expressing chimeric (DEC) cell therapy ameliorates cardiac, respiratory, and skeletal muscle's function in Duchenne muscular dystrophy.
Siemionow M; Langa P; Harasymczuk M; Cwykiel J; Sielewicz M; Smieszek J; Heydemann A
Stem Cells Transl Med; 2021 Oct; 10(10):1406-1418. PubMed ID: 34291884
[TBL] [Abstract][Full Text] [Related]
4. Receptor interacting protein kinase-3 mediates both myopathy and cardiomyopathy in preclinical animal models of Duchenne muscular dystrophy.
Bencze M; Periou B; Punzón I; Barthélémy I; Taglietti V; Hou C; Zaidan L; Kefi K; Blot S; Agbulut O; Gervais M; Derumeaux G; Authier FJ; Tiret L; Relaix F
J Cachexia Sarcopenia Muscle; 2023 Dec; 14(6):2520-2531. PubMed ID: 37909859
[TBL] [Abstract][Full Text] [Related]
5. Sildenafil reduces respiratory muscle weakness and fibrosis in the mdx mouse model of Duchenne muscular dystrophy.
Percival JM; Whitehead NP; Adams ME; Adamo CM; Beavo JA; Froehner SC
J Pathol; 2012 Sep; 228(1):77-87. PubMed ID: 22653783
[TBL] [Abstract][Full Text] [Related]
6. Long-Term Biodistribution and Safety of Human Dystrophin Expressing Chimeric Cell Therapy After Systemic-Intraosseous Administration to Duchenne Muscular Dystrophy Model.
Siemionow M; Brodowska S; Langa P; Zalants K; Kozlowska K; Grau-Kazmierczak W; Heydemann A
Arch Immunol Ther Exp (Warsz); 2022 Aug; 70(1):20. PubMed ID: 35978142
[TBL] [Abstract][Full Text] [Related]
7. Pharmacological Inhibition of PKCθ Counteracts Muscle Disease in a Mouse Model of Duchenne Muscular Dystrophy.
Marrocco V; Fiore P; Benedetti A; Pisu S; Rizzuto E; Musarò A; Madaro L; Lozanoska-Ochser B; Bouché M
EBioMedicine; 2017 Feb; 16():150-161. PubMed ID: 28089792
[TBL] [Abstract][Full Text] [Related]
8. Dose-Escalation Study of Systemically Delivered rAAVrh74.MHCK7.micro-dystrophin in the
Potter RA; Griffin DA; Heller KN; Peterson EL; Clark EK; Mendell JR; Rodino-Klapac LR
Hum Gene Ther; 2021 Apr; 32(7-8):375-389. PubMed ID: 33397205
[TBL] [Abstract][Full Text] [Related]
9. Label-free 3D characterization of cardiac fibrosis in muscular dystrophy using SHG imaging of cleared tissue.
Pichon J; Ledevin M; Larcher T; Jamme F; Rouger K; Dubreil L
Biol Cell; 2022 Mar; 114(3):91-103. PubMed ID: 34964145
[TBL] [Abstract][Full Text] [Related]
10. Xanthine oxidase is hyper-active in Duchenne muscular dystrophy.
Lindsay A; McCourt PM; Karachunski P; Lowe DA; Ervasti JM
Free Radic Biol Med; 2018 Dec; 129():364-371. PubMed ID: 30312761
[TBL] [Abstract][Full Text] [Related]
11. Validation of ultrasonography for non-invasive assessment of diaphragm function in muscular dystrophy.
Whitehead NP; Bible KL; Kim MJ; Odom GL; Adams ME; Froehner SC
J Physiol; 2016 Dec; 594(24):7215-7227. PubMed ID: 27570057
[TBL] [Abstract][Full Text] [Related]
12. Cardiac Protection after Systemic Transplant of Dystrophin Expressing Chimeric (DEC) Cells to the mdx Mouse Model of Duchenne Muscular Dystrophy.
Siemionow M; Malik M; Langa P; Cwykiel J; Brodowska S; Heydemann A
Stem Cell Rev Rep; 2019 Dec; 15(6):827-841. PubMed ID: 31612351
[TBL] [Abstract][Full Text] [Related]
13. The D2.mdx mouse as a preclinical model of the skeletal muscle pathology associated with Duchenne muscular dystrophy.
Hammers DW; Hart CC; Matheny MK; Wright LA; Armellini M; Barton ER; Sweeney HL
Sci Rep; 2020 Aug; 10(1):14070. PubMed ID: 32826942
[TBL] [Abstract][Full Text] [Related]
14. P2RX7 purinoceptor: a therapeutic target for ameliorating the symptoms of duchenne muscular dystrophy.
Sinadinos A; Young CN; Al-Khalidi R; Teti A; Kalinski P; Mohamad S; Floriot L; Henry T; Tozzi G; Jiang T; Wurtz O; Lefebvre A; Shugay M; Tong J; Vaudry D; Arkle S; doRego JC; Górecki DC
PLoS Med; 2015 Oct; 12(10):e1001888. PubMed ID: 26461208
[TBL] [Abstract][Full Text] [Related]
15. Antisense Oligonucleotide Treatment in a Humanized Mouse Model of Duchenne Muscular Dystrophy and Highly Sensitive Detection of Dystrophin Using Western Blotting.
Maruyama R; Yokota T
Methods Mol Biol; 2021; 2224():203-214. PubMed ID: 33606217
[TBL] [Abstract][Full Text] [Related]
16. Microdystrophin Gene Addition Significantly Improves Muscle Functionality and Diaphragm Muscle Histopathology in a Fibrotic Mouse Model of Duchenne Muscular Dystrophy.
Cernisova V; Lu-Nguyen N; Trundle J; Herath S; Malerba A; Popplewell L
Int J Mol Sci; 2023 May; 24(9):. PubMed ID: 37175881
[TBL] [Abstract][Full Text] [Related]
17. Therapeutic Exon Skipping Through a CRISPR-Guided Cytidine Deaminase Rescues Dystrophic Cardiomyopathy in Vivo.
Li J; Wang K; Zhang Y; Qi T; Yuan J; Zhang L; Qiu H; Wang J; Yang HT; Dai Y; Song Y; Chang X
Circulation; 2021 Nov; 144(22):1760-1776. PubMed ID: 34698513
[TBL] [Abstract][Full Text] [Related]
18. The BALB/c.mdx62 mouse exhibits a dystrophic muscle pathology and is a model of Duchenne muscular dystrophy.
Swiderski K; Chan AS; Herold MJ; Kueh AJ; Chung JD; Hardee JP; Trieu J; Chee A; Naim T; Gregorevic P; Lynch GS
Dis Model Mech; 2024 Apr; 17(4):. PubMed ID: 38602028
[TBL] [Abstract][Full Text] [Related]
19. A novel rabbit model of Duchenne muscular dystrophy generated by CRISPR/Cas9.
Sui T; Lau YS; Liu D; Liu T; Xu L; Gao Y; Lai L; Li Z; Han R
Dis Model Mech; 2018 Jun; 11(6):. PubMed ID: 29871865
[TBL] [Abstract][Full Text] [Related]
20. Alterations in Notch signalling in skeletal muscles from mdx and dko dystrophic mice and patients with Duchenne muscular dystrophy.
Church JE; Trieu J; Chee A; Naim T; Gehrig SM; Lamon S; Angelini C; Russell AP; Lynch GS
Exp Physiol; 2014 Apr; 99(4):675-87. PubMed ID: 24443351
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
