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4. Analysis of Enzyme Activity and Cellular Function for the N80S and S480F Asparagine Synthetase Variants Expressed in a Child with Asparagine Synthetase Deficiency. Staklinski SJ; Snanoudj S; Guerrot AM; Vanhulle C; Lecoquierre F; Bekri S; Kilberg MS Int J Mol Sci; 2022 Dec; 24(1):. PubMed ID: 36613999 [TBL] [Abstract][Full Text] [Related]
5. Characterization of a novel variant in siblings with Asparagine Synthetase Deficiency. Sacharow SJ; Dudenhausen EE; Lomelino CL; Rodan L; El Achkar CM; Olson HE; Genetti CA; Agrawal PB; McKenna R; Kilberg MS Mol Genet Metab; 2018 Mar; 123(3):317-325. PubMed ID: 29279279 [TBL] [Abstract][Full Text] [Related]
6. An intractable epilepsy phenotype of ASNS novel mutation in two patients with asparagine synthetase deficiency. Liu L; Wang J; Li H; Dong Y; Li Y; Xia L; Yang B; Wang H; Xu Y; Cheng G; Du K; Zhang X; Zhu C; Cui S; Ren C Clin Chim Acta; 2022 Jun; 531():331-336. PubMed ID: 35469797 [TBL] [Abstract][Full Text] [Related]
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9. In vitro functional analysis of four variants of human asparagine synthetase. Matsumoto H; Kawashima N; Yamamoto T; Nakama M; Otsuka H; Ago Y; Sasai H; Kubota K; Ozeki M; Kawamoto N; Esaka Y; Ohnishi H J Inherit Metab Dis; 2021 Sep; 44(5):1226-1234. PubMed ID: 34080208 [TBL] [Abstract][Full Text] [Related]
10. Asparagine Synthetase Deficiency causes reduced proliferation of cells under conditions of limited asparagine. Palmer EE; Hayner J; Sachdev R; Cardamone M; Kandula T; Morris P; Dias KR; Tao J; Miller D; Zhu Y; Macintosh R; Dinger ME; Cowley MJ; Buckley MF; Roscioli T; Bye A; Kilberg MS; Kirk EP Mol Genet Metab; 2015 Nov; 116(3):178-86. PubMed ID: 26318253 [TBL] [Abstract][Full Text] [Related]
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12. Asparagine synthetase deficiency detected by whole exome sequencing causes congenital microcephaly, epileptic encephalopathy and psychomotor delay. Ben-Salem S; Gleeson JG; Al-Shamsi AM; Islam B; Hertecant J; Ali BR; Al-Gazali L Metab Brain Dis; 2015 Jun; 30(3):687-94. PubMed ID: 25227173 [TBL] [Abstract][Full Text] [Related]
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17. A novel variant in ASNS gene responsible for syndromic intellectual disability and microcephaly: Case report and literature review. Jahanpanah M; Mokhtari D; Mokaber H; Arish S; Ahmadabadi F; Davarnia B Mol Genet Genomic Med; 2024 Apr; 12(4):e2424. PubMed ID: 38546112 [TBL] [Abstract][Full Text] [Related]
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