223 related articles for article (PubMed ID: 36103513)
21. Proximity proteomics of C9orf72 dipeptide repeat proteins identifies molecular chaperones as modifiers of poly-GA aggregation.
Liu F; Morderer D; Wren MC; Vettleson-Trutza SA; Wang Y; Rabichow BE; Salemi MR; Phinney BS; Oskarsson B; Dickson DW; Rossoll W
Acta Neuropathol Commun; 2022 Feb; 10(1):22. PubMed ID: 35164882
[TBL] [Abstract][Full Text] [Related]
22. Downregulation of Hsp90 and the antimicrobial peptide Mtk suppresses poly(GR)-induced neurotoxicity in C9ORF72-ALS/FTD.
Lee S; Jun YW; Linares GR; Butler B; Yuva-Adyemir Y; Moore J; Krishnan G; Ruiz-Juarez B; Santana M; Pons M; Silverman N; Weng Z; Ichida JK; Gao FB
Neuron; 2023 May; 111(9):1381-1390.e6. PubMed ID: 36931278
[TBL] [Abstract][Full Text] [Related]
23. Poly-GP in cerebrospinal fluid links
Lehmer C; Oeckl P; Weishaupt JH; Volk AE; Diehl-Schmid J; Schroeter ML; Lauer M; Kornhuber J; Levin J; Fassbender K; Landwehrmeyer B; ; Schludi MH; Arzberger T; Kremmer E; Flatley A; Feederle R; Steinacker P; Weydt P; Ludolph AC; Edbauer D; Otto M
EMBO Mol Med; 2017 Jul; 9(7):859-868. PubMed ID: 28408402
[TBL] [Abstract][Full Text] [Related]
24. Translation of dipeptide repeat proteins in
Sonobe Y; Lee S; Krishnan G; Gu Y; Kwon DY; Gao FB; Roos RP; Kratsios P
Elife; 2023 Sep; 12():. PubMed ID: 37675986
[TBL] [Abstract][Full Text] [Related]
25. C9orf72 arginine-rich dipeptide repeats inhibit UPF1-mediated RNA decay via translational repression.
Sun Y; Eshov A; Zhou J; Isiktas AU; Guo JU
Nat Commun; 2020 Jul; 11(1):3354. PubMed ID: 32620797
[TBL] [Abstract][Full Text] [Related]
26. Inflammasome-Mediated Neuronal-Microglial Crosstalk: a Therapeutic Substrate for the Familial C9orf72 Variant of Frontotemporal Dementia/Amyotrophic Lateral Sclerosis.
Trageser KJ; Yang EJ; Smith C; Iban-Arias R; Oguchi T; Sebastian-Valverde M; Iqbal UH; Wu H; Estill M; Al Rahim M; Raval U; Herman FJ; Zhang YJ; Petrucelli L; Pasinetti GM
Mol Neurobiol; 2023 Jul; 60(7):4004-4016. PubMed ID: 37010807
[TBL] [Abstract][Full Text] [Related]
27. C9orf72 and RAB7L1 regulate vesicle trafficking in amyotrophic lateral sclerosis and frontotemporal dementia.
Aoki Y; Manzano R; Lee Y; Dafinca R; Aoki M; Douglas AGL; Varela MA; Sathyaprakash C; Scaber J; Barbagallo P; Vader P; Mäger I; Ezzat K; Turner MR; Ito N; Gasco S; Ohbayashi N; El Andaloussi S; Takeda S; Fukuda M; Talbot K; Wood MJA
Brain; 2017 Apr; 140(4):887-897. PubMed ID: 28334866
[TBL] [Abstract][Full Text] [Related]
28. Senataxin helicase, the causal gene defect in ALS4, is a significant modifier of C9orf72 ALS G4C2 and arginine-containing dipeptide repeat toxicity.
Bennett CL; Dastidar S; Arnold FJ; McKinstry SU; Stockford C; Freibaum BD; Sopher BL; Wu M; Seidner G; Joiner W; Taylor JP; West RJH; La Spada AR
Acta Neuropathol Commun; 2023 Oct; 11(1):164. PubMed ID: 37845749
[TBL] [Abstract][Full Text] [Related]
29. Cell-to-Cell Transmission of Dipeptide Repeat Proteins Linked to C9orf72-ALS/FTD.
Westergard T; Jensen BK; Wen X; Cai J; Kropf E; Iacovitti L; Pasinelli P; Trotti D
Cell Rep; 2016 Oct; 17(3):645-652. PubMed ID: 27732842
[TBL] [Abstract][Full Text] [Related]
30. Dipeptide repeat protein inclusions are rare in the spinal cord and almost absent from motor neurons in C9ORF72 mutant amyotrophic lateral sclerosis and are unlikely to cause their degeneration.
Gomez-Deza J; Lee YB; Troakes C; Nolan M; Al-Sarraj S; Gallo JM; Shaw CE
Acta Neuropathol Commun; 2015 Jun; 3():38. PubMed ID: 26108573
[TBL] [Abstract][Full Text] [Related]
31. C9orf72 Dipeptide Repeats Cause Selective Neurodegeneration and Cell-Autonomous Excitotoxicity in
Xu W; Xu J
J Neurosci; 2018 Aug; 38(35):7741-7752. PubMed ID: 30037833
[TBL] [Abstract][Full Text] [Related]
32. Therapeutic reduction of GGGGCC repeat RNA levels by hnRNPA3 suppresses neurodegeneration in Drosophila models of C9orf72-linked ALS/FTD.
Taminato T; Takeuchi T; Ueyama M; Mori K; Ikeda M; Mochizuki H; Nagai Y
Hum Mol Genet; 2023 May; 32(10):1673-1682. PubMed ID: 36611007
[TBL] [Abstract][Full Text] [Related]
33. Circadian sleep/wake-associated cells show dipeptide repeat protein aggregates in C9orf72-related ALS and FTLD cases.
Dedeene L; Van Schoor E; Vandenberghe R; Van Damme P; Poesen K; Thal DR
Acta Neuropathol Commun; 2019 Dec; 7(1):189. PubMed ID: 31791419
[TBL] [Abstract][Full Text] [Related]
34. A C. elegans model of C9orf72-associated ALS/FTD uncovers a conserved role for eIF2D in RAN translation.
Sonobe Y; Aburas J; Krishnan G; Fleming AC; Ghadge G; Islam P; Warren EC; Gu Y; Kankel MW; Brown AEX; Kiskinis E; Gendron TF; Gao FB; Roos RP; Kratsios P
Nat Commun; 2021 Oct; 12(1):6025. PubMed ID: 34654821
[TBL] [Abstract][Full Text] [Related]
35. Metformin ameliorates mitochondrial damage induced by C9orf72 poly(GR) via upregulating AKT phosphorylation.
Feng Y; Xu Z; Jin H; Chen Y; Fu C; Zhang Y; Yin Y; Wang H; Cheng W
J Cell Biochem; 2024 Mar; 125(3):e30526. PubMed ID: 38229533
[TBL] [Abstract][Full Text] [Related]
36. Molecular Mechanisms of Neurodegeneration Related to
Babić Leko M; Župunski V; Kirincich J; Smilović D; Hortobágyi T; Hof PR; Šimić G
Behav Neurol; 2019; 2019():2909168. PubMed ID: 30774737
[TBL] [Abstract][Full Text] [Related]
37. Poly(GR) in C9ORF72-Related ALS/FTD Compromises Mitochondrial Function and Increases Oxidative Stress and DNA Damage in iPSC-Derived Motor Neurons.
Lopez-Gonzalez R; Lu Y; Gendron TF; Karydas A; Tran H; Yang D; Petrucelli L; Miller BL; Almeida S; Gao FB
Neuron; 2016 Oct; 92(2):383-391. PubMed ID: 27720481
[TBL] [Abstract][Full Text] [Related]
38. Poly(GR) and poly(GA) in cerebrospinal fluid as potential biomarkers for C9ORF72-ALS/FTD.
Krishnan G; Raitcheva D; Bartlett D; Prudencio M; McKenna-Yasek DM; Douthwright C; Oskarsson BE; Ladha S; King OD; Barmada SJ; Miller TM; Bowser R; Watts JK; Petrucelli L; Brown RH; Kankel MW; Gao FB
Nat Commun; 2022 May; 13(1):2799. PubMed ID: 35589711
[TBL] [Abstract][Full Text] [Related]
39. C9-ALS/FTD-linked proline-arginine dipeptide repeat protein associates with paraspeckle components and increases paraspeckle formation.
Suzuki H; Shibagaki Y; Hattori S; Matsuoka M
Cell Death Dis; 2019 Oct; 10(10):746. PubMed ID: 31582731
[TBL] [Abstract][Full Text] [Related]
40. Aberrant deposition of stress granule-resident proteins linked to C9orf72-associated TDP-43 proteinopathy.
Chew J; Cook C; Gendron TF; Jansen-West K; Del Rosso G; Daughrity LM; Castanedes-Casey M; Kurti A; Stankowski JN; Disney MD; Rothstein JD; Dickson DW; Fryer JD; Zhang YJ; Petrucelli L
Mol Neurodegener; 2019 Feb; 14(1):9. PubMed ID: 30767771
[TBL] [Abstract][Full Text] [Related]
[Previous] [Next] [New Search]
