These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
168 related articles for article (PubMed ID: 3677437)
1. New conjugated urinary metabolites in intermediate type maple syrup urine disease. Hagenfeldt L; Naglo AS Clin Chim Acta; 1987 Oct; 169(1):77-83. PubMed ID: 3677437 [TBL] [Abstract][Full Text] [Related]
2. Elevated excretion of N-acetylated branched-chain amino acids in maple syrup urine disease. Lehnert W; Werle E Clin Chim Acta; 1988 Feb; 172(1):123-6. PubMed ID: 3359650 [No Abstract] [Full Text] [Related]
3. Studies of urinary organic acid profiles of a patient with dihydrolipoyl dehydrogenase deficiency. Kuhara T; Shinka T; Inoue Y; Matsumoto M; Yoshino M; Sakaguchi Y; Matsumoto I Clin Chim Acta; 1983 Sep; 133(2):133-40. PubMed ID: 6688766 [TBL] [Abstract][Full Text] [Related]
4. [Clinical characteristics and analysis of mass spectrometric data in 33 patients with maple syrup urine disease]. Yang N; Han LS; Ye J; Qiu WJ; Zhang HW; Gao XL; Wang Y; Li XY; Xu H; Gu XF Zhonghua Yi Xue Za Zhi; 2012 Oct; 92(40):2839-42. PubMed ID: 23290213 [TBL] [Abstract][Full Text] [Related]
5. Use of a diode array detector in investigation of neonatal organic aciduria. Allen KR; Khan R; Watson D Clin Chem; 1985 Apr; 31(4):561-3. PubMed ID: 3978788 [TBL] [Abstract][Full Text] [Related]
6. Renal clearance of branched-chain L-amino and 2-oxo acids in maple syrup urine disease. Schadewaldt P; Hammen HW; Ott AC; Wendel U J Inherit Metab Dis; 1999 Aug; 22(6):706-22. PubMed ID: 10472531 [TBL] [Abstract][Full Text] [Related]
7. Screening of organic acids in urine by chemical ionization mass spectrometry. Issachar D; Yinon J Biomed Mass Spectrom; 1979 Feb; 6(2):47-56. PubMed ID: 420910 [TBL] [Abstract][Full Text] [Related]
8. Plasma amino acid analyses in two cases of maple syrup urine disease. Surarit R; Srisomsap C; Wasant P; Svasti J; Suthatvoravut U; Chokchaichamnankit D; Liammongkolkul S Southeast Asian J Trop Med Public Health; 1999; 30 Suppl 2():138-9. PubMed ID: 11400750 [TBL] [Abstract][Full Text] [Related]
10. MAPLE SYRUP URINE DISEASE. VOYCE MA; MONTGOMERY JN; LYNCH GA; BOWMAN JK Br Med J; 1964 May; 1(5393):1293. PubMed ID: 14123637 [No Abstract] [Full Text] [Related]
11. [Metabolic disorders of branched-chain amino acids: most common forms of organic aciduria in the neonatal period]. Sperl W; Lehnert W Klin Padiatr; 1990; 202(5):334-9. PubMed ID: 2214593 [TBL] [Abstract][Full Text] [Related]
12. Urinary excretion of N-acetyl amino acids in patients with some inborn errors of amino acid metabolism. Jellum E; Horn L; Thoresen O; Kvittingen EA; Stokke O Scand J Clin Lab Invest Suppl; 1986; 184():21-6. PubMed ID: 3473611 [TBL] [Abstract][Full Text] [Related]
13. The relationship between the branched chain amino acids and their alpha-ketoacids in maple syrup urine disease. Snyderman SE; Goldstein F; Sansaricq C; Norton PM Pediatr Res; 1984 Sep; 18(9):851-3. PubMed ID: 6483508 [TBL] [Abstract][Full Text] [Related]
14. An 11-day-old boy with lethargy, poor feeding, vomiting. Maple syrup urine disease. Charrow J Pediatr Ann; 2005 Oct; 34(10):772-4. PubMed ID: 16285630 [No Abstract] [Full Text] [Related]
15. [CLINICAL, BIOCHEMICAL, AND NEUROPATHOLOGIC ASPECTS OF MAPLE SYRUP URINE DISEASE. A KETOACIDURIA OF THE OPEN CHAIN AMINOACIDS LEUCINE, ISOLEUCINE AND VALINE]. SILBERMANSCHWARTZMAN J An Fac Med Lima; 1963 Sep; 46():339-65. PubMed ID: 14122039 [No Abstract] [Full Text] [Related]
16. MRI in acute intermittent maple syrup urine disease. Di Rocco M; Biancheri R; Rossi A; Allegri AE; Vecchi V; Tortori-Donati P Neurology; 2004 Sep; 63(6):1078. PubMed ID: 15452301 [No Abstract] [Full Text] [Related]
17. [Acrodermatitis enteropathica-like syndrome secondary to branched-chain amino acid deficiency during treatment of maple syrup urine disease]. Templier I; Reymond JL; Nguyen MA; Boujet C; Lantuejoul S; Beani JC; Leccia MT Ann Dermatol Venereol; 2006 Apr; 133(4):375-9. PubMed ID: 16733455 [TBL] [Abstract][Full Text] [Related]
18. Simultaneous retention index analysis of urinary amino acids and carboxylic acids for graphic recognition of abnormal state. Paik MJ; Lee HJ; Kim KR J Chromatogr B Analyt Technol Biomed Life Sci; 2005 Jul; 821(1):94-104. PubMed ID: 15894518 [TBL] [Abstract][Full Text] [Related]
19. 4,5-dimethyl-3-hydroxy-2[5H]-furanone (sotolone)--the odour of maple syrup urine disease. Podebrad F; Heil M; Reichert S; Mosandl A; Sewell AC; Böhles H J Inherit Metab Dis; 1999 Apr; 22(2):107-14. PubMed ID: 10234605 [TBL] [Abstract][Full Text] [Related]