208 related articles for article (PubMed ID: 36799301)
21. Hypoxia treatment reverses neurodegenerative disease in a mouse model of Leigh syndrome.
Ferrari M; Jain IH; Goldberger O; Rezoagli E; Thoonen R; Cheng KH; Sosnovik DE; Scherrer-Crosbie M; Mootha VK; Zapol WM
Proc Natl Acad Sci U S A; 2017 May; 114(21):E4241-E4250. PubMed ID: 28483998
[TBL] [Abstract][Full Text] [Related]
22. Neuronal complex I deficiency occurs throughout the Parkinson's disease brain, but is not associated with neurodegeneration or mitochondrial DNA damage.
Flønes IH; Fernandez-Vizarra E; Lykouri M; Brakedal B; Skeie GO; Miletic H; Lilleng PK; Alves G; Tysnes OB; Haugarvoll K; Dölle C; Zeviani M; Tzoulis C
Acta Neuropathol; 2018 Mar; 135(3):409-425. PubMed ID: 29270838
[TBL] [Abstract][Full Text] [Related]
23. Altered dopamine metabolism and increased vulnerability to MPTP in mice with partial deficiency of mitochondrial complex I in dopamine neurons.
Sterky FH; Hoffman AF; Milenkovic D; Bao B; Paganelli A; Edgar D; Wibom R; Lupica CR; Olson L; Larsson NG
Hum Mol Genet; 2012 Mar; 21(5):1078-89. PubMed ID: 22090423
[TBL] [Abstract][Full Text] [Related]
24. Ndufs4 KO mice: A model to study comorbid mood disorders associated with mitochondrial dysfunction.
van Rensburg DJ; Lindeque Z; Harvey BH; Steyn SF
Pharmacol Biochem Behav; 2024 Jan; 234():173689. PubMed ID: 38070656
[TBL] [Abstract][Full Text] [Related]
25. Hypoxia ameliorates brain hyperoxia and NAD
Grange RMH; Sharma R; Shah H; Reinstadler B; Goldberger O; Cooper MK; Nakagawa A; Miyazaki Y; Hindle AG; Batten AJ; Wojtkiewicz GR; Schleifer G; Bagchi A; Marutani E; Malhotra R; Bloch DB; Ichinose F; Mootha VK; Zapol WM
Mol Genet Metab; 2021 May; 133(1):83-93. PubMed ID: 33752971
[TBL] [Abstract][Full Text] [Related]
26. Effects of clofibrate and KH176 on life span and motor function in mitochondrial complex I-deficient mice.
Frambach SJCM; van de Wal MAE; van den Broek PHH; Smeitink JAM; Russel FGM; de Haas R; Schirris TJJ
Biochim Biophys Acta Mol Basis Dis; 2020 Jun; 1866(6):165727. PubMed ID: 32070771
[TBL] [Abstract][Full Text] [Related]
27. Metabolomics of Ndufs4
Terburgh K; Lindeque Z; Mason S; van der Westhuizen F; Louw R
Biochim Biophys Acta Mol Basis Dis; 2019 Jan; 1865(1):98-106. PubMed ID: 30391276
[TBL] [Abstract][Full Text] [Related]
28. Differential requirements for mitochondrial electron transport chain components in the adult murine liver.
Lesner NP; Wang X; Chen Z; Frank A; Menezes CJ; House S; Shelton SD; Lemoff A; McFadden DG; Wansapura J; DeBerardinis RJ; Mishra P
Elife; 2022 Sep; 11():. PubMed ID: 36154948
[TBL] [Abstract][Full Text] [Related]
29. Metabolic rescue ameliorates mitochondrial encephalo-cardiomyopathy in murine and human iPSC models of Leigh syndrome.
Yoon JY; Daneshgar N; Chu Y; Chen B; Hefti M; Vikram A; Irani K; Song LS; Brenner C; Abel ED; London B; Dai DF
Clin Transl Med; 2022 Jul; 12(7):e954. PubMed ID: 35872650
[TBL] [Abstract][Full Text] [Related]
30. NAD+ Regeneration Rescues Lifespan, but Not Ataxia, in a Mouse Model of Brain Mitochondrial Complex I Dysfunction.
McElroy GS; Reczek CR; Reyfman PA; Mithal DS; Horbinski CM; Chandel NS
Cell Metab; 2020 Aug; 32(2):301-308.e6. PubMed ID: 32574562
[TBL] [Abstract][Full Text] [Related]
31. Mitochondrial iron metabolism and neurodegenerative diseases.
Cheng R; Dhorajia VV; Kim J; Kim Y
Neurotoxicology; 2022 Jan; 88():88-101. PubMed ID: 34748789
[TBL] [Abstract][Full Text] [Related]
32. Metallothionein 1 Overexpression Does Not Protect Against Mitochondrial Disease Pathology in Ndufs4 Knockout Mice.
Miller HC; Louw R; Mereis M; Venter G; Boshoff JD; Mienie L; van Reenen M; Venter M; Lindeque JZ; Domínguez-Martínez A; Quintana A; van der Westhuizen FH
Mol Neurobiol; 2021 Jan; 58(1):243-262. PubMed ID: 32918239
[TBL] [Abstract][Full Text] [Related]
33. NDUFS4 deletion triggers loss of NDUFA12 in Ndufs4
Adjobo-Hermans MJW; de Haas R; Willems PHGM; Wojtala A; van Emst-de Vries SE; Wagenaars JA; van den Brand M; Rodenburg RJ; Smeitink JAM; Nijtmans LG; Sazanov LA; Wieckowski MR; Koopman WJH
Biochim Biophys Acta Bioenerg; 2020 Aug; 1861(8):148213. PubMed ID: 32335026
[TBL] [Abstract][Full Text] [Related]
34. Tetracyclines promote survival and fitness in mitochondrial disease models.
Perry EA; Bennett CF; Luo C; Balsa E; Jedrychowski M; O'Malley KE; Latorre-Muro P; Ladley RP; Reda K; Wright PM; Gygi SP; Myers AG; Puigserver P
Nat Metab; 2021 Jan; 3(1):33-42. PubMed ID: 33462515
[TBL] [Abstract][Full Text] [Related]
35. Rare causes of hereditary iron overload.
Ponka P
Semin Hematol; 2002 Oct; 39(4):249-62. PubMed ID: 12382200
[TBL] [Abstract][Full Text] [Related]
36. Elevated susceptibility to exogenous seizure triggers and impaired interneuron excitability in a mouse model of Leigh syndrome epilepsy.
Manning A; Han V; Stephens A; Wang R; Bush N; Bard M; Ramirez JM; Kalume F
Neurobiol Dis; 2023 Oct; 187():106288. PubMed ID: 37704057
[TBL] [Abstract][Full Text] [Related]
37. Gene replacement therapy provides benefit in an adult mouse model of Leigh syndrome.
Reynaud-Dulaurier R; Benegiamo G; Marrocco E; Al-Tannir R; Surace EM; Auwerx J; Decressac M
Brain; 2020 Jun; 143(6):1686-1696. PubMed ID: 32413099
[TBL] [Abstract][Full Text] [Related]
38. Ubiquinone (coenzyme q10) and mitochondria in oxidative stress of parkinson's disease.
Ebadi M; Govitrapong P; Sharma S; Muralikrishnan D; Shavali S; Pellett L; Schafer R; Albano C; Eken J
Biol Signals Recept; 2001; 10(3-4):224-53. PubMed ID: 11351130
[TBL] [Abstract][Full Text] [Related]
39. AAV9-based gene therapy partially ameliorates the clinical phenotype of a mouse model of Leigh syndrome.
Di Meo I; Marchet S; Lamperti C; Zeviani M; Viscomi C
Gene Ther; 2017 Oct; 24(10):661-667. PubMed ID: 28753212
[TBL] [Abstract][Full Text] [Related]
40. Iron-sulfur enzyme mediated mitochondrial superoxide toxicity in experimental Parkinson's disease.
Liang LP; Patel M
J Neurochem; 2004 Sep; 90(5):1076-84. PubMed ID: 15312163
[TBL] [Abstract][Full Text] [Related]
[Previous] [Next] [New Search]