278 related articles for article (PubMed ID: 36834591)
1. FUS Alters circRNA Metabolism in Human Motor Neurons Carrying the ALS-Linked P525L Mutation.
Colantoni A; Capauto D; Alfano V; D'Ambra E; D'Uva S; Tartaglia GG; Morlando M
Int J Mol Sci; 2023 Feb; 24(4):. PubMed ID: 36834591
[TBL] [Abstract][Full Text] [Related]
2. FUS affects circular RNA expression in murine embryonic stem cell-derived motor neurons.
Errichelli L; Dini Modigliani S; Laneve P; Colantoni A; Legnini I; Capauto D; Rosa A; De Santis R; Scarfò R; Peruzzi G; Lu L; Caffarelli E; Shneider NA; Morlando M; Bozzoni I
Nat Commun; 2017 Mar; 8():14741. PubMed ID: 28358055
[TBL] [Abstract][Full Text] [Related]
3. The fused in sarcoma protein forms cytoplasmic aggregates in motor neurons derived from integration-free induced pluripotent stem cells generated from a patient with familial amyotrophic lateral sclerosis carrying the FUS-P525L mutation.
Liu X; Chen J; Liu W; Li X; Chen Q; Liu T; Gao S; Deng M
Neurogenetics; 2015 Jul; 16(3):223-31. PubMed ID: 25912081
[TBL] [Abstract][Full Text] [Related]
4. A Regulatory Circuitry Between Gria2, miR-409, and miR-495 Is Affected by ALS FUS Mutation in ESC-Derived Motor Neurons.
Capauto D; Colantoni A; Lu L; Santini T; Peruzzi G; Biscarini S; Morlando M; Shneider NA; Caffarelli E; Laneve P; Bozzoni I
Mol Neurobiol; 2018 Oct; 55(10):7635-7651. PubMed ID: 29430619
[TBL] [Abstract][Full Text] [Related]
5. The ALS-Associated FUS (P525L) Variant Does Not Directly Interfere with Microtubule-Dependent Kinesin-1 Motility.
Seifert A; Drechsler H; Japtok J; Korten T; Diez S; Hermann A
Int J Mol Sci; 2021 Feb; 22(5):. PubMed ID: 33670886
[TBL] [Abstract][Full Text] [Related]
6. RNA-binding ability of FUS regulates neurodegeneration, cytoplasmic mislocalization and incorporation into stress granules associated with FUS carrying ALS-linked mutations.
Daigle JG; Lanson NA; Smith RB; Casci I; Maltare A; Monaghan J; Nichols CD; Kryndushkin D; Shewmaker F; Pandey UB
Hum Mol Genet; 2013 Mar; 22(6):1193-205. PubMed ID: 23257289
[TBL] [Abstract][Full Text] [Related]
7. Stress-Specific Spatiotemporal Responses of RNA-Binding Proteins in Human Stem-Cell-Derived Motor Neurons.
Harley J; Patani R
Int J Mol Sci; 2020 Nov; 21(21):. PubMed ID: 33172210
[TBL] [Abstract][Full Text] [Related]
8. Deficient RNA-editing enzyme ADAR2 in an amyotrophic lateral sclerosis patient with a FUS(P525L) mutation.
Aizawa H; Hideyama T; Yamashita T; Kimura T; Suzuki N; Aoki M; Kwak S
J Clin Neurosci; 2016 Oct; 32():128-9. PubMed ID: 27343041
[TBL] [Abstract][Full Text] [Related]
9. ALS mutations of FUS suppress protein translation and disrupt the regulation of nonsense-mediated decay.
Kamelgarn M; Chen J; Kuang L; Jin H; Kasarskis EJ; Zhu H
Proc Natl Acad Sci U S A; 2018 Dec; 115(51):E11904-E11913. PubMed ID: 30455313
[TBL] [Abstract][Full Text] [Related]
10. Aberrant axon branching via Fos-B dysregulation in FUS-ALS motor neurons.
Akiyama T; Suzuki N; Ishikawa M; Fujimori K; Sone T; Kawada J; Funayama R; Fujishima F; Mitsuzawa S; Ikeda K; Ono H; Shijo T; Osana S; Shirota M; Nakagawa T; Kitajima Y; Nishiyama A; Izumi R; Morimoto S; Okada Y; Kamei T; Nishida M; Nogami M; Kaneda S; Ikeuchi Y; Mitsuhashi H; Nakayama K; Fujii T; Warita H; Okano H; Aoki M
EBioMedicine; 2019 Jul; 45():362-378. PubMed ID: 31262712
[TBL] [Abstract][Full Text] [Related]
11. Homozygous ALS-linked FUS P525L mutations cell- autonomously perturb transcriptome profile and chemoreceptor signaling in human iPSC microglia.
Kerk SY; Bai Y; Smith J; Lalgudi P; Hunt C; Kuno J; Nuara J; Yang T; Lanza K; Chan N; Coppola A; Tang Q; Espert J; Jones H; Fannell C; Zambrowicz B; Chiao E
Stem Cell Reports; 2022 Mar; 17(3):678-692. PubMed ID: 35120624
[TBL] [Abstract][Full Text] [Related]
12. ALS-Related Mutant FUS Protein Is Mislocalized to Cytoplasm and Is Recruited into Stress Granules of Fibroblasts from Asymptomatic FUS P525L Mutation Carriers.
Lo Bello M; Di Fini F; Notaro A; Spataro R; Conforti FL; La Bella V
Neurodegener Dis; 2017; 17(6):292-303. PubMed ID: 29035885
[TBL] [Abstract][Full Text] [Related]
13. Impaired nuclear transport induced by juvenile ALS causing P525L mutation in NLS domain of FUS: A molecular mechanistic study.
Basu S; Rajendra KC; Alagar S; Bahadur RP
Biochim Biophys Acta Proteins Proteom; 2022 Apr; 1870(4):140766. PubMed ID: 35134572
[TBL] [Abstract][Full Text] [Related]
14. Cytoplasmic aggregation of mutant FUS causes multistep RNA splicing perturbations in the course of motor neuron pathology.
Rezvykh AP; Ustyugov AA; Chaprov KD; Teterina EV; Nebogatikov VO; Spasskaya DS; Evgen'ev MB; Morozov AV; Funikov SY
Nucleic Acids Res; 2023 Jun; 51(11):5810-5830. PubMed ID: 37115004
[TBL] [Abstract][Full Text] [Related]
15. Human TDP-43 and FUS selectively affect motor neuron maturation and survival in a murine cell model of ALS by non-cell-autonomous mechanisms.
Wächter N; Storch A; Hermann A
Amyotroph Lateral Scler Frontotemporal Degener; 2015; 16(7-8):431-41. PubMed ID: 26174443
[TBL] [Abstract][Full Text] [Related]
16. Altered calcium dynamics and glutamate receptor properties in iPSC-derived motor neurons from ALS patients with C9orf72, FUS, SOD1 or TDP43 mutations.
Bursch F; Kalmbach N; Naujock M; Staege S; Eggenschwiler R; Abo-Rady M; Japtok J; Guo W; Hensel N; Reinhardt P; Boeckers TM; Cantz T; Sterneckert J; Van Den Bosch L; Hermann A; Petri S; Wegner F
Hum Mol Genet; 2019 Sep; 28(17):2835-2850. PubMed ID: 31108504
[TBL] [Abstract][Full Text] [Related]
17. ALS-associated mutations in FUS disrupt the axonal distribution and function of SMN.
Groen EJ; Fumoto K; Blokhuis AM; Engelen-Lee J; Zhou Y; van den Heuvel DM; Koppers M; van Diggelen F; van Heest J; Demmers JA; Kirby J; Shaw PJ; Aronica E; Spliet WG; Veldink JH; van den Berg LH; Pasterkamp RJ
Hum Mol Genet; 2013 Sep; 22(18):3690-704. PubMed ID: 23681068
[TBL] [Abstract][Full Text] [Related]
18. Upregulation of β-catenin due to loss of miR-139 contributes to motor neuron death in amyotrophic lateral sclerosis.
Hawkins S; Namboori SC; Tariq A; Blaker C; Flaxman C; Dey NS; Henley P; Randall A; Rosa A; Stanton LW; Bhinge A
Stem Cell Reports; 2022 Jul; 17(7):1650-1665. PubMed ID: 35750046
[TBL] [Abstract][Full Text] [Related]
19. ALS-linked FUS mutations dysregulate G-quadruplex-dependent liquid-liquid phase separation and liquid-to-solid transition.
Ishiguro A; Lu J; Ozawa D; Nagai Y; Ishihama A
J Biol Chem; 2021 Nov; 297(5):101284. PubMed ID: 34624313
[TBL] [Abstract][Full Text] [Related]
20. lncRNA Sequencing Reveals Neurodegeneration-Associated FUS Mutations Alter Transcriptional Landscape of iPS Cells That Persists in Motor Neurons.
Provasek VE; Kodavati M; Guo W; Wang H; Boldogh I; Van Den Bosch L; Britz G; Hegde ML
Cells; 2023 Oct; 12(20):. PubMed ID: 37887305
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]