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5. Mechanisms of angiogenic incompetence in Hutchinson-Gilford progeria via downregulation of endothelial NOS. Gete YG; Koblan LW; Mao X; Trappio M; Mahadik B; Fisher JP; Liu DR; Cao K Aging Cell; 2021 Jul; 20(7):e13388. PubMed ID: 34086398 [TBL] [Abstract][Full Text] [Related]
6. Molecular and Cellular Mechanisms Driving Cardiovascular Disease in Hutchinson-Gilford Progeria Syndrome: Lessons Learned from Animal Models. Benedicto I; Dorado B; Andrés V Cells; 2021 May; 10(5):. PubMed ID: 34064612 [TBL] [Abstract][Full Text] [Related]
7. FDA approval summary for lonafarnib (Zokinvy) for the treatment of Hutchinson-Gilford progeria syndrome and processing-deficient progeroid laminopathies. Suzuki M; Jeng LJB; Chefo S; Wang Y; Price D; Li X; Wang J; Li RJ; Ma L; Yang Y; Zhang X; Zheng N; Zhang K; Joseph DB; Shroff H; Doan J; Pacanowski M; Smpokou P; Donohue K; Joffe HV Genet Med; 2023 Feb; 25(2):100335. PubMed ID: 36507973 [TBL] [Abstract][Full Text] [Related]
8. Vascular Smooth Muscle-Specific Progerin Expression Accelerates Atherosclerosis and Death in a Mouse Model of Hutchinson-Gilford Progeria Syndrome. Hamczyk MR; Villa-Bellosta R; Gonzalo P; Andrés-Manzano MJ; Nogales P; Bentzon JF; López-Otín C; Andrés V Circulation; 2018 Jul; 138(3):266-282. PubMed ID: 29490993 [TBL] [Abstract][Full Text] [Related]
9. Vascular smooth muscle cell loss underpins the accelerated atherosclerosis in Hutchinson-Gilford progeria syndrome. Hamczyk MR; Andrés V Nucleus; 2019 Dec; 10(1):28-34. PubMed ID: 30900948 [TBL] [Abstract][Full Text] [Related]
10. Impaired LEF1 Activation Accelerates iPSC-Derived Keratinocytes Differentiation in Hutchinson-Gilford Progeria Syndrome. Mao X; Xiong ZM; Xue H; Brown MA; Gete YG; Yu R; Sun L; Cao K Int J Mol Sci; 2022 May; 23(10):. PubMed ID: 35628310 [TBL] [Abstract][Full Text] [Related]
12. A human iPSC model of Hutchinson Gilford Progeria reveals vascular smooth muscle and mesenchymal stem cell defects. Zhang J; Lian Q; Zhu G; Zhou F; Sui L; Tan C; Mutalif RA; Navasankari R; Zhang Y; Tse HF; Stewart CL; Colman A Cell Stem Cell; 2011 Jan; 8(1):31-45. PubMed ID: 21185252 [TBL] [Abstract][Full Text] [Related]
13. Progerin-expressing endothelial cells are unable to adapt to shear stress. Danielsson BE; Peters HC; Bathula K; Spear LM; Noll NA; Dahl KN; Conway DE Biophys J; 2022 Feb; 121(4):620-628. PubMed ID: 34999130 [TBL] [Abstract][Full Text] [Related]
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19. Premature Vascular Aging with Features of Plaque Vulnerability in an Atheroprone Mouse Model of Hutchinson-Gilford Progeria Syndrome with Nevado RM; Hamczyk MR; Gonzalo P; Andrés-Manzano MJ; Andrés V Cells; 2020 Oct; 9(10):. PubMed ID: 33049978 [TBL] [Abstract][Full Text] [Related]