These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
224 related articles for article (PubMed ID: 37242166)
1. Citrin Deficiency: Clinical and Nutritional Features. Komatsu M; Tanaka N; Kimura T; Yazaki M Nutrients; 2023 May; 15(10):. PubMed ID: 37242166 [No Abstract] [Full Text] [Related]
2. Current treatment for citrin deficiency during NICCD and adaptation/compensation stages: Strategy to prevent CTLN2. Okano Y; Ohura T; Sakamoto O; Inui A Mol Genet Metab; 2019 Jul; 127(3):175-183. PubMed ID: 31255436 [TBL] [Abstract][Full Text] [Related]
3. Pathogenesis and Management of Citrin Deficiency. Hayasaka K Intern Med; 2024 Jul; 63(14):1977-1986. PubMed ID: 37952953 [TBL] [Abstract][Full Text] [Related]
4. Medium-chain triglyceride supplementation under a low-carbohydrate formula is a promising therapy for adult-onset type II citrullinemia. Hayasaka K; Numakura C; Toyota K; Kakizaki S; Watanabe H; Haga H; Takahashi H; Takahashi Y; Kaneko M; Yamakawa M; Nunoi H; Kato T; Ueno Y; Mori M Mol Genet Metab Rep; 2014; 1():42-50. PubMed ID: 27896073 [TBL] [Abstract][Full Text] [Related]
5. Hypoglycemic attacks and growth failure are the most common manifestations of citrin deficiency after 1 year of age. Arai-Ichinoi N; Kikuchi A; Wada Y; Sakamoto O; Kure S J Inherit Metab Dis; 2021 Jul; 44(4):838-846. PubMed ID: 33861477 [TBL] [Abstract][Full Text] [Related]
6. Steatogenesis in adult-onset type II citrullinemia is associated with down-regulation of PPARα. Komatsu M; Kimura T; Yazaki M; Tanaka N; Yang Y; Nakajima T; Horiuchi A; Fang ZZ; Joshita S; Matsumoto A; Umemura T; Tanaka E; Gonzalez FJ; Ikeda S; Aoyama T Biochim Biophys Acta; 2015 Mar; 1852(3):473-81. PubMed ID: 25533124 [TBL] [Abstract][Full Text] [Related]
7. Update on the diagnosis and management of neonatal intrahepatic cholestasis caused by citrin deficiency: Expert review on behalf of the Asian Pan-Pacific Society for Pediatric Gastroenterology, Hepatology, and Nutrition. Inui A; Ko JS; Chongsrisawat V; Sibal A; Hardikar W; Chang MH; Treepongkaruna S; Arai K; Kim KM; Chen HL J Pediatr Gastroenterol Nutr; 2024 Feb; 78(2):178-187. PubMed ID: 38374571 [TBL] [Abstract][Full Text] [Related]
8. Clinical findings in five Turkish patients with citrin deficiency and identification of a novel mutation on SLC25A13. Köse MD; Kagnici M; Özdemir TR; Erdur CB; Erdemir G; Karakoyun M; Guzin Y; Ceylaner S; Genel F J Pediatr Endocrinol Metab; 2020 Jan; 33(1):157-163. PubMed ID: 31809266 [TBL] [Abstract][Full Text] [Related]
9. Mitochondrial aspartate glutamate carrier (citrin) deficiency as the cause of adult-onset type II citrullinemia (CTLN2) and idiopathic neonatal hepatitis (NICCD). Saheki T; Kobayashi K J Hum Genet; 2002; 47(7):333-41. PubMed ID: 12111366 [TBL] [Abstract][Full Text] [Related]
10. AGC2 (Citrin) Deficiency-From Recognition of the Disease till Construction of Therapeutic Procedures. Saheki T; Moriyama M; Funahashi A; Kuroda E Biomolecules; 2020 Jul; 10(8):. PubMed ID: 32722104 [TBL] [Abstract][Full Text] [Related]
11. Neonatal intrahepatic cholestasis caused by citrin deficiency (NICCD) in three Malay children. Ngu HL; Zabedah MY; Kobayashi K Malays J Pathol; 2010 Jun; 32(1):53-7. PubMed ID: 20614727 [TBL] [Abstract][Full Text] [Related]
12. Metabolic basis and treatment of citrin deficiency. Hayasaka K J Inherit Metab Dis; 2021 Jan; 44(1):110-117. PubMed ID: 32740958 [TBL] [Abstract][Full Text] [Related]
13. Analysis of daily energy, protein, fat, and carbohydrate intake in citrin-deficient patients: Towards prevention of adult-onset type II citrullinemia. Okano Y; Okamoto M; Yazaki M; Inui A; Ohura T; Murayama K; Watanabe Y; Tokuhara D; Takeshima Y Mol Genet Metab; 2021 May; 133(1):63-70. PubMed ID: 33741270 [TBL] [Abstract][Full Text] [Related]
14. Conventional diet therapy for hyperammonemia is risky in the treatment of hepatic encephalopathy associated with citrin deficiency. Fukushima K; Yazaki M; Nakamura M; Tanaka N; Kobayashi K; Saheki T; Takei H; Ikeda S Intern Med; 2010; 49(3):243-7. PubMed ID: 20118603 [TBL] [Abstract][Full Text] [Related]
15. Adult-onset type II citrullinemia: Current insights and therapy. Hayasaka K; Numakura C Appl Clin Genet; 2018; 11():163-170. PubMed ID: 30588060 [TBL] [Abstract][Full Text] [Related]
16. Clinical manifestation and long-term outcome of citrin deficiency: Report from a nationwide study in Japan. Kido J; Häberle J; Sugawara K; Tanaka T; Nagao M; Sawada T; Wada Y; Numakura C; Murayama K; Watanabe Y; Kojima-Ishii K; Sasai H; Kosugiyama K; Nakamura K J Inherit Metab Dis; 2022 May; 45(3):431-444. PubMed ID: 35142380 [TBL] [Abstract][Full Text] [Related]
17. Effects of supplementation on food intake, body weight and hepatic metabolites in the citrin/mitochondrial glycerol-3-phosphate dehydrogenase double-knockout mouse model of human citrin deficiency. Saheki T; Inoue K; Ono H; Katsura N; Yokogawa M; Yoshidumi Y; Furuie S; Kuroda E; Ushikai M; Asakawa A; Inui A; Eto K; Kadowaki T; Sinasac DS; Yamamura K; Kobayashi K Mol Genet Metab; 2012 Nov; 107(3):322-9. PubMed ID: 22921887 [TBL] [Abstract][Full Text] [Related]
18. Medium-chain triglycerides supplement therapy with a low-carbohydrate formula can supply energy and enhance ammonia detoxification in the hepatocytes of patients with adult-onset type II citrullinemia. Hayasaka K; Numakura C; Yamakawa M; Mitsui T; Watanabe H; Haga H; Yazaki M; Ohira H; Ochiai Y; Tahara T; Nakahara T; Yamashiki N; Nakayama T; Kon T; Mitsubuchi H; Yoshida H J Inherit Metab Dis; 2018 Sep; 41(5):777-784. PubMed ID: 29651749 [TBL] [Abstract][Full Text] [Related]
19. Citrin deficiency as a cause of chronic liver disorder mimicking non-alcoholic fatty liver disease. Komatsu M; Yazaki M; Tanaka N; Sano K; Hashimoto E; Takei Y; Song YZ; Tanaka E; Kiyosawa K; Saheki T; Aoyama T; Kobayashi K J Hepatol; 2008 Nov; 49(5):810-20. PubMed ID: 18620775 [TBL] [Abstract][Full Text] [Related]