171 related articles for article (PubMed ID: 37525026)
1. Olaparib Attenuates Demyelination and Neuroinflammation in an Organotypic Slice Culture Model of Metachromatic Leukodystrophy.
Mekhaeil M; Conroy MJ; Dev KK
Neurotherapeutics; 2023 Sep; 20(5):1347-1368. PubMed ID: 37525026
[TBL] [Abstract][Full Text] [Related]
2. Elucidating the Therapeutic Utility of Olaparib in Sulfatide-Induced Human Astrocyte Toxicity and Neuroinflammation.
Mekhaeil M; Conroy MJ; Dev KK
J Neuroimmune Pharmacol; 2023 Dec; 18(4):592-609. PubMed ID: 37924373
[TBL] [Abstract][Full Text] [Related]
3. Arylsulfatase A Overexpressing Human iPSC-derived Neural Cells Reduce CNS Sulfatide Storage in a Mouse Model of Metachromatic Leukodystrophy.
Doerr J; Böckenhoff A; Ewald B; Ladewig J; Eckhardt M; Gieselmann V; Matzner U; Brüstle O; Koch P
Mol Ther; 2015 Sep; 23(9):1519-31. PubMed ID: 26061647
[TBL] [Abstract][Full Text] [Related]
4. Deletion of fatty acid amide hydrolase reduces lyso-sulfatide levels but exacerbates metachromatic leukodystrophy in mice.
Yaghootfam C; Gehrig B; Sylvester M; Gieselmann V; Matzner U
J Biol Chem; 2021 Sep; 297(3):101064. PubMed ID: 34375644
[TBL] [Abstract][Full Text] [Related]
5. Increasing sulfatide synthesis in myelin-forming cells of arylsulfatase A-deficient mice causes demyelination and neurological symptoms reminiscent of human metachromatic leukodystrophy.
Ramakrishnan H; Hedayati KK; Lüllmann-Rauch R; Wessig C; Fewou SN; Maier H; Goebel HH; Gieselmann V; Eckhardt M
J Neurosci; 2007 Aug; 27(35):9482-90. PubMed ID: 17728461
[TBL] [Abstract][Full Text] [Related]
6. [Pathophysiology of sulfatide metabolism in metachromatic leukodystrophy].
Wiesmann UN
Bull Schweiz Akad Med Wiss; 1978 Mar; 34(1-3):33-47. PubMed ID: 27269
[TBL] [Abstract][Full Text] [Related]
7. Treatment of adult metachromatic leukodystrophy model mice using intrathecal administration of type 9 AAV vector encoding arylsulfatase A.
Miyake N; Miyake K; Sakai A; Yamamoto M; Suzuki H; Shimada T
Sci Rep; 2021 Oct; 11(1):20513. PubMed ID: 34654893
[TBL] [Abstract][Full Text] [Related]
8. A spontaneously immortalized Schwann cell line to study the molecular aspects of metachromatic leukodystrophy.
Saravanan K; Büssow H; Weiler N; Gieselmann V; Franken S
J Neurosci Methods; 2007 Apr; 161(2):223-33. PubMed ID: 17204333
[TBL] [Abstract][Full Text] [Related]
9. Oligodendroglial progenitor cell therapy limits central neurological deficits in mice with metachromatic leukodystrophy.
Givogri MI; Galbiati F; Fasano S; Amadio S; Perani L; Superchi D; Morana P; Del Carro U; Marchesini S; Brambilla R; Wrabetz L; Bongarzone E
J Neurosci; 2006 Mar; 26(12):3109-19. PubMed ID: 16554462
[TBL] [Abstract][Full Text] [Related]
10. Clinical, Biochemical, and Molecular Characterization of Metachromatic Leukodystrophy Among Egyptian Pediatric Patients: Expansion of the ARSA Mutational Spectrum.
Amr K; Fateen E; Mansour L; Tosson AM; Zaki MS; Salam GMA; Mohamed AN; El-Bassyouni HT
J Mol Neurosci; 2021 May; 71(5):1112-1130. PubMed ID: 33185815
[TBL] [Abstract][Full Text] [Related]
11. Lysosomal sulfatide storage in the brain of arylsulfatase A-deficient mice: cellular alterations and topographic distribution.
Wittke D; Hartmann D; Gieselmann V; Lüllmann-Rauch R
Acta Neuropathol; 2004 Oct; 108(4):261-71. PubMed ID: 15322834
[TBL] [Abstract][Full Text] [Related]
12. Enzymatic characterization of novel arylsulfatase A variants using human arylsulfatase A-deficient immortalized mesenchymal stromal cells.
Böhringer J; Santer R; Schumacher N; Gieseke F; Cornils K; Pechan M; Kustermann-Kuhn B; Handgretinger R; Schöls L; Harzer K; Krägeloh-Mann I; Müller I
Hum Mutat; 2017 Nov; 38(11):1511-1520. PubMed ID: 28762252
[TBL] [Abstract][Full Text] [Related]
13. Generation of Human Induced Pluripotent Stem Cell-Derived Bona Fide Neural Stem Cells for Ex Vivo Gene Therapy of Metachromatic Leukodystrophy.
Meneghini V; Frati G; Sala D; De Cicco S; Luciani M; Cavazzin C; Paulis M; Mentzen W; Morena F; Giannelli S; Sanvito F; Villa A; Bulfone A; Broccoli V; Martino S; Gritti A
Stem Cells Transl Med; 2017 Feb; 6(2):352-368. PubMed ID: 28191778
[TBL] [Abstract][Full Text] [Related]
14. Specific downregulation and mistargeting of the lipid raft-associated protein MAL in a glycolipid storage disorder.
Saravanan K; Schaeren-Wiemers N; Klein D; Sandhoff R; Schwarz A; Yaghootfam A; Gieselmann V; Franken S
Neurobiol Dis; 2004 Jul; 16(2):396-406. PubMed ID: 15193296
[TBL] [Abstract][Full Text] [Related]
15. A new analytical bench assay for the determination of arylsulfatase a activity toward galactosyl-3-sulfate ceramide: implication for metachromatic leukodystrophy diagnosis.
Morena F; di Girolamo I; Emiliani C; Gritti A; Biffi A; Martino S
Anal Chem; 2014 Jan; 86(1):473-81. PubMed ID: 24294900
[TBL] [Abstract][Full Text] [Related]
16. Embryonic stem cell-based reduction of central nervous system sulfatide storage in an animal model of metachromatic leukodystrophy.
Klein D; Schmandt T; Muth-Köhne E; Perez-Bouza A; Segschneider M; Gieselmann V; Brüstle O
Gene Ther; 2006 Dec; 13(24):1686-95. PubMed ID: 16871228
[TBL] [Abstract][Full Text] [Related]
17. Saposin B-dependent reconstitution of arylsulfatase A activity in vitro and in cell culture models of metachromatic leukodystrophy.
Matzner U; Breiden B; Schwarzmann G; Yaghootfam A; Fluharty AL; Hasilik A; Sandhoff K; Gieselmann V
J Biol Chem; 2009 Apr; 284(14):9372-81. PubMed ID: 19224915
[TBL] [Abstract][Full Text] [Related]
18. Metachromatic leukodystrophy without arylsulfatase A deficiency: a new case of saposin-B deficiency.
Deconinck N; Messaaoui A; Ziereisen F; Kadhim H; Sznajer Y; Pelc K; Nassogne MC; Vanier MT; Dan B
Eur J Paediatr Neurol; 2008 Jan; 12(1):46-50. PubMed ID: 17616409
[TBL] [Abstract][Full Text] [Related]
19. Accumulation of lysosulfatide in the brain of arylsulfatase A-deficient mice.
Blomqvist M; Gieselmann V; Månsson JE
Lipids Health Dis; 2011 Feb; 10():28. PubMed ID: 21299873
[TBL] [Abstract][Full Text] [Related]
20. Gene therapy of metachromatic leukodystrophy reverses neurological damage and deficits in mice.
Biffi A; Capotondo A; Fasano S; del Carro U; Marchesini S; Azuma H; Malaguti MC; Amadio S; Brambilla R; Grompe M; Bordignon C; Quattrini A; Naldini L
J Clin Invest; 2006 Nov; 116(11):3070-82. PubMed ID: 17080200
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]