These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
194 related articles for article (PubMed ID: 38285890)
1. Sirtuin3 promotes the degradation of hepatic Z alpha-1 antitrypsin through lipophagy. Poole B; Oshins R; Huo Z; Aranyos A; West J; Duarte S; Clark VC; Beduschi T; Zarrinpar A; Brantly M; Khodayari N Hepatol Commun; 2024 Feb; 8(2):. PubMed ID: 38285890 [TBL] [Abstract][Full Text] [Related]
2. The Mechanism of Mitochondrial Injury in Alpha-1 Antitrypsin Deficiency Mediated Liver Disease. Khodayari N; Wang RL; Oshins R; Lu Y; Millett M; Aranyos AM; Mostofizadeh S; Scindia Y; Flagg TO; Brantly M Int J Mol Sci; 2021 Dec; 22(24):. PubMed ID: 34948056 [TBL] [Abstract][Full Text] [Related]
3. Modulation of calreticulin expression reveals a novel exosome-mediated mechanism of Z variant α Khodayari N; Oshins R; Alli AA; Tuna KM; Holliday LS; Krotova K; Brantly M J Biol Chem; 2019 Apr; 294(16):6240-6252. PubMed ID: 30833329 [TBL] [Abstract][Full Text] [Related]
4. Characterization of hepatic inflammatory changes in a C57BL/6J mouse model of alpha1-antitrypsin deficiency. Khodayari N; Oshins R; Aranyos AM; Duarte S; Mostofizadeh S; Lu Y; Brantly M Am J Physiol Gastrointest Liver Physiol; 2022 Dec; 323(6):G594-G608. PubMed ID: 36256438 [TBL] [Abstract][Full Text] [Related]
5. Erdj3 Has an Essential Role for Z Variant Alpha-1-Antitrypsin Degradation. Khodayari N; Marek G; Lu Y; Krotova K; Wang RL; Brantly M J Cell Biochem; 2017 Oct; 118(10):3090-3101. PubMed ID: 28419579 [TBL] [Abstract][Full Text] [Related]
6. SVIP regulates Z variant alpha-1 antitrypsin retro-translocation by inhibiting ubiquitin ligase gp78. Khodayari N; Wang RL; Marek G; Krotova K; Kirst M; Liu C; Rouhani F; Brantly M PLoS One; 2017; 12(3):e0172983. PubMed ID: 28301499 [TBL] [Abstract][Full Text] [Related]
7. The Autophagy Pathway: A Critical Route in the Disposal of Alpha 1-Antitrypsin Aggregates That Holds Many Mysteries. Leon C; Bouchecareilh M Int J Mol Sci; 2021 Feb; 22(4):. PubMed ID: 33668611 [TBL] [Abstract][Full Text] [Related]
11. The role of autophagy in alpha-1-antitrypsin deficiency. Hidvegi T; Mukherjee A; Ewing M; Kemp C; Perlmutter DH Methods Enzymol; 2011; 499():33-54. PubMed ID: 21683248 [TBL] [Abstract][Full Text] [Related]
12. An autophagy-enhancing drug promotes degradation of mutant alpha1-antitrypsin Z and reduces hepatic fibrosis. Hidvegi T; Ewing M; Hale P; Dippold C; Beckett C; Kemp C; Maurice N; Mukherjee A; Goldbach C; Watkins S; Michalopoulos G; Perlmutter DH Science; 2010 Jul; 329(5988):229-32. PubMed ID: 20522742 [TBL] [Abstract][Full Text] [Related]
13. Clinical and histologic features of adults with alpha-1 antitrypsin deficiency in a non-cirrhotic cohort. Clark VC; Marek G; Liu C; Collinsworth A; Shuster J; Kurtz T; Nolte J; Brantly M J Hepatol; 2018 Dec; 69(6):1357-1364. PubMed ID: 30138687 [TBL] [Abstract][Full Text] [Related]
14. Protein Misfolding and Aggregation: The Relatedness between Parkinson's Disease and Hepatic Endoplasmic Reticulum Storage Disorders. Padilla-Godínez FJ; Ramos-Acevedo R; Martínez-Becerril HA; Bernal-Conde LD; Garrido-Figueroa JF; Hiriart M; Hernández-López A; Argüero-Sánchez R; Callea F; Guerra-Crespo M Int J Mol Sci; 2021 Nov; 22(22):. PubMed ID: 34830348 [TBL] [Abstract][Full Text] [Related]
15. Quantitative Lipid Profiling Reveals Major Differences between Liver Organoids with Normal Pi*M and Deficient Pi*Z Variants of Alpha-1-antitrypsin. Pérez-Luz S; Lalchandani J; Matamala N; Barrero MJ; Gil-Martín S; Saz SR; Varona S; Monzón S; Cuesta I; Justo I; Marcacuzco A; Hierro L; Garfia C; Gomez-Mariano G; Janciauskiene S; Martínez-Delgado B Int J Mol Sci; 2023 Aug; 24(15):. PubMed ID: 37569847 [TBL] [Abstract][Full Text] [Related]
16. Liver Fibrosis and Metabolic Alterations in Adults With alpha-1-antitrypsin Deficiency Caused by the Pi*ZZ Mutation. Hamesch K; Mandorfer M; Pereira VM; Moeller LS; Pons M; Dolman GE; Reichert MC; Schneider CV; Woditsch V; Voss J; Lindhauer C; Fromme M; Spivak I; Guldiken N; Zhou B; Arslanow A; Schaefer B; Zoller H; Aigner E; Reiberger T; Wetzel M; Siegmund B; Simões C; Gaspar R; Maia L; Costa D; Bento-Miranda M; van Helden J; Yagmur E; Bzdok D; Stolk J; Gleiber W; Knipel V; Windisch W; Mahadeva R; Bals R; Koczulla R; Barrecheguren M; Miravitlles M; Janciauskiene S; Stickel F; Lammert F; Liberal R; Genesca J; Griffiths WJ; Trauner M; Krag A; Trautwein C; Strnad P; Gastroenterology; 2019 Sep; 157(3):705-719.e18. PubMed ID: 31121167 [TBL] [Abstract][Full Text] [Related]
17. Gene transfer of master autophagy regulator TFEB results in clearance of toxic protein and correction of hepatic disease in alpha-1-anti-trypsin deficiency. Pastore N; Blomenkamp K; Annunziata F; Piccolo P; Mithbaokar P; Maria Sepe R; Vetrini F; Palmer D; Ng P; Polishchuk E; Iacobacci S; Polishchuk R; Teckman J; Ballabio A; Brunetti-Pierri N EMBO Mol Med; 2013 Mar; 5(3):397-412. PubMed ID: 23381957 [TBL] [Abstract][Full Text] [Related]
19. Tauroursodeoxycholic acid inhibits apoptosis induced by Z alpha-1 antitrypsin via inhibition of Bad. Miller SD; Greene CM; McLean C; Lawless MW; Taggart CC; O'Neill SJ; McElvaney NG Hepatology; 2007 Aug; 46(2):496-503. PubMed ID: 17559149 [TBL] [Abstract][Full Text] [Related]
20. The pathological Trento variant of alpha-1-antitrypsin (E75V) shows nonclassical behaviour during polymerization. Miranda E; Ferrarotti I; Berardelli R; Laffranchi M; Cerea M; Gangemi F; Haq I; Ottaviani S; Lomas DA; Irving JA; Fra A FEBS J; 2017 Jul; 284(13):2110-2126. PubMed ID: 28504839 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]