165 related articles for article (PubMed ID: 38467696)
1. Evidence for disrupted copper availability in human spinal cord supports Cu
Hilton JBW; Kysenius K; Liddell JR; Mercer SW; Paul B; Beckman JS; McLean CA; White AR; Donnelly PS; Bush AI; Hare DJ; Roberts BR; Crouch PJ
Sci Rep; 2024 Mar; 14(1):5929. PubMed ID: 38467696
[TBL] [Abstract][Full Text] [Related]
2. The accumulation of enzymatically inactive cuproenzymes is a CNS-specific phenomenon of the SOD1
Hilton JB; Kysenius K; White AR; Crouch PJ
Exp Neurol; 2018 Sep; 307():118-128. PubMed ID: 29906423
[TBL] [Abstract][Full Text] [Related]
3. Zn II(atsm) is protective in amyotrophic lateral sclerosis model mice via a copper delivery mechanism.
McAllum EJ; Roberts BR; Hickey JL; Dang TN; Grubman A; Donnelly PS; Liddell JR; White AR; Crouch PJ
Neurobiol Dis; 2015 Sep; 81():20-4. PubMed ID: 25766674
[TBL] [Abstract][Full Text] [Related]
4. Oral treatment with Cu(II)(atsm) increases mutant SOD1 in vivo but protects motor neurons and improves the phenotype of a transgenic mouse model of amyotrophic lateral sclerosis.
Roberts BR; Lim NK; McAllum EJ; Donnelly PS; Hare DJ; Doble PA; Turner BJ; Price KA; Lim SC; Paterson BM; Hickey JL; Rhoads TW; Williams JR; Kanninen KM; Hung LW; Liddell JR; Grubman A; Monty JF; Llanos RM; Kramer DR; Mercer JF; Bush AI; Masters CL; Duce JA; Li QX; Beckman JS; Barnham KJ; White AR; Crouch PJ
J Neurosci; 2014 Jun; 34(23):8021-31. PubMed ID: 24899723
[TBL] [Abstract][Full Text] [Related]
5. Cu
Hilton JB; Mercer SW; Lim NK; Faux NG; Buncic G; Beckman JS; Roberts BR; Donnelly PS; White AR; Crouch PJ
Sci Rep; 2017 Feb; 7():42292. PubMed ID: 28205575
[TBL] [Abstract][Full Text] [Related]
6. Diacetylbis(N(4)-methylthiosemicarbazonato) copper(II) (CuII(atsm)) protects against peroxynitrite-induced nitrosative damage and prolongs survival in amyotrophic lateral sclerosis mouse model.
Soon CPW; Donnelly PS; Turner BJ; Hung LW; Crouch PJ; Sherratt NA; Tan JL; Lim NK; Lam L; Bica L; Lim S; Hickey JL; Morizzi J; Powell A; Finkelstein DI; Culvenor JG; Masters CL; Duce J; White AR; Barnham KJ; Li QX
J Biol Chem; 2011 Dec; 286(51):44035-44044. PubMed ID: 22033929
[TBL] [Abstract][Full Text] [Related]
7. Copper-ATSM as a Treatment for ALS: Support from Mutant SOD1 Models and Beyond.
Nikseresht S; Hilton JBW; Kysenius K; Liddell JR; Crouch PJ
Life (Basel); 2020 Nov; 10(11):. PubMed ID: 33158182
[TBL] [Abstract][Full Text] [Related]
8. Therapeutic effects of CuII(atsm) in the SOD1-G37R mouse model of amyotrophic lateral sclerosis.
McAllum EJ; Lim NK; Hickey JL; Paterson BM; Donnelly PS; Li QX; Liddell JR; Barnham KJ; White AR; Crouch PJ
Amyotroph Lateral Scler Frontotemporal Degener; 2013 Dec; 14(7-8):586-90. PubMed ID: 23952668
[TBL] [Abstract][Full Text] [Related]
9. Copper and zinc metallation status of copper-zinc superoxide dismutase from amyotrophic lateral sclerosis transgenic mice.
Lelie HL; Liba A; Bourassa MW; Chattopadhyay M; Chan PK; Gralla EB; Miller LM; Borchelt DR; Valentine JS; Whitelegge JP
J Biol Chem; 2011 Jan; 286(4):2795-806. PubMed ID: 21068388
[TBL] [Abstract][Full Text] [Related]
10. A copper-deficient form of mutant Cu/Zn-superoxide dismutase as an early pathological species in amyotrophic lateral sclerosis.
Tokuda E; Nomura T; Ohara S; Watanabe S; Yamanaka K; Morisaki Y; Misawa H; Furukawa Y
Biochim Biophys Acta Mol Basis Dis; 2018 Jun; 1864(6 Pt A):2119-2130. PubMed ID: 29551730
[TBL] [Abstract][Full Text] [Related]
11. Comparing effects of microgravity and amyotrophic lateral sclerosis in the mouse ventral lumbar spinal cord.
Yoshikawa M; Ishikawa C; Li H; Kudo T; Shiba D; Shirakawa M; Muratani M; Takahashi S; Aizawa S; Shiga T
Mol Cell Neurosci; 2022 Jul; 121():103745. PubMed ID: 35660087
[TBL] [Abstract][Full Text] [Related]
12. Endogenous Cu in the central nervous system fails to satiate the elevated requirement for Cu in a mutant SOD1 mouse model of ALS.
Hilton JB; White AR; Crouch PJ
Metallomics; 2016 Sep; 8(9):1002-11. PubMed ID: 27357743
[TBL] [Abstract][Full Text] [Related]
13. Overexpression of metallothionein-I, a copper-regulating protein, attenuates intracellular copper dyshomeostasis and extends lifespan in a mouse model of amyotrophic lateral sclerosis caused by mutant superoxide dismutase-1.
Tokuda E; Okawa E; Watanabe S; Ono S
Hum Mol Genet; 2014 Mar; 23(5):1271-85. PubMed ID: 24163136
[TBL] [Abstract][Full Text] [Related]
14. Histological evidence of protein aggregation in mutant SOD1 transgenic mice and in amyotrophic lateral sclerosis neural tissues.
Watanabe M; Dykes-Hoberg M; Culotta VC; Price DL; Wong PC; Rothstein JD
Neurobiol Dis; 2001 Dec; 8(6):933-41. PubMed ID: 11741389
[TBL] [Abstract][Full Text] [Related]
15. Overexpression of Abeta is associated with acceleration of onset of motor impairment and superoxide dismutase 1 aggregation in an amyotrophic lateral sclerosis mouse model.
Li QX; Mok SS; Laughton KM; McLean CA; Volitakis I; Cherny RA; Cheung NS; White AR; Masters CL
Aging Cell; 2006 Apr; 5(2):153-65. PubMed ID: 16626394
[TBL] [Abstract][Full Text] [Related]
16. Anatomical redistribution of endogenous copper in embryonic mice overexpressing SOD1.
Kysenius K; Hilton JB; Paul B; Hare DJ; Crouch PJ
Metallomics; 2019 Jan; 11(1):141-150. PubMed ID: 30255176
[TBL] [Abstract][Full Text] [Related]
17. Heat shock factor 1 over-expression protects against exposure of hydrophobic residues on mutant SOD1 and early mortality in a mouse model of amyotrophic lateral sclerosis.
Lin PY; Simon SM; Koh WK; Folorunso O; Umbaugh CS; Pierce A
Mol Neurodegener; 2013 Nov; 8():43. PubMed ID: 24256636
[TBL] [Abstract][Full Text] [Related]
18. Dysregulation of intracellular copper homeostasis is common to transgenic mice expressing human mutant superoxide dismutase-1s regardless of their copper-binding abilities.
Tokuda E; Okawa E; Watanabe S; Ono S; Marklund SL
Neurobiol Dis; 2013 Jun; 54():308-19. PubMed ID: 23321002
[TBL] [Abstract][Full Text] [Related]
19. Misfolded SOD1 is not a primary component of sporadic ALS.
Da Cruz S; Bui A; Saberi S; Lee SK; Stauffer J; McAlonis-Downes M; Schulte D; Pizzo DP; Parone PA; Cleveland DW; Ravits J
Acta Neuropathol; 2017 Jul; 134(1):97-111. PubMed ID: 28247063
[TBL] [Abstract][Full Text] [Related]
20. Cortical hyperexcitability in mouse models and patients with amyotrophic lateral sclerosis is linked to noradrenaline deficiency.
Scekic-Zahirovic J; Benetton C; Brunet A; Ye X; Logunov E; Douchamps V; Megat S; Andry V; Kan VWY; Stuart-Lopez G; Gilet J; Guillot SJ; Dirrig-Grosch S; Gorin C; Trombini M; Dieterle S; Sinniger J; Fischer M; René F; Gunes Z; Kessler P; Dupuis L; Pradat PF; Goumon Y; Goutagny R; Marchand-Pauvert V; Liebscher S; Rouaux C
Sci Transl Med; 2024 Mar; 16(738):eadg3665. PubMed ID: 38478631
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]