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4. Homocystinuria due to cystathionine beta-synthase deficiency in Ireland: 25 years' experience of a newborn screened and treated population with reference to clinical outcome and biochemical control. Yap S; Naughten E J Inherit Metab Dis; 1998 Oct; 21(7):738-47. PubMed ID: 9819703 [TBL] [Abstract][Full Text] [Related]
5. Psychiatric manifestations of homocystinuria due to cystathionine beta-synthase deficiency: prevalence, natural history, and relationship to neurologic impairment and vitamin B6-responsiveness. Abbott MH; Folstein SE; Abbey H; Pyeritz RE Am J Med Genet; 1987 Apr; 26(4):959-69. PubMed ID: 3591841 [TBL] [Abstract][Full Text] [Related]
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9. Lenticular subluxation in a patient with homocystinuria undetected by neonatal screening. Cheng KH; Hung MC; Chen SJ; Kao CH; Niu DM J Chin Med Assoc; 2007 Dec; 70(12):562-4. PubMed ID: 18194900 [TBL] [Abstract][Full Text] [Related]
10. Vascular complications of severe hyperhomocysteinemia in patients with homocystinuria due to cystathionine beta-synthase deficiency: effects of homocysteine-lowering therapy. Yap S; Naughten ER; Wilcken B; Wilcken DE; Boers GH Semin Thromb Hemost; 2000; 26(3):335-40. PubMed ID: 11011851 [TBL] [Abstract][Full Text] [Related]
11. High prevalence of cerebral venous sinus thrombosis (CVST) as presentation of cystathionine beta-synthase deficiency in childhood: molecular and clinical findings of Turkish probands. Karaca M; Hismi B; Ozgul RK; Karaca S; Yilmaz DY; Coskun T; Sivri HS; Tokatli A; Dursun A Gene; 2014 Jan; 534(2):197-203. PubMed ID: 24211323 [TBL] [Abstract][Full Text] [Related]
12. Strategies for the treatment of cystathionine beta-synthase deficiency: the experience of the Willink Biochemical Genetics Unit over the past 30 years. Walter JH; Wraith JE; White FJ; Bridge C; Till J Eur J Pediatr; 1998 Apr; 157 Suppl 2():S71-6. PubMed ID: 9587030 [TBL] [Abstract][Full Text] [Related]
13. A cautionary tale of pyridoxine toxicity in cystathionine beta-synthase deficiency detected by two-tier newborn screening highlights the need for clear pyridoxine dosing guidelines. Ames EG; Scott AJ; Pappas KB; Moloney SM; Conway RL; Ahmad A Am J Med Genet A; 2020 Nov; 182(11):2704-2708. PubMed ID: 32820583 [TBL] [Abstract][Full Text] [Related]
14. Electroencephalographic abnormalities in homocystinuria due to cystathionine synthase deficiency. Del Giudice E; Striano S; Andria G Clin Neurol Neurosurg; 1983; 85(3):165-8. PubMed ID: 6315290 [TBL] [Abstract][Full Text] [Related]
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