These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
22. Pharmacotherapy of the ion transport defect in cystic fibrosis: role of purinergic receptor agonists and other potential therapeutics. Kunzelmann K; Mall M Am J Respir Med; 2003; 2(4):299-309. PubMed ID: 14719996 [TBL] [Abstract][Full Text] [Related]
23. Low temperature and chemical rescue affect molecular proximity of DeltaF508-cystic fibrosis transmembrane conductance regulator (CFTR) and epithelial sodium channel (ENaC). Qadri YJ; Cormet-Boyaka E; Rooj AK; Lee W; Parpura V; Fuller CM; Berdiev BK J Biol Chem; 2012 May; 287(20):16781-90. PubMed ID: 22442149 [TBL] [Abstract][Full Text] [Related]
24. Cystic Fibrosis Reprograms Airway Epithelial IL-33 Release and Licenses IL-33-Dependent Inflammation. Cook DP; Thomas CM; Wu AY; Rusznak M; Zhang J; Zhou W; Cephus JY; Gibson-Corley KN; Polosukhin VV; Norlander AE; Newcomb DC; Stoltz DA; Peebles RS Am J Respir Crit Care Med; 2023 Jun; 207(11):1486-1497. PubMed ID: 36952660 [No Abstract] [Full Text] [Related]
25. Bioelectric characterization of epithelia from neonatal CFTR knockout ferrets. Fisher JT; Tyler SR; Zhang Y; Lee BJ; Liu X; Sun X; Sui H; Liang B; Luo M; Xie W; Yi Y; Zhou W; Song Y; Keiser N; Wang K; de Jonge HR; Engelhardt JF Am J Respir Cell Mol Biol; 2013 Nov; 49(5):837-44. PubMed ID: 23782101 [TBL] [Abstract][Full Text] [Related]
26. AMPK agonists ameliorate sodium and fluid transport and inflammation in cystic fibrosis airway epithelial cells. Myerburg MM; King JD; Oyster NM; Fitch AC; Magill A; Baty CJ; Watkins SC; Kolls JK; Pilewski JM; Hallows KR Am J Respir Cell Mol Biol; 2010 Jun; 42(6):676-84. PubMed ID: 19617399 [TBL] [Abstract][Full Text] [Related]
28. The ΔF508-CFTR mutation inhibits wild-type CFTR processing and function when co-expressed in human airway epithelia and in mouse nasal mucosa. Tucker TA; Fortenberry JA; Zsembery A; Schwiebert LM; Schwiebert EM BMC Physiol; 2012 Sep; 12():12. PubMed ID: 22999299 [TBL] [Abstract][Full Text] [Related]
29. Control of the proinflammatory state in cystic fibrosis lung epithelial cells by genes from the TNF-alphaR/NFkappaB pathway. Eidelman O; Srivastava M; Zhang J; Leighton X; Murtie J; Jozwik C; Jacobson K; Weinstein DL; Metcalf EL; Pollard HB Mol Med; 2001 Aug; 7(8):523-34. PubMed ID: 11591888 [TBL] [Abstract][Full Text] [Related]
30. Modulator Combination Improves In Vitro the Microrheological Properties of the Airway Surface Liquid of Cystic Fibrosis Airway Epithelia. Ludovico A; Moran O; Baroni D Int J Mol Sci; 2022 Sep; 23(19):. PubMed ID: 36232697 [TBL] [Abstract][Full Text] [Related]
31. Effects of cystic fibrosis transmembrane conductance regulator and DeltaF508CFTR on inflammatory response, ER stress, and Ca2+ of airway epithelia. Hybiske K; Fu Z; Schwarzer C; Tseng J; Do J; Huang N; Machen TE Am J Physiol Lung Cell Mol Physiol; 2007 Nov; 293(5):L1250-60. PubMed ID: 17827250 [TBL] [Abstract][Full Text] [Related]
36. Defective CFTR induces aggresome formation and lung inflammation in cystic fibrosis through ROS-mediated autophagy inhibition. Luciani A; Villella VR; Esposito S; Brunetti-Pierri N; Medina D; Settembre C; Gavina M; Pulze L; Giardino I; Pettoello-Mantovani M; D'Apolito M; Guido S; Masliah E; Spencer B; Quaratino S; Raia V; Ballabio A; Maiuri L Nat Cell Biol; 2010 Sep; 12(9):863-75. PubMed ID: 20711182 [TBL] [Abstract][Full Text] [Related]
37. Modulation of Ion Transport to Restore Airway Hydration in Cystic Fibrosis. Reihill JA; Douglas LEJ; Martin SL Genes (Basel); 2021 Mar; 12(3):. PubMed ID: 33810137 [TBL] [Abstract][Full Text] [Related]
38. Lack of correlation between CFTR expression, CFTR Cl- currents, amiloride-sensitive Na+ conductance, and cystic fibrosis phenotype. Beck S; Kühr J; Schütz VV; Seydewitz HH; Brandis M; Greger R; Kunzelmann K Pediatr Pulmonol; 1999 Apr; 27(4):251-9. PubMed ID: 10230924 [TBL] [Abstract][Full Text] [Related]
39. Airway surface hyperviscosity and defective mucociliary transport by IL-17/TNF-α are corrected by β-adrenergic stimulus. Guidone D; Buccirossi M; Scudieri P; Genovese M; Sarnataro S; De Cegli R; Cresta F; Terlizzi V; Planelles G; Crambert G; Sermet I; Galietta LJ JCI Insight; 2022 Nov; 7(22):. PubMed ID: 36219481 [TBL] [Abstract][Full Text] [Related]
40. Spliceosome-mediated RNA trans-splicing with recombinant adeno-associated virus partially restores cystic fibrosis transmembrane conductance regulator function to polarized human cystic fibrosis airway epithelial cells. Liu X; Luo M; Zhang LN; Yan Z; Zak R; Ding W; Mansfield SG; Mitchell LG; Engelhardt JF Hum Gene Ther; 2005 Sep; 16(9):1116-23. PubMed ID: 16149910 [TBL] [Abstract][Full Text] [Related] [Previous] [Next] [New Search]