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4. Neural-specific alterations in glycosphingolipid biosynthesis and cell signaling associated with two human ganglioside GM3 synthase deficiency variants. Dookwah M; Wagner SK; Ishihara M; Yu SH; Ulrichs H; Kulik MJ; Zeltner N; Dalton S; Strauss KA; Aoki K; Steet R; Tiemeyer M Hum Mol Genet; 2023 Dec; 32(24):3323-3341. PubMed ID: 37676252 [TBL] [Abstract][Full Text] [Related]
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6. Early growth and development impairments in patients with ganglioside GM3 synthase deficiency. Wang H; Wang A; Wang D; Bright A; Sency V; Zhou A; Xin B Clin Genet; 2016 May; 89(5):625-9. PubMed ID: 26649472 [TBL] [Abstract][Full Text] [Related]
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9. Regulation of ganglioside composition and synthesis is different in developing chick retinal pigment epithelium and neural retina. Daniotti JL; Landa CA; Maccioni HJ J Neurochem; 1994 Mar; 62(3):1131-6. PubMed ID: 7509373 [TBL] [Abstract][Full Text] [Related]
10. Ganglioside GM3 Synthase Deficiency in Mouse Models and Human Patients. Inamori KI; Inokuchi JI Int J Mol Sci; 2022 May; 23(10):. PubMed ID: 35628171 [TBL] [Abstract][Full Text] [Related]
11. Glycosylation pathways in the biosynthesis of gangliosides in melanoma and neuroblastoma cells: relative glycosyltransferase levels determine ganglioside patterns. Ruan S; Lloyd KO Cancer Res; 1992 Oct; 52(20):5725-31. PubMed ID: 1394196 [TBL] [Abstract][Full Text] [Related]
12. Developmental changes in ganglioside composition and synthesis in embryonic rat brain. Yu RK; Macala LJ; Taki T; Weinfield HM; Yu FS J Neurochem; 1988 Jun; 50(6):1825-9. PubMed ID: 3131485 [TBL] [Abstract][Full Text] [Related]
14. Synthetic GM1 improves motor and memory dysfunctions in mice with monoallelic or biallelic disruption of GM3 synthase. Chowdhury S; Kumar R; Zepeda E; DeFrees S; Ledeen R FEBS Open Bio; 2023 Sep; 13(9):1651-1657. PubMed ID: 37401916 [TBL] [Abstract][Full Text] [Related]
15. Roles for UDP-GlcNAc 2-epimerase/ManNAc 6-kinase outside of sialic acid biosynthesis: modulation of sialyltransferase and BiP expression, GM3 and GD3 biosynthesis, proliferation, and apoptosis, and ERK1/2 phosphorylation. Wang Z; Sun Z; Li AV; Yarema KJ J Biol Chem; 2006 Sep; 281(37):27016-28. PubMed ID: 16847058 [TBL] [Abstract][Full Text] [Related]
16. Modification of Ganglioside Content of Human Gastric Epithelial Cell Membrane Decreases Helicobacter pylori Adhesion. Rivas-Serna IM; Mazurak VC; Keelan M; Clandinin MT J Pediatr Gastroenterol Nutr; 2017 Oct; 65(4):456-461. PubMed ID: 28945209 [TBL] [Abstract][Full Text] [Related]
17. Ganglioside GM3 deficiency enhances mast cell sensitivity. Komuro M; Mizugaki H; Nagane M; Morimoto M; Fukuyama T; Ogihara K; Naya Y; Yokomori E; Kaneshima K; Kawakami Y; Kamiie J; Shibata Y; Suzuki M; Shimizu T; Kawashima N; Okamoto M; Ikeda T; Yamashita T FEBS J; 2023 Sep; 290(17):4268-4280. PubMed ID: 37098812 [TBL] [Abstract][Full Text] [Related]
18. Activities of five different sialyltransferases in fish and rat brains. Freischütz B; Saito M; Rahmann H; Yu RK J Neurochem; 1994 May; 62(5):1965-73. PubMed ID: 8158143 [TBL] [Abstract][Full Text] [Related]
19. Deficiency of ganglioside biosynthesis in metastatic human melanoma cells: relevance of CMP-NeuAc:LacCer alpha 2-3 sialyltransferase (GM3 synthase). Zebda N; Pedron S; Rebbaa A; Portoukalian J; Berthier-Vergnes O FEBS Lett; 1995 Apr; 362(2):161-4. PubMed ID: 7720864 [TBL] [Abstract][Full Text] [Related]