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8. Lactic acidosis in biotin-responsive multiple carboxylase deficiency caused by holocarboxylase synthetase deficiency of early and late onset. Sherwood WG; Saunders M; Robinson BH; Brewster T; Gravel RA J Pediatr; 1982 Oct; 101(4):546-50. PubMed ID: 6811711 [TBL] [Abstract][Full Text] [Related]
11. Five patients with a biotin-responsive defect in holocarboxylase formation: evaluation of responsiveness to biotin therapy in vivo and comparative biochemical studies in vitro. Suormala T; Fowler B; Duran M; Burtscher A; Fuchshuber A; Tratzmüller R; Lenze MJ; Raab K; Baur B; Wick H; Baumgartner R Pediatr Res; 1997 May; 41(5):666-73. PubMed ID: 9128289 [TBL] [Abstract][Full Text] [Related]
12. Enzyme studies in combined carboxylase deficiency. Bartlett K; Ghneim HK; Stirk JH; Wastell HJ; Sherratt HS; Leonard JV Ann N Y Acad Sci; 1985; 447():235-51. PubMed ID: 2861780 [No Abstract] [Full Text] [Related]
13. Biochemical evidence for diverse etiologies in biotin-responsive multiple carboxylase deficiency. Packman S; Caswell NM; Baker H Biochem Genet; 1982 Feb; 20(1-2):17-28. PubMed ID: 6807281 [TBL] [Abstract][Full Text] [Related]
14. Biotin-reversible neurodegenerative disease in infancy. Low LC; Stephenson JB; Bartlett K; Seakins JW; Shaikh SA Aust Paediatr J; 1986 Feb; 22(1):65-8. PubMed ID: 3087340 [TBL] [Abstract][Full Text] [Related]
15. Heterogeneity of holocarboxylase synthetase in patients with biotin-responsive multiple carboxylase deficiency. Burri BJ; Sweetman L; Nyhan WL Am J Hum Genet; 1985 Mar; 37(2):326-37. PubMed ID: 3920902 [TBL] [Abstract][Full Text] [Related]
17. Prenatal administration of biotin in biotin responsive multiple carboxylase deficiency. Roth KS; Yang W; Allan L; Saunders M; Gravel RA; Dakshinamurti K Pediatr Res; 1982 Feb; 16(2):126-9. PubMed ID: 6799930 [TBL] [Abstract][Full Text] [Related]
18. A combined defect of three mitochondrial carboxylases presenting as biotin-responsive 3-methylcrotonyl glycinuria and 3-hydroxyisovaleric aciduria. Bartlett K; Ng H; Leonard JV Clin Chim Acta; 1980 Jan; 100(2):183-6. PubMed ID: 6766095 [TBL] [Abstract][Full Text] [Related]
19. Deficient acetyl CoA carboxylase activity in multiple carboxylase deficiency. Feldman GL; Wolf B Clin Chim Acta; 1981 Apr; 111(2-3):147-51. PubMed ID: 6112081 [TBL] [Abstract][Full Text] [Related]
20. Biotinidase deficiency. Wolf B; Heard GS; McVoy JR; Grier RE Ann N Y Acad Sci; 1985; 447():252-62. PubMed ID: 3925856 [No Abstract] [Full Text] [Related] [Next] [New Search]