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6. Evidence that C9ORF72 Dipeptide Repeat Proteins Associate with U2 snRNP to Cause Mis-splicing in ALS/FTD Patients. Yin S; Lopez-Gonzalez R; Kunz RC; Gangopadhyay J; Borufka C; Gygi SP; Gao FB; Reed R Cell Rep; 2017 Jun; 19(11):2244-2256. PubMed ID: 28614712 [TBL] [Abstract][Full Text] [Related]
7. Cell-to-Cell Transmission of Dipeptide Repeat Proteins Linked to C9orf72-ALS/FTD. Westergard T; Jensen BK; Wen X; Cai J; Kropf E; Iacovitti L; Pasinelli P; Trotti D Cell Rep; 2016 Oct; 17(3):645-652. PubMed ID: 27732842 [TBL] [Abstract][Full Text] [Related]
8. Poly(ADP-ribose) promotes toxicity of Gao J; Mewborne QT; Girdhar A; Sheth U; Coyne AN; Punathil R; Kang BG; Dasovich M; Veire A; DeJesus Hernandez M; Liu S; Shi Z; Dafinca R; Fouquerel E; Talbot K; Kam TI; Zhang YJ; Dickson D; Petrucelli L; van Blitterswijk M; Guo L; Dawson TM; Dawson VL; Leung AKL; Lloyd TE; Gendron TF; Rothstein JD; Zhang K Sci Transl Med; 2022 Sep; 14(662):eabq3215. PubMed ID: 36103513 [TBL] [Abstract][Full Text] [Related]
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10. C9orf72-associated dipeptide protein repeats form A11-positive oligomers in amyotrophic lateral sclerosis and frontotemporal dementia. Bhatt N; Puangmalai N; Sengupta U; Jerez C; Kidd M; Gandhi S; Kayed R J Biol Chem; 2024 Feb; 300(2):105628. PubMed ID: 38295729 [TBL] [Abstract][Full Text] [Related]
11. Dipeptide repeat proteins inhibit homology-directed DNA double strand break repair in C9ORF72 ALS/FTD. Andrade NS; Ramic M; Esanov R; Liu W; Rybin MJ; Gaidosh G; Abdallah A; Del'Olio S; Huff TC; Chee NT; Anatha S; Gendron TF; Wahlestedt C; Zhang Y; Benatar M; Mueller C; Zeier Z Mol Neurodegener; 2020 Feb; 15(1):13. PubMed ID: 32093728 [TBL] [Abstract][Full Text] [Related]
12. Synaptic dysfunction and altered excitability in C9ORF72 ALS/FTD. Starr A; Sattler R Brain Res; 2018 Aug; 1693(Pt A):98-108. PubMed ID: 29453960 [TBL] [Abstract][Full Text] [Related]
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17. Modifiers of C9orf72 dipeptide repeat toxicity connect nucleocytoplasmic transport defects to FTD/ALS. Jovičić A; Mertens J; Boeynaems S; Bogaert E; Chai N; Yamada SB; Paul JW; Sun S; Herdy JR; Bieri G; Kramer NJ; Gage FH; Van Den Bosch L; Robberecht W; Gitler AD Nat Neurosci; 2015 Sep; 18(9):1226-9. PubMed ID: 26308983 [TBL] [Abstract][Full Text] [Related]
18. C9orf72 Dipeptide Repeats Impair the Assembly, Dynamics, and Function of Membrane-Less Organelles. Lee KH; Zhang P; Kim HJ; Mitrea DM; Sarkar M; Freibaum BD; Cika J; Coughlin M; Messing J; Molliex A; Maxwell BA; Kim NC; Temirov J; Moore J; Kolaitis RM; Shaw TI; Bai B; Peng J; Kriwacki RW; Taylor JP Cell; 2016 Oct; 167(3):774-788.e17. PubMed ID: 27768896 [TBL] [Abstract][Full Text] [Related]
19. C9orf72-associated arginine-rich dipeptide repeats induce RNA-dependent nuclear accumulation of Staufen in neurons. Kim ES; Chung CG; Park JH; Ko BS; Park SS; Kim YH; Cha IJ; Kim J; Ha CM; Kim HJ; Lee SB Hum Mol Genet; 2021 Jun; 30(12):1084-1100. PubMed ID: 33783499 [TBL] [Abstract][Full Text] [Related]
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