These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
28. Heparan sulfate and dermatan sulfate from the liver of a patient with Hurler syndrome: high performance liquid chromatography of their degradation products after incubation with alpha-L-iduronidase-deficient fibroblasts. Minami R; Fujibayashi S; Igarashi C; Ishikawa Y; Wagatsuma K; Nakao T; Tsugawa S Clin Chim Acta; 1984 Feb; 137(2):179-87. PubMed ID: 6231139 [TBL] [Abstract][Full Text] [Related]
29. Use of 4-trifluoromethylumbelliferyl-alpha-L-iduronide as a new substrate for detection of alpha-L-iduronidase deficiency in human tissues and for rapid prenatal diagnosis of Hurler disease. Tsvetkova IV; Karpova EA; Voznyi YV; Zolotukhina TV; Biryukov VV; Semyachkina AN J Inherit Metab Dis; 1991; 14(2):134-9. PubMed ID: 1909400 [TBL] [Abstract][Full Text] [Related]
30. Recognition and receptor-mediated uptake of a lysosomal enzyme, alpha-l-iduronidase, by cultured human fibroblasts. Sando GN; Neufeld EF Cell; 1977 Nov; 12(3):619-27. PubMed ID: 922886 [No Abstract] [Full Text] [Related]
31. Studies on the alpha-L-iduronidase activity of beta-glucuronidase preparations from bovine liver, rat liver, and rat preputial gland. Kosaka H; Isemura M; Ono T; Nishimura Y; Kato K J Biochem; 1980 Jul; 88(1):69-75. PubMed ID: 7410341 [TBL] [Abstract][Full Text] [Related]
32. [Use of 4-methylumbelliferryl-alpha-L-iduronide and 4-trifluoromethylumbelliferryl-alpha-L-iduronide for detecting alpha-L-iduronidase deficiencies in human tissue and for rapid prenatal diagnosis of Hurler disease]. Tsvetkova IV; Karpova EA; Voznyĭ IaV; Zolotukhina TV; Biriukov VB; Semiachkina AN Vopr Med Khim; 1991; 37(1):74-7. PubMed ID: 1907053 [TBL] [Abstract][Full Text] [Related]
33. Human alpha-L-iduronidase. Catalytic properties and an integrated role in the lysosomal degradation of heparan sulphate. Freeman C; Hopwood JJ Biochem J; 1992 Mar; 282 ( Pt 3)(Pt 3):899-908. PubMed ID: 1554373 [TBL] [Abstract][Full Text] [Related]
34. A canine model of human alpha-L-iduronidase deficiency. Spellacy E; Shull RM; Constantopoulos G; Neufeld EF Proc Natl Acad Sci U S A; 1983 Oct; 80(19):6091-5. PubMed ID: 6412235 [TBL] [Abstract][Full Text] [Related]
35. Toward reducing immunogenicity of enzyme replacement therapy: altering the specificity of human β-glucuronidase to compensate for α-iduronidase deficiency. Chuang HY; Suen CS; Hwang MJ; Roffler SR Protein Eng Des Sel; 2015 Nov; 28(11):519-29. PubMed ID: 26319005 [TBL] [Abstract][Full Text] [Related]
36. Fluorometric measurement of urinary alpha-L-iduronidase activity. Isemura M; Kosaka H; Ikenaka T; Kido R; Yoshimura T J Biochem; 1978 Sep; 84(3):627-32. PubMed ID: 102641 [TBL] [Abstract][Full Text] [Related]
37. Residual α-L-iduronidase activity in fibroblasts of mild to severe Mucopolysaccharidosis type I patients. Oussoren E; Keulemans J; van Diggelen OP; Oemardien LF; Timmermans RG; van der Ploeg AT; Ruijter GJ Mol Genet Metab; 2013 Aug; 109(4):377-81. PubMed ID: 23786846 [TBL] [Abstract][Full Text] [Related]