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4. Biosynthesis of triacylglycerols containing isovaleric acid. Malins DC; Robisch PA; Varanasi U Biochem Biophys Res Commun; 1972 Jul; 48(2):314-9. PubMed ID: 5043185 [No Abstract] [Full Text] [Related]
5. Possibility of inborn defect in isovalericacidaemia involving altered enzyme specificity rather than total inactivity. Engel PC Nature; 1974 Mar; 248(5444):140-2. PubMed ID: 4818917 [No Abstract] [Full Text] [Related]
6. Leucine catabolism and CO2 fixation into fatty acids by Tetrahymena: evidence for two pools of CO2. Borowitz M; Raugi G; Liang T; Blum JJ J Biol Chem; 1977 May; 252(10):3402-7. PubMed ID: 405384 [No Abstract] [Full Text] [Related]
8. The isolation and identification of N-isovalerylglycine from urine of patients with isovaleric acidemia. Tanaka K; Isselbacher KJ J Biol Chem; 1967 Jun; 242(12):2966-72. PubMed ID: 6027258 [No Abstract] [Full Text] [Related]
9. Hypoglycin A: a specific inhibitor of isovaleryl CoA dehydrogenase. Tanaka K; Miller EM; Isselbacher KJ Proc Natl Acad Sci U S A; 1971 Jan; 68(1):20-4. PubMed ID: 5276292 [TBL] [Abstract][Full Text] [Related]
10. Acute neonatal isovaleric acidemia. A report of two cases. Spirer Z; Swirsky-Fein S; Zakut V; Legum C; Bogair N; Charles R; Gil-Av E Isr J Med Sci; 1975 Oct; 11(10):1005-10. PubMed ID: 1193830 [TBL] [Abstract][Full Text] [Related]
11. Localisation of enzymic defect in propionicacidaemia. Gompertz D; Storrs CN; Bau DC; Peters TJ; Hughes EA Lancet; 1970 May; 1(7657):1140-3. PubMed ID: 4192098 [No Abstract] [Full Text] [Related]
12. Prenatal diagnosis and a case report of isovaleric acidaemia. Blaskovics ME; Ng WG; Donnell GN J Inherit Metab Dis; 1978; 1(1):9-11. PubMed ID: 117238 [No Abstract] [Full Text] [Related]
13. Mechanisms of inhibition of fatty acid oxidation by pent-4-enoic acid: evidence against the coenzyme A-depletion hypothesis. Holland PC; Sherratt HS Biochem J; 1972 Apr; 127(3):79P. PubMed ID: 5076223 [No Abstract] [Full Text] [Related]
14. Isovaleric acidemia. Can Med Assoc J; 1967 Nov; 97(20):1230-1. PubMed ID: 6058164 [No Abstract] [Full Text] [Related]
15. Organic aciduria associated with isovaleric acidemia. Wysocki SJ; French NP; Grauaug A Clin Chem; 1983 May; 29(5):1002-3. PubMed ID: 6839449 [No Abstract] [Full Text] [Related]
18. Isovaleric acidemia: identification of isovalerate, isovalerylglycine, and 3-hydroxyisovalerate in urine of a patient previously reported as having butyric and hexanoic acidemia. Ando T; Nyhan WL; Bachmann C; Rasmussen K; Scott R; Smith EK J Pediatr; 1973 Feb; 82(2):243-8. PubMed ID: 4684367 [No Abstract] [Full Text] [Related]
19. [Congenital metabolic acidosis in the postnatal period]. Schreier K; Porath U Dtsch Med Wochenschr; 1978 Jun; 103(22):943-7. PubMed ID: 207503 [No Abstract] [Full Text] [Related]