These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
22. [Neonatal form of isovaleric acidemia. Apropos of a new case]. Beauvais P; Peter MO; Barbier B Arch Fr Pediatr; 1985; 42(7):531-3. PubMed ID: 4083972 [TBL] [Abstract][Full Text] [Related]
23. 3-Hydroxyisoheptanoic acid: a new metabolite in isovaleric acidemia. Lehnert W Clin Chim Acta; 1981 Jun; 113(1):101-3. PubMed ID: 7237839 [No Abstract] [Full Text] [Related]
24. Excretion of N-isovalerylglutamic acid in isovaleric acidemia. Lehnert W Clin Chim Acta; 1981 Oct; 116(2):249-52. PubMed ID: 7296890 [No Abstract] [Full Text] [Related]
25. Child with a defect in leucine metabolism associated with beta-hydroxyisovaleric aciduria and beta-methylcrotonylglycinuria. Gompertz D; Bartlett K; Blair D; Stern CM Arch Dis Child; 1973 Dec; 48(12):975-7. PubMed ID: 4765660 [No Abstract] [Full Text] [Related]
27. Amino-acid depletion induced by abnormal amino-acid conjugation and protein restriction in isovaleric acidemia. Loots DT; Mienie LJ; Erasmus E Eur J Clin Nutr; 2007 Nov; 61(11):1323-7. PubMed ID: 17299485 [TBL] [Abstract][Full Text] [Related]
28. [A case of isovaleric acidemia]. Guibaud P; Divry P; Dubois Y; Collombel C; Larbre F Arch Fr Pediatr; 1973; 30(6):633-45. PubMed ID: 4805283 [No Abstract] [Full Text] [Related]
29. Glycine therapy in isovaleric acidemia. Yudkoff M; Cohn RM; Puschak R; Rothman R; Segal S J Pediatr; 1978 May; 92(5):813-7. PubMed ID: 641635 [TBL] [Abstract][Full Text] [Related]
30. Neonatal lethargy due to isovaleric acidemia and hyperammonemia. Mendiola J; Robotham JL; Liehr JG; Williams JC Tex Med; 1984 Jan; 80(1):52-4. PubMed ID: 6695347 [No Abstract] [Full Text] [Related]
31. Diagnosis of isovaleric acidemia in cultured fibroblasts. Shih VE; Mandell R; Tanaka K Clin Chim Acta; 1973 Nov; 48(4):437-9. PubMed ID: 4761592 [No Abstract] [Full Text] [Related]
32. Unusual Metabolites in a Patient with Isovaleric Acidemia. De Biase I; Pasquali M; Asamoah A Clin Chem; 2019 Apr; 65(4):595-597. PubMed ID: 30923063 [No Abstract] [Full Text] [Related]
33. [2-Methyl-3-oxovaleric acid: a characteristic metabolite in propionic acidemia]. Lehnert W; Junker A Clin Chim Acta; 1980 May; 104(1):47-51. PubMed ID: 7389125 [TBL] [Abstract][Full Text] [Related]
34. Endogenous catabolism as source of toxic metabolites in isovaleric acidemia. Pollitt RJ J Pediatr; 1987 Sep; 111(3):477-8. PubMed ID: 3625423 [No Abstract] [Full Text] [Related]
35. Different outcome in isovaleric acidemia might be related to unsatisfactory diet compliance. Castorina M; Rigante D; Antuzzi D; Sciascia Cannizzaro G; Ricci R Scand J Gastroenterol; 2008; 43(6):767-8. PubMed ID: 18569998 [No Abstract] [Full Text] [Related]
36. NMR spectroscopic studies on the late onset form of 3-methylglutaconic aciduria type I and other defects in leucine metabolism. Engelke UF; Kremer B; Kluijtmans LA; van der Graaf M; Morava E; Loupatty FJ; Wanders RJ; Moskau D; Loss S; van den Bergh E; Wevers RA NMR Biomed; 2006 Apr; 19(2):271-8. PubMed ID: 16541463 [TBL] [Abstract][Full Text] [Related]
37. Beta-methylcrotonyl-CoA carboxylase deficiency: a new metabolic error in leucine degradation. Stokke O; Eldjarn L; Jellum E; Pande H; Waaler PE Pediatrics; 1972 May; 49(5):726-35. PubMed ID: 5035417 [No Abstract] [Full Text] [Related]
38. Isovaleric acidemia. Pascarella A; Rosa M; della Casa R; Andria G; Parenti G J Pediatr Endocrinol Metab; 2011; 24(5-6):399. PubMed ID: 21823546 [No Abstract] [Full Text] [Related]
39. Isovaleric acidemia: identification of isovalerate, isovalerylglycine, and 3-hydroxyisovalerate in urine of a patient previously reported as having butyric and hexanoic acidemia. Ando T; Nyhan WL; Bachmann C; Rasmussen K; Scott R; Smith EK J Pediatr; 1973 Feb; 82(2):243-8. PubMed ID: 4684367 [No Abstract] [Full Text] [Related]