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2. Thiamine non-responsive intermittent branched-chain ketoaciduria in a Laotian child. Pueschel SM J Inherit Metab Dis; 1986; 9(1):72. PubMed ID: 3088326 [No Abstract] [Full Text] [Related]
3. Evaluation of branched-chain amino acid intake in children with maple syrup urine disease and methylmalonic aciduria. Parsons HG; Carter RJ; Unrath M; Snyder FF J Inherit Metab Dis; 1990; 13(2):125-36. PubMed ID: 2116544 [TBL] [Abstract][Full Text] [Related]
4. [Intermittent branched--chain ketoacidurie in ketotic hypoglycemia: investigations to localize the biochemical defect (author's transl)]. Held KR; Sternowsky HJ; Singh S; Plettner C; Grüttner R Monatsschr Kinderheilkd (1902); 1976 Feb; 124(2):59-65. PubMed ID: 1256452 [TBL] [Abstract][Full Text] [Related]
5. Effects of thiamine in a patient with a variant form of branched-chian ketoaciduria. Duran M; Tielens AG; Wadman SK; Stigter JC; Kleijer WJ Acta Paediatr Scand; 1978 May; 67(3):367-72. PubMed ID: 654914 [TBL] [Abstract][Full Text] [Related]
6. High-performance liquid chromatographic separation of six essential amino acids and its use as an aid in the diagnosis of branched-chain ketoaciduria. Wassner SJ; Li JB J Chromatogr; 1982 Feb; 227(2):497-502. PubMed ID: 7061660 [No Abstract] [Full Text] [Related]
7. Absorption of keto-analogues of branched-chain amino acids from rat small intestine. Weber FL; Deak SB; Laine RA Gastroenterology; 1979 Jan; 76(1):62-70. PubMed ID: 758150 [No Abstract] [Full Text] [Related]
9. Disorders of the degradation of branched chain amino acids: what is new in clinics and laboratories? Sass JO J Inherit Metab Dis; 2012 Jan; 35(1):1. PubMed ID: 22139495 [No Abstract] [Full Text] [Related]
10. Hypervalinemia. A defect in valine transamination. Dancis J; Hutzler J; Tada K; Wada Y; Morikawa T; Arakawa T Pediatrics; 1967 Jun; 39(6):813-7. PubMed ID: 6067402 [No Abstract] [Full Text] [Related]
11. The mitochondrial branched-chain aminotransferase (AtBCAT-1) is capable to initiate degradation of leucine, isoleucine and valine in almost all tissues in Arabidopsis thaliana. Schuster J; Binder S Plant Mol Biol; 2005 Jan; 57(2):241-54. PubMed ID: 15821880 [TBL] [Abstract][Full Text] [Related]
12. The effects of branched-chain amino acid interactions on growth performance, blood metabolites, enzyme kinetics and transcriptomics in weaned pigs. Wiltafsky MK; Pfaffl MW; Roth FX Br J Nutr; 2010 Apr; 103(7):964-76. PubMed ID: 20196890 [TBL] [Abstract][Full Text] [Related]
13. Treatment of branched chain ketoaciduria (BCKA) during acute illness: approaches to the correction of the acidosis. Waisman HA; Smith BA; Brown ES; Gerritsen T Clin Pediatr (Phila); 1972 Jun; 11(6):360-3. PubMed ID: 5032163 [No Abstract] [Full Text] [Related]
14. Roles of branched-chain amino acids in metabolic regulation. Adibi SA J Lab Clin Med; 1980 Apr; 95(4):475-84. PubMed ID: 6102106 [No Abstract] [Full Text] [Related]
15. Common enzymes of branched-chain amino acid catabolism in Pseudomonas putida. Martin RR; Marshall VD; Sokatch JR; Unger L J Bacteriol; 1973 Jul; 115(1):198-204. PubMed ID: 4352175 [TBL] [Abstract][Full Text] [Related]
16. Clinical consequences of disorders in the intermediate metabolism of branched chain amino acids (valine, leucine and isoleucine). Mogoş T; Cheţa CP; Mincu IT Rom J Intern Med; 1994; 32(1):57-61. PubMed ID: 8081313 [TBL] [Abstract][Full Text] [Related]
17. Metabolism of branched-chain amino acids in starved rats: the role of hepatic tissue. Holecek M; Sprongl L; Tilser I Physiol Res; 2001; 50(1):25-33. PubMed ID: 11300224 [TBL] [Abstract][Full Text] [Related]
18. Vitamin B12-dependent methylmalonicaciduria: amino acid toxicity, long chain ketonuria, and protective effect of vitamin B12. Hsia YE; Lilljeqvist AC; Rosenberg LE Pediatrics; 1970 Oct; 46(4):497-507. PubMed ID: 5503685 [No Abstract] [Full Text] [Related]