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3. 2-Ethylhydracrylic acid: a newly described urinary organic acid. Mamer OA; Tjoa SS Clin Chim Acta; 1974 Sep; 55(2):199-204. PubMed ID: 4458986 [No Abstract] [Full Text] [Related]
4. Beta-ketothiolase deficiency as a cause of the "ketotic hyperglycinemia syndrome". Hillman RE; Keating JP Pediatrics; 1974 Feb; 53(2):221-5. PubMed ID: 4812006 [No Abstract] [Full Text] [Related]
5. The identification of tiglylglycine in the urine of a child with -methylcrotonylglycinuria. Gompertz D; Draffan GH Clin Chim Acta; 1972 Mar; 37():405-10. PubMed ID: 5022104 [No Abstract] [Full Text] [Related]
6. Hyperglycinemia with ketosis due to a defect in isoleucine metabolism: a preliminary report. Keating JP; Feigin RD; Tenenbaum SM; Hillman RE Pediatrics; 1972 Dec; 50(6):890-5. PubMed ID: 4636454 [No Abstract] [Full Text] [Related]
7. The occurrence of 2-hydroxyisovaleric acid in patients with lactic acidosis and ketoacidosis. Landaas S; Jakobs C Clin Chim Acta; 1977 Aug; 78(3):489-93. PubMed ID: 884872 [TBL] [Abstract][Full Text] [Related]
8. A defect in l-isoleucine metabolism associated with alpha-methyl-beta-hydroxybutyric and alpha-methylacetoacetic aciduria: quantitative in vivo and in vitro studies. Gompertz D; Saudubray JM; Charpentier C; Bartlett K; Goodey PA; Draffan GH Clin Chim Acta; 1974 Dec; 57(3):269-81. PubMed ID: 4434646 [No Abstract] [Full Text] [Related]
9. 2-Methylbutyryl-coenzyme A dehydrogenase deficiency: functional and molecular studies on a defect in isoleucine catabolism. Sass JO; Ensenauer R; Röschinger W; Reich H; Steuerwald U; Schirrmacher O; Engel K; Häberle J; Andresen BS; Mégarbané A; Lehnert W; Zschocke J Mol Genet Metab; 2008 Jan; 93(1):30-5. PubMed ID: 17945527 [TBL] [Abstract][Full Text] [Related]
10. [Congenital metabolic acidosis in the postnatal period]. Schreier K; Porath U Dtsch Med Wochenschr; 1978 Jun; 103(22):943-7. PubMed ID: 207503 [No Abstract] [Full Text] [Related]
11. Abnormal metabolites of isoleucine in a patient with propionyl-CoA carboxylase deficiency. Sweetman L; Weyler W; Nyhan WL; de Céspedes C; Loria AR; Estrada Y Biomed Mass Spectrom; 1978 Mar; 5(3):198-207. PubMed ID: 630060 [TBL] [Abstract][Full Text] [Related]
12. Beta-methylcrotonyl-CoA carboxylase deficiency: a new metabolic error in leucine degradation. Stokke O; Eldjarn L; Jellum E; Pande H; Waaler PE Pediatrics; 1972 May; 49(5):726-35. PubMed ID: 5035417 [No Abstract] [Full Text] [Related]
13. Accumulation of 3-hydroxyisobutyric acid, 2-methyl-3-hydroxybutyric acid and 3-hydroxyisovaleric acid in ketoacidosis. Landaas S Clin Chim Acta; 1975 Oct; 64(2):143-54. PubMed ID: 126826 [TBL] [Abstract][Full Text] [Related]
14. The identification of 3-keto-2-methylvaleric acid and 3-hydroxy-2-methylvaleric acid in a patient with propionic acidemia. Truscott RJ; Pullin CJ; Halpern B; Hammond J; Haan E; Danks DM Biomed Mass Spectrom; 1979 Jul; 6(7):294-300. PubMed ID: 486715 [TBL] [Abstract][Full Text] [Related]
15. Inhibition of glycine oxidation in cultured fibroblasts by isoleucine. Hillman RE; Sowers LH; Cohen JL Pediatr Res; 1973 Dec; 7(12):945-7. PubMed ID: 4753048 [No Abstract] [Full Text] [Related]
16. A combined defect of three mitochondrial carboxylases presenting as biotin-responsive 3-methylcrotonyl glycinuria and 3-hydroxyisovaleric aciduria. Bartlett K; Ng H; Leonard JV Clin Chim Acta; 1980 Jan; 100(2):183-6. PubMed ID: 6766095 [TBL] [Abstract][Full Text] [Related]