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4. Combined iminoglycinuria and cystine- and dibasic aminoaciduria in patients with propionic acidaemia and 3-methylcrotonylglycinuria. Purkiss P; Chalmers RA; Borud O J Inherit Metab Dis; 1980; 3(3):85-6. PubMed ID: 6775144 [TBL] [Abstract][Full Text] [Related]
5. A combined defect of three mitochondrial carboxylases presenting as biotin-responsive 3-methylcrotonyl glycinuria and 3-hydroxyisovaleric aciduria. Bartlett K; Ng H; Leonard JV Clin Chim Acta; 1980 Jan; 100(2):183-6. PubMed ID: 6766095 [TBL] [Abstract][Full Text] [Related]
6. Propionyl-CoA carboxylase deficiency in a patient with biotin-responsive 3-methylcrotonylglycinuria. Sweetman L; Bates SP; Hull D; Nyhan WL Pediatr Res; 1977 Nov; 11(11):1144-7. PubMed ID: 917614 [TBL] [Abstract][Full Text] [Related]
10. Beta-methylcrotonyl-CoA carboxylase deficiency: a new metabolic error in leucine degradation. Stokke O; Eldjarn L; Jellum E; Pande H; Waaler PE Pediatrics; 1972 May; 49(5):726-35. PubMed ID: 5035417 [No Abstract] [Full Text] [Related]
11. [Convulsions in an infant with biotin-dependent 3-methylcrotonylglycinuria]. Lehnert W; Niederhoff H; Saule H Monatsschr Kinderheilkd (1902); 1980 May; 128(5):380-1. PubMed ID: 7421860 [No Abstract] [Full Text] [Related]
12. Studies on the urinary acidic metabolites excreted by patients with beta-methylcrotonylglycinuria, propionic acidaemia and methylmalonic acidaemia, using gas-liquid chromatography and mass spectrometry. Chalmers RA; Lawson AM; Watts RW Clin Chim Acta; 1974 Mar; 52(1):43-51. PubMed ID: 4827458 [No Abstract] [Full Text] [Related]
13. Deficiency of propionyl-Co A carboxylase and methylcrotonyl-Co A carboxylase in a patient with methylcrotonylglycinuria. Weyler W; Sweetman L; Maggio DC; Nyhan WL Clin Chim Acta; 1977 May; 76(3):321-8. PubMed ID: 858206 [TBL] [Abstract][Full Text] [Related]
14. Mutant holocarboxylase synthetase: evidence for the enzyme defect in early infantile biotin-responsive multiple carboxylase deficiency. Burri BJ; Sweetman L; Nyhan WL J Clin Invest; 1981 Dec; 68(6):1491-5. PubMed ID: 6798072 [TBL] [Abstract][Full Text] [Related]
15. Comparative GC/MS studies on the urinary acidic metabolites in beta-methylcrotonylglycinuria propionic acidaemia and methylmalonic acidaemia. Lawson AM; Chalmers RA; Watts RW Z Klin Chem Klin Biochem; 1974 May; 12(5):260. PubMed ID: 4440174 [No Abstract] [Full Text] [Related]
17. Localisation of enzymic defect in propionicacidaemia. Gompertz D; Storrs CN; Bau DC; Peters TJ; Hughes EA Lancet; 1970 May; 1(7657):1140-3. PubMed ID: 4192098 [No Abstract] [Full Text] [Related]
18. Stimulation of propionyl CoA and beta-methylcrotonyl CoA carboxylase activities in human leukocytes and cultured fibroblasts by biotin. Wolf B; Rosenberg LE Pediatr Res; 1979 Nov; 13(11):1275-9. PubMed ID: 514693 [No Abstract] [Full Text] [Related]