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3. Methylmalonic aciduria. An inborn error leading to metabolic acidosis, long-chain ketonuria and intermittent hyperglycinemia. Rosenberg LE; Lilljeqvist AC; Hsia YE N Engl J Med; 1968 Jun; 278(24):1319-22. PubMed ID: 5648598 [No Abstract] [Full Text] [Related]
4. American Academy of Pediatrics. Committee on Nutrition: special diets for infants with inborn errors of amino acid metabolism. Pediatrics; 1976 May; 57(5):783-92. PubMed ID: 940719 [TBL] [Abstract][Full Text] [Related]
6. Methylmalonic acid excretion in methylmalonic acidemia. Kelly S; Cowger M N Y State J Med; 1980 Feb; 80(2):240-3. PubMed ID: 6929423 [No Abstract] [Full Text] [Related]
7. Beta-ketothiolase deficiency as a cause of the "ketotic hyperglycinemia syndrome". Hillman RE; Keating JP Pediatrics; 1974 Feb; 53(2):221-5. PubMed ID: 4812006 [No Abstract] [Full Text] [Related]
8. Response to dietary therapy in B 12 unresponsive methylmalonic acidemia. Nyhan WL; Fawcett N; Ando T; Rennert OM; Julius RL Pediatrics; 1973 Mar; 51(3):539-48. PubMed ID: 4707869 [No Abstract] [Full Text] [Related]
9. [Dietetics in hereditary enzyme deficiencies]. Royer P Sem Hop; 1970 Feb; 46(10):653-9. PubMed ID: 4314674 [No Abstract] [Full Text] [Related]
10. Propionicacidemia (ketotic hyperglycinemia): dietary treatment resulting in normal growth and development. Brandt IK; Hsia YE; Clement DH; Provence SA Pediatrics; 1974 Mar; 53(3):391-5. PubMed ID: 4815259 [No Abstract] [Full Text] [Related]
12. [Value of peritoneal dialysis in the emergency treatment of metabolic diseases of constitutional origin revealed in the neonatal period]. Saudubray JM; Fournet JP; Cloup M Ann Med Interne (Paris); 1971 Dec; 122(12):1279-83. PubMed ID: 5151629 [No Abstract] [Full Text] [Related]
13. [13C]Valine metabolism in methylmalonicacidemia using nuclear magnetic resonance: propinonate as an obligate intermediate. Tanaka K; Armitage IM; Ramsdell HS; Hsia YE; Lipsky SR; Rosenberg LE Proc Natl Acad Sci U S A; 1975 Sep; 72(9):3692-6. PubMed ID: 1059159 [TBL] [Abstract][Full Text] [Related]
14. Effects of protein or amino acid deprivation on the tissue distribution of vitamin B12. Aschkenasy A Isr J Med Sci; 1965 Jul; 1(4):709-11. PubMed ID: 5856102 [No Abstract] [Full Text] [Related]
16. New disorder of vitamin B12 metabolism (cobalamin F) presenting as methylmalonic aciduria. Rosenblatt DS; Laframboise R; Pichette J; Langevin P; Cooper BA; Costa T Pediatrics; 1986 Jul; 78(1):51-4. PubMed ID: 3725502 [TBL] [Abstract][Full Text] [Related]
17. Studies in a patient with methylmalonic acidemia. Morrow G; Barness LA J Pediatr; 1969 May; 74(5):691-8. PubMed ID: 5778825 [No Abstract] [Full Text] [Related]
18. [Prognosis of congenital methylmalonic aciduria. Correlations between tolerance to proteins, response to vitamin B12 and enzymatic defect (author's transl)]. Saudubray JM; Charpentier C; Coude FX; Ogier H; Pham Dinh D; Bartlett K; Gompertz D Arch Fr Pediatr; 1980; 37 Suppl 2():IX-XIV. PubMed ID: 6108749 [TBL] [Abstract][Full Text] [Related]
19. Hyperglycinemia with ketosis due to a defect in isoleucine metabolism: a preliminary report. Keating JP; Feigin RD; Tenenbaum SM; Hillman RE Pediatrics; 1972 Dec; 50(6):890-5. PubMed ID: 4636454 [No Abstract] [Full Text] [Related]
20. Clinical consequences of disorders in the intermediate metabolism of branched chain amino acids (valine, leucine and isoleucine). Mogoş T; Cheţa CP; Mincu IT Rom J Intern Med; 1994; 32(1):57-61. PubMed ID: 8081313 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]