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4. Blood and tissue branched-chain amino and alpha-keto acid concentrations: effect of diet, starvation, and disease. Hutson SM; Harper AE Am J Clin Nutr; 1981 Feb; 34(2):173-83. PubMed ID: 7211722 [TBL] [Abstract][Full Text] [Related]
5. THE DIAGNOSIS OF MAPLE SYRUP URINE DISEASE (BRANCHED- CHAIN KETOACIDURIA) BY THE IN VITRO STUDY OF THE PERIPHERAL LEUKOCYTE. DANCIS J; HUTZLER J; LEVITZ M Pediatrics; 1963 Aug; 32():234-8. PubMed ID: 14044451 [No Abstract] [Full Text] [Related]
6. Effects of maple syrup urine disease metabolites on mouse L-fibroblasts in vitro: a fine structural and biochemical study. Bissell MG; Bensch KG; Herman MM J Neurochem; 1974 Jun; 22(6):957-64. PubMed ID: 4859303 [No Abstract] [Full Text] [Related]
7. Oxidation of branched chain amino acids by isolated hearts and diaphragms of the rat. The effect of fatty acids, glucose, and pyruvate respiration. Buse MG; Biggers JF; Friderici KH; Buse JF J Biol Chem; 1972 Dec; 247(24):8085-96. PubMed ID: 4640937 [No Abstract] [Full Text] [Related]
8. [CLINICAL, BIOCHEMICAL, AND NEUROPATHOLOGIC ASPECTS OF MAPLE SYRUP URINE DISEASE. A KETOACIDURIA OF THE OPEN CHAIN AMINOACIDS LEUCINE, ISOLEUCINE AND VALINE]. SILBERMANSCHWARTZMAN J An Fac Med Lima; 1963 Sep; 46():339-65. PubMed ID: 14122039 [No Abstract] [Full Text] [Related]
9. Site of action of insulin in promoting leucine utilization in adipose tissue. Goodman HM Am J Physiol; 1977 Aug; 233(2):E97-103. PubMed ID: 888951 [No Abstract] [Full Text] [Related]
10. Enzyme activity in classical and variant forms of maple syrup urine disease. Dancis J; Hutzler J; Snyderman SE; Cox RP J Pediatr; 1972 Aug; 81(2):312-20. PubMed ID: 5042489 [No Abstract] [Full Text] [Related]
11. Catabolism of leucine to branched-chain fatty acids in Staphylococcus xylosus. Beck HC; Hansen AM; Lauritsen FR J Appl Microbiol; 2004; 96(5):1185-93. PubMed ID: 15078537 [TBL] [Abstract][Full Text] [Related]
13. Valine, leucine, and isoleucine metabolism by lactating bovine mammary tissue. Wohlt JE; Clark JH; Derrig RG; Davis CL J Dairy Sci; 1977 Dec; 60(12):1875-82. PubMed ID: 563875 [TBL] [Abstract][Full Text] [Related]
14. Release of leucine and isoleucine metabolites by perfused skeletal muscle and liver of rat. Spydevold O; Hokland B Int J Biochem; 1983; 15(8):985-90. PubMed ID: 6617955 [TBL] [Abstract][Full Text] [Related]
15. On the mechanism of L-alloisoleucine formation: studies on a healthy subject and in fibroblasts from normals and patients with maple syrup urine disease. Schadewaldt P; Hammen HW; Dalle-Feste C; Wendel U J Inherit Metab Dis; 1990; 13(2):137-50. PubMed ID: 2116545 [TBL] [Abstract][Full Text] [Related]
17. M aple syrup urine disease. A review with a report of an additional case. Schwartz JF; Kolendrianos ET Dev Med Child Neurol; 1969 Aug; 11(4):460-70. PubMed ID: 5805351 [No Abstract] [Full Text] [Related]
18. Leucine equivalency system in managing branched chain ketoaciduria. Smith BA; Waisman HA J Am Diet Assoc; 1971 Oct; 59(4):342-6. PubMed ID: 5095277 [No Abstract] [Full Text] [Related]