These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
147 related articles for article (PubMed ID: 6425346)
21. Increased de novo purine synthesis in cultured skin fibroblasts from heterozygotes for the Lesch-Nyhan syndrome. A sensitive marker for carrier detection. Zoref E; Sperling O Hum Hered; 1979; 29(1):64-8. PubMed ID: 761926 [TBL] [Abstract][Full Text] [Related]
22. A review of the molecular basis of hypoxanthine-guanine phosphoribosyltransferase (HPRT) deficiency. Sculley DG; Dawson PA; Emmerson BT; Gordon RB Hum Genet; 1992 Nov; 90(3):195-207. PubMed ID: 1487231 [TBL] [Abstract][Full Text] [Related]
23. Kelley-Seegmiller syndrome in a patient with complete hypoxanthine-guanine phosphoribosyltransferase deficiency. Cossu A; Micheli V; Jacomelli G; Carcassi A Clin Exp Rheumatol; 2002; 20(6):851-3. PubMed ID: 12508781 [TBL] [Abstract][Full Text] [Related]
24. Overproduction of uric acid in hypoxanthine-guanine phosphoribosyltransferase deficiency. Contribution by impaired purine salvage. Edwards NL; Recker D; Fox IH J Clin Invest; 1979 May; 63(5):922-30. PubMed ID: 447834 [TBL] [Abstract][Full Text] [Related]
26. Lesch-Nyhan syndrome due to a single nucleotide change in the hypoxanthine-guanine phosphoribosyltransferase gene (HPRTYale). Fujimori S; Davidson BL; Kelley WN; Palella TD Adv Exp Med Biol; 1989; 253A():135-8. PubMed ID: 2624182 [TBL] [Abstract][Full Text] [Related]
27. Inherited deficiency of hypoxanthine-guanine phosphoribosyltransferase in X-linked uric aciduria (the Lesch-Nyhan syndrome and its variants). Seegmiller JE Adv Hum Genet; 1976; 6():75-163. PubMed ID: 779428 [No Abstract] [Full Text] [Related]
28. Efficacy and safety of allopurinol in patients with the Lesch-Nyhan syndrome and partial hypoxanthine- phosphoribosyltransferase deficiency: a follow-up study of 18 Spanish patients. Torres RJ; Prior C; Puig JG Nucleosides Nucleotides Nucleic Acids; 2006; 25(9-11):1077-82. PubMed ID: 17065067 [TBL] [Abstract][Full Text] [Related]
30. Missense mutations and evolutionary conserved amino acids at the human hypoxanthine phosphoribosyl-transferase locus. Lambert B; Marcus S; Andersson B; Hou SM; Steen AM; Hellgren D Pharmacogenetics; 1992 Dec; 2(6):329-36. PubMed ID: 1306134 [TBL] [Abstract][Full Text] [Related]
31. Molecular analysis of HPRT deficiencies: an update of the spectrum of Asian mutations with novel mutations. Yamada Y; Nomura N; Yamada K; Wakamatsu N Mol Genet Metab; 2007 Jan; 90(1):70-6. PubMed ID: 17027311 [TBL] [Abstract][Full Text] [Related]
32. [Complete and partial deficiency of HPRT]. Ogasawara N Nihon Rinsho; 1996 Dec; 54(12):3315-20. PubMed ID: 8976112 [TBL] [Abstract][Full Text] [Related]
33. HPRT deficiency in a two-month-old child presenting acute renal failure and gout with a new deletion of two bases in exon 3 of the HPRT gene. Zamora A; Escárcega RO; Vazquez R; Zamora A; O'Neill JP Arch Med Res; 2007 May; 38(4):460-2. PubMed ID: 17416296 [TBL] [Abstract][Full Text] [Related]
34. Selection against blood cells deficient in hypoxanthine phosphoribosyltransferase (HPRT) in Lesch-Nyhan heterozygotes occurs at the level of multipotent stem cells. Hakoda M; Hirai Y; Akiyama M; Yamanaka H; Terai C; Kamatani N; Kashiwazaki S Hum Genet; 1995 Dec; 96(6):674-80. PubMed ID: 8522326 [TBL] [Abstract][Full Text] [Related]
35. Molecular analysis of five independent Japanese mutant genes responsible for hypoxanthine guanine phosphoribosyltransferase (HPRT) deficiency. Yamada Y; Goto H; Suzumori K; Adachi R; Ogasawara N Hum Genet; 1992 Dec; 90(4):379-84. PubMed ID: 1483694 [TBL] [Abstract][Full Text] [Related]
36. Alzheimer's disease shares gene expression aberrations with purinergic dysregulation of HPRT deficiency (Lesch-Nyhan disease). Kang TH; Friedmann T Neurosci Lett; 2015 Mar; 590():35-9. PubMed ID: 25636690 [TBL] [Abstract][Full Text] [Related]
37. HGPRT-deficiency--the molecular basis of the clinical syndromes. Kelley WN; Searle JG; Wilson JM Verh Dtsch Ges Inn Med; 1986; 92():465-9. PubMed ID: 3811548 [No Abstract] [Full Text] [Related]
38. Lesch Nyhan syndrome: a novel complex mutation in a Tunisian child. Rebai I; Kraoua I; Benrhouma H; Rouissi A; Turki I; Ceballos-Picot I; Gouider-Khouja N Brain Dev; 2014 Nov; 36(10):921-3. PubMed ID: 24503445 [TBL] [Abstract][Full Text] [Related]
39. Purine synthesis de novo and salvage in hypoxanthine phosphoribosyltransferase-deficient mice. Allsop J; Watts RW Enzyme; 1990; 43(3):155-9. PubMed ID: 2095336 [TBL] [Abstract][Full Text] [Related]