165 related articles for article (PubMed ID: 6430599)
1. Pyruvate dehydrogenase subcomplex with lipoamide dehydrogenase deficiency in a patient with lactic acidosis and branched chain ketoaciduria.
Matuda S; Kitano A; Sakaguchi Y; Yoshino M; Saheki T
Clin Chim Acta; 1984 Jun; 140(1):59-64. PubMed ID: 6430599
[TBL] [Abstract][Full Text] [Related]
2. Leigh disease with deficiency of lipoamide dehydrogenase: treatment failure with dichloroacetate.
Craigen WJ
Pediatr Neurol; 1996 Jan; 14(1):69-71. PubMed ID: 8652022
[TBL] [Abstract][Full Text] [Related]
3. Immunochemical comparison of lipoamide dehydrogenases from various sources and reactivity of various lipoamide dehydrogenases with rat heart pyruvate dehydrogenase-subcomplex.
Matuda S; Saheki T
Biochem Biophys Res Commun; 1985 Jun; 129(2):479-84. PubMed ID: 3893428
[TBL] [Abstract][Full Text] [Related]
4. Deficiency of dihydrolipoyl dehydrogenase (a component of the pyruvate and alpha-ketoglutarate dehydrogenase complexes): a cause of congenital chronic lactic acidosis in infancy.
Robinson BH; Taylor J; Sherwood WG
Pediatr Res; 1977 Dec; 11(12):1198-202. PubMed ID: 413089
[TBL] [Abstract][Full Text] [Related]
5. Purification and immunochemical studies of pyruvate dehydrogenase complex from rat heart, and cell-free synthesis of lipoamide dehydrogenase, a component of the complex.
Matuda S; Shirahama T; Saheki T; Miura S; Mori M
Biochim Biophys Acta; 1983 Oct; 741(1):86-93. PubMed ID: 6412756
[TBL] [Abstract][Full Text] [Related]
6. Deficiency of the pyruvate dehydrogenase component in pyruvate dehydrogenase complex-deficient human fibroblasts. Immunological identification.
Ho L; Hu CW; Packman S; Patel MS
J Clin Invest; 1986 Sep; 78(3):844-7. PubMed ID: 3091638
[TBL] [Abstract][Full Text] [Related]
7. [E2 and E3 deficiency of pyruvate dehydrogenase complex].
Matuda S
Tanpakushitsu Kakusan Koso; 1988 Apr; 33(5):666-9. PubMed ID: 3152088
[No Abstract] [Full Text] [Related]
8. Congenital lactic acidosis, alpha-ketoglutaric aciduria and variant form of maple syrup urine disease due to a single enzyme defect: dihydrolipoyl dehydrogenase deficiency.
Munnich A; Saudubray JM; Taylor J; Charpentier C; Marsac C; Rocchiccioli F; Amedee-Manesme O; Coude FX; Frezal J; Robinson BH
Acta Paediatr Scand; 1982 Jan; 71(1):167-71. PubMed ID: 6897145
[TBL] [Abstract][Full Text] [Related]
9. Turnover of pegeon breast muscle pyruvate dehydrogenase complex.
Furuta S
J Biochem; 1979 Jul; 86(1):183-90. PubMed ID: 113394
[TBL] [Abstract][Full Text] [Related]
10. Disorders of the pyruvate dehydrogenase complex.
Stansbie D; Wallace SJ; Marsac C
J Inherit Metab Dis; 1986; 9(2):105-19. PubMed ID: 3018357
[TBL] [Abstract][Full Text] [Related]
11. Lipoamide dehydrogenase deficiency with primary lactic acidosis: favorable response to treatment with oral lipoic acid.
Matalon R; Stumpf DA; Michals K; Hart RD; Parks JK; Goodman SI
J Pediatr; 1984 Jan; 104(1):65-9. PubMed ID: 6418873
[TBL] [Abstract][Full Text] [Related]
12. A defect in branched-chain amino acid metabolism in a patient with congenital lactic acidosis due to dihydrolipoyl dehydrogenase deficiency.
Taylor J; Robinson BH; Sherwood WG
Pediatr Res; 1978 Jan; 12(1):60-2. PubMed ID: 643378
[TBL] [Abstract][Full Text] [Related]
13. Lactic acidemia, neurologic deterioration and carbohydrate dependence in a girl with dihydrolipoyl dehydrogenase deficiency.
Robinson BH; Taylor J; Kahler SG; Kirkman HN
Eur J Pediatr; 1981 Mar; 136(1):35-9. PubMed ID: 6894281
[No Abstract] [Full Text] [Related]
14. Pyruvate dehydrogenase phosphatase deficiency: a cause of congenital chronic lactic acidosis in infancy.
Robinson BH; Sherwood WG
Pediatr Res; 1975 Dec; 9(12):935-9. PubMed ID: 172850
[TBL] [Abstract][Full Text] [Related]
15. Inhibition of glycine oxidation by pyruvate, alpha-ketoglutarate, and branched-chain alpha-keto acids in rat liver mitochondria: presence of interaction between the glycine cleavage system and alpha-keto acid dehydrogenase complexes.
Kochi H; Seino H; Ono K
Arch Biochem Biophys; 1986 Sep; 249(2):263-72. PubMed ID: 3753002
[TBL] [Abstract][Full Text] [Related]
16. Lipoamide dehydrogenase deficiency due to a novel mutation in the interface domain.
Shany E; Saada A; Landau D; Shaag A; Hershkovitz E; Elpeleg ON
Biochem Biophys Res Commun; 1999 Aug; 262(1):163-6. PubMed ID: 10448086
[TBL] [Abstract][Full Text] [Related]
17. Bovine kidney pyruvate dehydrogenase complex. Isolation of the component enzymes after limited proteolysis with papain.
Kresze GB; Ronft H; Dietl B
Eur J Biochem; 1980 Apr; 105(2):371-9. PubMed ID: 6769670
[TBL] [Abstract][Full Text] [Related]
18. Characterization and immunochemistry of pyruvate dehydrogenase complex of Ascaris muscle.
Matuda S; Nakano K; Saheki T
Biochem Int; 1986 Oct; 13(4):599-608. PubMed ID: 3099796
[TBL] [Abstract][Full Text] [Related]
19. Inborn errors of pyruvate metabolism.
Robinson BH
Biochem Soc Trans; 1983 Dec; 11(6):623-6. PubMed ID: 6421637
[No Abstract] [Full Text] [Related]
20. Purification and properties of the pyruvate dehydrogenase complex from Salmonella typhimurium and formation of hybrids with the enzyme complex from Escherichia coli.
Seckler R; Binder R; Bisswanger H
Biochim Biophys Acta; 1982 Jul; 705(2):210-7. PubMed ID: 7052136
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
