151 related articles for article (PubMed ID: 6475955)
1. Direct physical evidence for stabilization of branched-chain alpha-ketoacid dehydrogenase by thiamin pyrophosphate.
Heffelfinger SC; Sewell ET; Elsas LJ; Danner DJ
Am J Hum Genet; 1984 Jul; 36(4):802-7. PubMed ID: 6475955
[TBL] [Abstract][Full Text] [Related]
2. Stabilization of mammalian liver branched-chain alpha-ketoacid dehydrogenase by thiamin pyrophosphate.
Danner DJ; Lemmon SK; Elsas LJ
Arch Biochem Biophys; 1980 Jun; 202(1):23-8. PubMed ID: 7396533
[No Abstract] [Full Text] [Related]
3. Studies on the regulation of the mitochondrial alpha-ketoacid dehydrogenase complexes and their kinases.
Harris RA; Hawes JW; Popov KM; Zhao Y; Shimomura Y; Sato J; Jaskiewicz J; Hurley TD
Adv Enzyme Regul; 1997; 37():271-93. PubMed ID: 9381974
[TBL] [Abstract][Full Text] [Related]
4. The role of thiamin in maple syrup urine disease.
Elsas LJ; Danner DJ
Ann N Y Acad Sci; 1982; 378():404-21. PubMed ID: 7044230
[No Abstract] [Full Text] [Related]
5. Evidence that the mitochondrial activator of phosphorylated branched-chain 2-oxoacid dehydrogenase complex is the dissociated E1 component of the complex.
Yeaman SJ; Cook KG; Boyd RW; Lawson R
FEBS Lett; 1984 Jun; 172(1):38-42. PubMed ID: 6610568
[TBL] [Abstract][Full Text] [Related]
6. Purification, characterization, regulation and molecular cloning of mitochondrial protein kinases.
Harris RA; Popov KM; Shimomura Y; Zhao Y; Jaskiewicz J; Nanaumi N; Suzuki M
Adv Enzyme Regul; 1992; 32():267-84. PubMed ID: 1496922
[TBL] [Abstract][Full Text] [Related]
7. Uncertainties in the mechanism of thiamin pyrophosphate-dependent alpha-keto acid dehydrogenase complexes.
Nutr Rev; 1984 Sep; 42(9):328-30. PubMed ID: 6504412
[No Abstract] [Full Text] [Related]
8. Regulation of branched-chain alpha-ketoacid dehydrogenase complex by covalent modification.
Harris RA; Paxton R; Powell SM; Goodwin GW; Kuntz MJ; Han AC
Adv Enzyme Regul; 1986; 25():219-37. PubMed ID: 3028049
[TBL] [Abstract][Full Text] [Related]
9. Regulation of the branched-chain alpha-ketoacid dehydrogenase and elucidation of a molecular basis for maple syrup urine disease.
Harris RA; Zhang B; Goodwin GW; Kuntz MJ; Shimomura Y; Rougraff P; Dexter P; Zhao Y; Gibson R; Crabb DW
Adv Enzyme Regul; 1990; 30():245-63. PubMed ID: 2403034
[TBL] [Abstract][Full Text] [Related]
10. Identification of specific subunits of highly purified bovine liver branched-chain ketoacid dehydrogenase.
Heffelfinger SC; Sewell ET; Danner DJ
Biochemistry; 1983 Nov; 22(24):5519-22. PubMed ID: 6652074
[TBL] [Abstract][Full Text] [Related]
11. Dietary thiamin level influences levels of its diphosphate form and thiamin-dependent enzymic activities of rat liver.
Blair PV; Kobayashi R; Edwards HM; Shay NF; Baker DH; Harris RA
J Nutr; 1999 Mar; 129(3):641-8. PubMed ID: 10082768
[TBL] [Abstract][Full Text] [Related]
12. Thiamin-responsive maple-syrup-urine disease: decreased affinity of the mutant branched-chain alpha-keto acid dehydrogenase for alpha-ketoisovalerate and thiamin pyrophosphate.
Chuang DT; Ku LS; Cox RP
Proc Natl Acad Sci U S A; 1982 May; 79(10):3300-4. PubMed ID: 6954481
[TBL] [Abstract][Full Text] [Related]
13. Purification and characterization of branched chain alpha-ketoacid dehydrogenase from bovine liver mitochondria.
Danner DJ; Lemmon SK; Besharse JC; Elsas LJ
J Biol Chem; 1979 Jun; 254(12):5522-6. PubMed ID: 447664
[TBL] [Abstract][Full Text] [Related]
14. Multi-site phosphorylation of branched-chain 2-oxoacid dehydrogenase complex within mitochondria isolated from rat liver, kidney and heart.
Cook KG; Lawson R; Yeaman SJ
FEBS Lett; 1983 Nov; 164(1):85-8. PubMed ID: 6653787
[TBL] [Abstract][Full Text] [Related]
15. Isolation of branched-chain alpha-keto acid dehydrogenase as active complex from bovine liver.
Danner DJ; Heffelfinger SC
Methods Enzymol; 1988; 166():298-302. PubMed ID: 3071712
[No Abstract] [Full Text] [Related]
16. Phosphorylation sites and inactivation of branched-chain alpha-ketoacid dehydrogenase isolated from rat heart, bovine kidney, and rabbit liver, kidney, heart, brain, and skeletal muscle.
Paxton R; Kuntz M; Harris RA
Arch Biochem Biophys; 1986 Jan; 244(1):187-201. PubMed ID: 3947057
[TBL] [Abstract][Full Text] [Related]
17. Import rate of the E1beta subunit of human branched chain alpha-ketoacid dehydrogenase is a limiting factor in the amount of complex formed in the mitochondria.
Sitler TL; McKean MC; Peinemann F; Jackson E; Danner DJ
Biochim Biophys Acta; 1998 Sep; 1404(3):385-92. PubMed ID: 9739167
[TBL] [Abstract][Full Text] [Related]
18. Roles of amino acid residues surrounding phosphorylation site 1 of branched-chain alpha-ketoacid dehydrogenase (BCKDH) in catalysis and phosphorylation site recognition by BCKDH kinase.
Hawes JW; Schnepf RJ; Jenkins AE; Shimomura Y; Popov KM; Harris RA
J Biol Chem; 1995 Dec; 270(52):31071-6. PubMed ID: 8537366
[TBL] [Abstract][Full Text] [Related]
19. Phylogenetic comparisons of the branched-chain alpha-ketoacid dehydrogenase complex.
Eisenstein RS; Miller RH; Hoganson G; Harper AE
Comp Biochem Physiol B; 1990; 97(4):719-26. PubMed ID: 2085956
[TBL] [Abstract][Full Text] [Related]
20. A direct spectrophotometric assay for branched-chain 2-oxo acid dehydrogenase activity in intact rat liver mitochondria.
Bartlett K; Sherratt HS
Biochem Soc Trans; 1981 Feb; 9(1):117-8. PubMed ID: 7215633
[No Abstract] [Full Text] [Related]
[Next] [New Search]