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3. Cognitive functioning in two sisters with carbamyl phosphate synthetase I deficiency. Sassaman EA; Zartler AS; Mulick JA J Pediatr Psychol; 1981 Jun; 6(2):171-5. PubMed ID: 7252721 [No Abstract] [Full Text] [Related]
4. Survival after early treatment for carbamyl phosphate synthetase (CPS) I deficiency associated with increase of intramitochondrial CPS I. Zimmer KP; Naim HY; Koch HG; Colombo JP; Rossi R; Schmid KW; Deufel T; Ullrich K; Harms E Lancet; 1995 Dec; 346(8989):1530-1. PubMed ID: 7491050 [TBL] [Abstract][Full Text] [Related]
5. Successful treatment of severe carbamyl phosphate synthetase I deficiency. Van de Bor M; Mooy P; van Zoeren D; Berger R; van Gelderen HH; Teijema HL Arch Dis Child; 1984 Dec; 59(12):1183-5. PubMed ID: 6524951 [TBL] [Abstract][Full Text] [Related]
6. Kinetic abnormalities of carbamyl phosphate synthetase-I in a case of congenital hyperammonaemia. Qureshi IA; Letarte J; Ouellet R; Lemieux B; Cathelineau L J Inherit Metab Dis; 1986; 9(3):253-60. PubMed ID: 3099069 [TBL] [Abstract][Full Text] [Related]
7. Autosomal recessive inheritance of human mitochondrial carbamyl phosphate synthetase deficiency. McReynolds JW; Crowley B; Mahoney MJ; Rosenberg LE Am J Hum Genet; 1981 May; 33(3):345-53. PubMed ID: 7246541 [TBL] [Abstract][Full Text] [Related]
9. A lethal neonatal variant of carbamoyl-phosphate synthetase deficiency in combination with an intermediate activity of L-ornithine: 2-oxoglutarate amino-transferase. van der Heiden C; Beemer FA; van Dijk HA; Desplanque J; Gerards LJ Clin Genet; 1983 May; 23(5):363-8. PubMed ID: 6851228 [TBL] [Abstract][Full Text] [Related]
10. Carbamyl phosphate synthetase I deficiency with no detectable mRNA activity. Suzuki Y; Matsushima A; Ohtake A; Mori M; Tatibana M; Orii T Eur J Pediatr; 1986 Oct; 145(5):406-8. PubMed ID: 3792387 [TBL] [Abstract][Full Text] [Related]
11. Liver ultrastructure in mitochondrial urea cycle enzyme deficiencies and comparison with Reye's syndrome. Latham PS; LaBrecque DR; McReynolds JW; Klatskin G Hepatology; 1984; 4(3):404-7. PubMed ID: 6724509 [TBL] [Abstract][Full Text] [Related]
12. Proceedings: Hepatic ultrastructure in a child with carbamyl phosphate synthetase deficiency, hyperornithinaemia, hyperammonaemia, and homocitrullinuria. Haust MD; Gatfield PD Arch Dis Child; 1975 Aug; 50(8):663. PubMed ID: 173245 [No Abstract] [Full Text] [Related]
13. A carbamylphosphate synthetase deficiency with no detectable immunoreactive enzyme and no translatable mRNA. Graf L; McIntyre P; Hoogenraad N; Brown G; Haan EA J Inherit Metab Dis; 1984; 7(3):104-6. PubMed ID: 6438391 [TBL] [Abstract][Full Text] [Related]
15. [Therapy of hyperammonemia in carbamyl phosphate synthase deficiency with peritoneal dialysis and venovenous hemofiltration]. Lettgen B; Bonzel KE; Colombo JP; Fuchs B; Kordass U; Wendel K; Rascher W Monatsschr Kinderheilkd; 1991 Sep; 139(9):612-7. PubMed ID: 1745252 [TBL] [Abstract][Full Text] [Related]
16. Carbamyl phosphate synthetase deficiency and postpartum hyperammonemia. Kotani Y; Shiota M; Umemoto M; Tsuritani M; Hoshiai H Am J Obstet Gynecol; 2010 Jul; 203(1):e10-1. PubMed ID: 20471629 [TBL] [Abstract][Full Text] [Related]
17. [Hyperammonemia: partial carbamyl phosphate synthetase deficiency]. Szentpéteri J; Kovács J; Földes G Orv Hetil; 1982 Aug; 123(31):1923-6. PubMed ID: 7133689 [No Abstract] [Full Text] [Related]
18. Clinical features of carbamyl phosphate synthetase-I deficiency in an adult. Call G; Seay AR; Sherry R; Qureshi IA Ann Neurol; 1984 Jul; 16(1):90-3. PubMed ID: 6465866 [TBL] [Abstract][Full Text] [Related]
19. Dysautonomia in an infant with secondary hyperammonemia due to propionyl coenzyme A carboxylase deficiency. Harris DJ; Yang BI; Wolf B; Snodgrass PJ Pediatrics; 1980 Jan; 65(1):107-10. PubMed ID: 7355003 [TBL] [Abstract][Full Text] [Related]