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2. Enzymologic studies and therapy of Leigh's disease associated with pyruvate decarboxylase deficiency. Toshima K; Kuroda Y; Hashimoto T; Ito M; Watanabe T; Miyao M; Ii K Pediatr Res; 1982 Jun; 16(6):430-5. PubMed ID: 7099758 [TBL] [Abstract][Full Text] [Related]
3. Citrate treatment in a patient with pyruvate decarboxylase deficiency. Oka Y; Matsuda I; Arashima S; Anakura M; Mitsuyama T Tohoku J Exp Med; 1976 Feb; 118(2):131-5. PubMed ID: 982428 [TBL] [Abstract][Full Text] [Related]
6. Leigh's disease with decreased activities of pyruvate carboxylase and pyruvate decarboxylase. Van Biervliet JP; Duran M; Wadman SK; Koster JF; van Rossum A J Inherit Metab Dis; 1980; 2(1):15-8. PubMed ID: 6796755 [TBL] [Abstract][Full Text] [Related]
7. Urinary organic acids in a case of congenital lactic acidosis due to pyruvate decarboxylase deficiency. Chalmers RA; Lawson AM; Borud O J Inherit Metab Dis; 1978; 1(1):15-6. PubMed ID: 117229 [No Abstract] [Full Text] [Related]
8. The effect of a high fat diet on pyruvate decarboxylase deficiency without central nervous system involvement. Kodama S; Yagi R; Ninomiya M; Goji K; Takahashi T; Morishita Y; Matsuo T Brain Dev; 1983; 5(4):381-9. PubMed ID: 6416099 [TBL] [Abstract][Full Text] [Related]
9. Pyruvate decarboxylase deficiency in a patient with Leigh's encephalomyelopathy. Ohtake M; Takada G; Miyabayashi S; Arai N; Tada K; Morinaga S Tohoku J Exp Med; 1982 Aug; 137(4):379-86. PubMed ID: 7123539 [TBL] [Abstract][Full Text] [Related]
11. Two-center mechanism for the oxidative decarboxylation of pyruvate by the pyruvate decarboxylating component of the pyruvate dehydrogenase complex of pigeon breast muscle. Hübner G; Neef H; Schellenberger A FEBS Lett; 1978 Feb; 86(1):6-8. PubMed ID: 620829 [No Abstract] [Full Text] [Related]
12. Gas chromatographic and mass spectrometric studies on urinary organic acids in a patient with congenital lactic acidosis due to pyruvate decarboxylase deficiency. Chalmers RA; Lawson AM; Borud O Clin Chim Acta; 1977 Jun; 77(2):117-24. PubMed ID: 19171 [TBL] [Abstract][Full Text] [Related]
13. Identification of an AMP-activatable pyruvate dehydrogenase isozyme in embryos and tumors. Lazo PA; Sols A FEBS Lett; 1980 Nov; 120(2):287-8. PubMed ID: 6254809 [No Abstract] [Full Text] [Related]
14. Absence of pyruvate decarboxylase activity in man: a cause of congenital lactic acidosis. Farrell DF; Clark AF; Scott CR; Wennberg RP Science; 1975 Mar; 187(4181):1082-4. PubMed ID: 803713 [TBL] [Abstract][Full Text] [Related]
15. A case of pyruvate carboxylase deficiency with later prenatal diagnosis of an unaffected sibling. Tsuchiyama A; Oyanagi K; Hirano S; Tachi N; Sogawa H; Wagatsuma K; Nakao T; Tsugawa S; Kawamura Y J Inherit Metab Dis; 1983; 6(3):85-8. PubMed ID: 6422150 [TBL] [Abstract][Full Text] [Related]
16. Partial pyruvate decarboxylase deficiency with profound lactic acidosis and hyperammonemia: responses to dichloroacetate and benzoate. McCormick K; Viscardi RM; Robinson B; Heininger J Am J Med Genet; 1985 Oct; 22(2):291-9. PubMed ID: 4050860 [TBL] [Abstract][Full Text] [Related]
17. Familial intermittent ataxia due to a defect of the E1 component of pyruvate dehydrogenase complex. Bindoff LA; Birch-Machin MA; Farnsworth L; Gardner-Medwin D; Lindsay JG; Turnbull DM J Neurol Sci; 1989 Nov; 93(2-3):311-8. PubMed ID: 2592988 [TBL] [Abstract][Full Text] [Related]
18. Pyruvate decarboxylase is like acetolactate synthase (ILV2) and not like the pyruvate dehydrogenase E1 subunit. Green JB FEBS Lett; 1989 Mar; 246(1-2):1-5. PubMed ID: 2651151 [TBL] [Abstract][Full Text] [Related]
19. Pyruvate decarboxylase--potentially inactive in the absence of the substrate. Hübner G; Schellenberger A Biochem Int; 1986 Nov; 13(5):767-72. PubMed ID: 3545209 [TBL] [Abstract][Full Text] [Related]
20. Inhibition of pyruvate:ferredoxin oxidoreductase from Trichomonas vaginalis by pyruvate and its analogues. Comparison with the pyruvate decarboxylase component of the pyruvate dehydrogenase complex. Williams KP; Leadlay PF; Lowe PN Biochem J; 1990 May; 268(1):69-75. PubMed ID: 2188649 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]