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3. Direct physical evidence for stabilization of branched-chain alpha-ketoacid dehydrogenase by thiamin pyrophosphate. Heffelfinger SC; Sewell ET; Elsas LJ; Danner DJ Am J Hum Genet; 1984 Jul; 36(4):802-7. PubMed ID: 6475955 [TBL] [Abstract][Full Text] [Related]
4. The role of thiamin in maple syrup urine disease. Elsas LJ; Danner DJ Ann N Y Acad Sci; 1982; 378():404-21. PubMed ID: 7044230 [No Abstract] [Full Text] [Related]
6. Thiamin-responsive maple-syrup-urine disease: decreased affinity of the mutant branched-chain alpha-keto acid dehydrogenase for alpha-ketoisovalerate and thiamin pyrophosphate. Chuang DT; Ku LS; Cox RP Proc Natl Acad Sci U S A; 1982 May; 79(10):3300-4. PubMed ID: 6954481 [TBL] [Abstract][Full Text] [Related]
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8. Role of carnitine in branched chain ketoacid metabolism. Nutr Rev; 1981 Nov; 39(11):406-7. PubMed ID: 7031525 [No Abstract] [Full Text] [Related]
9. Regulation of the branched chain alpha-ketoacid pathway in liver. Corkey BE; Martin-Requero A; Walajtys-Rode E; Williams RJ; Williamson JR J Biol Chem; 1982 Aug; 257(16):9668-76. PubMed ID: 6809741 [No Abstract] [Full Text] [Related]
10. Thoughts on the role of branched-chain alpha-keto acid dehydrogenase complex in nitrogen metabolism. Harper AE Ann N Y Acad Sci; 1989; 573():267-73. PubMed ID: 2699400 [No Abstract] [Full Text] [Related]
11. Low activity of branched-chain alpha-keto acid dehydrogenase complex in human liver. Nonami T; Taniguchi K; Kurokawa T; Kasai Y; Takagi H; Sugiyama S; Shimomura Y; Hutson SM Am J Clin Nutr; 1995 Nov; 62(5):1023. PubMed ID: 7572728 [No Abstract] [Full Text] [Related]
12. Biological activity of 1,N6-ethenothiamin, a fluorescent analog of thiamin, in rats. Gibby WA; Gubler CJ J Nutr; 1980 Oct; 110(10):2117-20. PubMed ID: 7420211 [TBL] [Abstract][Full Text] [Related]
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