149 related articles for article (PubMed ID: 6510434)
1. The effect of intravenous L-carnitine on propionic acid excretion in acute propionic acidaemia.
Böhles H; Lehnert W
Eur J Pediatr; 1984 Nov; 143(1):61-3. PubMed ID: 6510434
[TBL] [Abstract][Full Text] [Related]
2. Direct identification of propionylcarnitine in propionic acidaemia: biochemical and clinical results of oral carnitine supplementation.
Duran M; Ketting D; Beckeringh TE; Leupold D; Wadman SK
J Inherit Metab Dis; 1986; 9(2):202-7. PubMed ID: 3091925
[TBL] [Abstract][Full Text] [Related]
3. Propionylcarnitine excretion is not affected by metronidazole administration to patients with disorders of propionate metabolism.
Burns SP; Iles RA; Saudubray JM; Chalmers RA
Eur J Pediatr; 1996 Jan; 155(1):31-5. PubMed ID: 8750807
[TBL] [Abstract][Full Text] [Related]
4. Acylcarnitines in amniotic fluid: application to the prenatal diagnosis of propionic acidaemia.
Van Hove JL; Chace DH; Kahler SG; Millington DS
J Inherit Metab Dis; 1993; 16(2):361-7. PubMed ID: 8411998
[TBL] [Abstract][Full Text] [Related]
5. Carnitine therapy and metabolism in the disorders of propionyl-CoA metabolism studied using 1H-NMR spectroscopy.
Davies SE; Iles RA; Stacey TE; de Sousa C; Chalmers RA
Clin Chim Acta; 1991 Dec; 204(1-3):263-77. PubMed ID: 1819469
[TBL] [Abstract][Full Text] [Related]
6. Metabolic response to carnitine in methylmalonic aciduria. An effective strategy for elimination of propionyl groups.
Roe CR; Hoppel CL; Stacey TE; Chalmers RA; Tracey BM; Millington DS
Arch Dis Child; 1983 Nov; 58(11):916-20. PubMed ID: 6651329
[TBL] [Abstract][Full Text] [Related]
7. Liver transplantation in propionic acidaemia.
Saudubray JM; Touati G; Delonlay P; Jouvet P; Schlenzig J; Narcy C; Laurent J; Rabier D; Kamoun P; Jan D; Revillon Y
Eur J Pediatr; 1999 Dec; 158 Suppl 2():S65-9. PubMed ID: 10603102
[TBL] [Abstract][Full Text] [Related]
8. Propionylcarnitine excretion in propionic and methylmalonic acidurias: a cause of carnitine deficiency.
Di Donato S; Rimoldi M; Garavaglia B; Uziel G
Clin Chim Acta; 1984 May; 139(1):13-21. PubMed ID: 6723070
[TBL] [Abstract][Full Text] [Related]
9. Reduction of lipid and protein damage in patients with disorders of propionate metabolism under treatment: a possible protective role of L-carnitine supplementation.
Ribas GS; Manfredini V; de Mari JF; Wayhs CY; Vanzin CS; Biancini GB; Sitta A; Deon M; Wajner M; Vargas CR
Int J Dev Neurosci; 2010 Apr; 28(2):127-32. PubMed ID: 20100562
[TBL] [Abstract][Full Text] [Related]
10. Cardiomyopathy in propionic acidaemia.
Massoud AF; Leonard JV
Eur J Pediatr; 1993 May; 152(5):441-5. PubMed ID: 8319715
[TBL] [Abstract][Full Text] [Related]
11. L-carnitine enhances excretion of propionyl coenzyme A as propionylcarnitine in propionic acidemia.
Roe CR; Millington DS; Maltby DA; Bohan TP; Hoppel CL
J Clin Invest; 1984 Jun; 73(6):1785-8. PubMed ID: 6725560
[TBL] [Abstract][Full Text] [Related]
12. Absence of acidosis in the initial presentation of propionic acidaemia.
Walter JH; Wraith JE; Cleary MA
Arch Dis Child Fetal Neonatal Ed; 1995 May; 72(3):F197-9. PubMed ID: 7796239
[TBL] [Abstract][Full Text] [Related]
13. [The neonatal form of propionic acidemia].
Figueras Aloy J; Ribes Rubio A; Vilaseca Busca MA; Lluch Mir M; Brines Godino P; Jiménez González R; Cruz Hernández M
An Esp Pediatr; 1988 Dec; 29(6):459-62. PubMed ID: 3245641
[TBL] [Abstract][Full Text] [Related]
14. Carnitine deficiency in inherited organic acid disorders and Reye syndrome.
Sugiyama N; Kidouchi K; Kobayashi M; Wada Y
Acta Paediatr Jpn; 1990 Aug; 32(4):410-6. PubMed ID: 2288224
[TBL] [Abstract][Full Text] [Related]
15. Clinical outcome and long-term management of 17 patients with propionic acidaemia.
van der Meer SB; Poggi F; Spada M; Bonnefont JP; Ogier H; Hubert P; Depondt E; Rapoport D; Rabier D; Charpentier C; Parvy P; Bardet J; Kamoun P; Saudubray JM
Eur J Pediatr; 1996 Mar; 155(3):205-10. PubMed ID: 8929729
[TBL] [Abstract][Full Text] [Related]
16. Carnitine reduces fasting ketogenesis in patients with disorders of propionate metabolism.
Wolff JA; Carroll JE; Le Phuc Thuy ; Prodanos C; Haas R; Nyhan WL
Lancet; 1986 Feb; 1(8476):289-91. PubMed ID: 2868163
[TBL] [Abstract][Full Text] [Related]
17. Urinary propionylcarnitine analysis for monitoring carnitine supplementation in inherited disorders of propionate metabolism.
Sugiyama N; Matsuda I; Wada Y; Narisawa K; Kobayashi M; Kidouchi K
J Inherit Metab Dis; 1994; 17(5):611-5. PubMed ID: 7837769
[No Abstract] [Full Text] [Related]
18. Methylcitrate in maternal urine during a pregnancy with a fetus affected with propionic acidaemia.
Aramaki S; Lehotay D; Nyhan WL; MacLeod PM; Sweetman L
J Inherit Metab Dis; 1989; 12(1):86-8. PubMed ID: 2501588
[TBL] [Abstract][Full Text] [Related]
19. Oxidative stress parameters in urine from patients with disorders of propionate metabolism: a beneficial effect of L:-carnitine supplementation.
Ribas GS; Biancini GB; Mescka C; Wayhs CY; Sitta A; Wajner M; Vargas CR
Cell Mol Neurobiol; 2012 Jan; 32(1):77-82. PubMed ID: 21833551
[TBL] [Abstract][Full Text] [Related]
20. The response to L-carnitine and glycine therapy in isovaleric acidaemia.
de Sousa C; Chalmers RA; Stacey TE; Tracey BM; Weaver CM; Bradley D
Eur J Pediatr; 1986 Feb; 144(5):451-6. PubMed ID: 3956533
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]