These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
3. Role of lysosomal acid lipase in the metabolism of plasma low density lipoprotein. Observations in cultured fibroblasts from a patient with cholesteryl ester storage disease. Goldstein JL; Dana SE; Faust JR; Beaudet AL; Brown MS J Biol Chem; 1975 Nov; 250(21):8487-95. PubMed ID: 172501 [TBL] [Abstract][Full Text] [Related]
4. Lysosomal acid lipase in cultivated fibroblasts: characterization of enzyme activity in normal and enzymatically deficient cell lines. Burton BK; Emery D; Mueller HW Clin Chim Acta; 1980 Feb; 101(1):25-32. PubMed ID: 6892615 [No Abstract] [Full Text] [Related]
5. Acid lipase deficiency: clinical and biochemical heterogeneity. Aubert-Tulkens G; Van Hoof F Acta Paediatr Belg; 1979; 32(4):239-45. PubMed ID: 546024 [No Abstract] [Full Text] [Related]
6. New spectrophotometric assays of acid lipase and their use in the diagnosis of Wolman and cholesteryl ester storage diseases. Nègre A; Salvayre R; Dagan A; Borrone C; Gatt S Anal Biochem; 1985 Mar; 145(2):398-405. PubMed ID: 4014671 [TBL] [Abstract][Full Text] [Related]
7. [Cholesterol ester storage disease in children. Comparative biochemistry of hepatocyte and fibroblast cultures]. Gautier M; Lapous D; Raulin J Arch Fr Pediatr; 1978 Dec; 35(10 Suppl):38-49. PubMed ID: 749752 [TBL] [Abstract][Full Text] [Related]
8. Use of Nile red stain in the detection of cholesteryl ester accumulation in acid lipase-deficient fibroblasts. Brown WJ; Warfel J; Greenspan P Arch Pathol Lab Med; 1988 Mar; 112(3):295-7. PubMed ID: 3345127 [TBL] [Abstract][Full Text] [Related]
11. Neutral lipid storage with acid lipase deficiency: a new variant of Wolman's disease with features of the Senior syndrome. Philippart M; Durand P; Borrone C Pediatr Res; 1982 Nov; 16(11):954-9. PubMed ID: 7155665 [TBL] [Abstract][Full Text] [Related]
12. Acid lipase cross-reacting material in Wolman disease and cholesterol ester storage disease. Burton BK; Reed SP Am J Hum Genet; 1981 Mar; 33(2):203-8. PubMed ID: 6782865 [TBL] [Abstract][Full Text] [Related]
14. [Clinical and histoenzymological peculiarities of cholesterol storage in 2 children of the same family]. Lageron A; Gautier M; Scotto J Arch Fr Pediatr; 1985; 42 Suppl 1():605-11. PubMed ID: 4083993 [TBL] [Abstract][Full Text] [Related]
15. Pulmonary hypertension in an 18-year-old girl with cholesteryl ester storage disease (CESD). Cagle PT; Ferry GD; Beaudet AL; Hawkins EP Am J Med Genet; 1986 Aug; 24(4):711-22. PubMed ID: 3740103 [No Abstract] [Full Text] [Related]
16. Cholesterol ester and triglyceride metabolism in intact fibroblasts from patients with Wolman's disease and cholesterol ester storage disease. Burton BK; Remy WT; Rayman L Pediatr Res; 1984 Dec; 18(12):1242-5. PubMed ID: 6522136 [TBL] [Abstract][Full Text] [Related]
17. [Wolman disease and cholesterol ester storage disease in adults. New means of study and diagnosis]. Salvayre R; Nègre A; Maret A; Radom J; Douste-Blazy L Ann Biol Clin (Paris); 1986; 44(6):611-7. PubMed ID: 3826777 [TBL] [Abstract][Full Text] [Related]
18. Metabolism of 1-pyrenedecanoic acid and accumulation of neutral fluorescent lipids in cultured fibroblasts of multisystemic lipid storage myopathy. Radom J; Salvayre R; Maret A; Nègre A; Douste-Blazy L Biochim Biophys Acta; 1987 Jul; 920(2):131-9. PubMed ID: 3607075 [TBL] [Abstract][Full Text] [Related]