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5. Propionyl-CoA carboxylase deficiency: case report, effect of low-protein diet and identification of 3-oxo-2-methylvaleric acid 3-hydroxy-2-methylvaleric acid, and maleic acid in urine. Bergstrøm T; Greter J; Levin AH; Steen G; Tryding N; Wass U Scand J Clin Lab Invest; 1981 Apr; 41(2):117-26. PubMed ID: 7313494 [TBL] [Abstract][Full Text] [Related]
6. The identification of 3-keto-2-methylvaleric acid and 3-hydroxy-2-methylvaleric acid in a patient with propionic acidemia. Truscott RJ; Pullin CJ; Halpern B; Hammond J; Haan E; Danks DM Biomed Mass Spectrom; 1979 Jul; 6(7):294-300. PubMed ID: 486715 [TBL] [Abstract][Full Text] [Related]
7. [Neonatal onset of organic acidemia (propionic) diagnosed by tandem mass spectrometry]. Cifuentes Y; De la Hoz I; Bermúdez M; Arteaga C Biomedica; 2008 Mar; 28(1):10-7. PubMed ID: 18645657 [TBL] [Abstract][Full Text] [Related]
8. Increased excretion of four acetyl-CoA precursors during clinical episode of propionic acidaemia. Kuhara T; Shinka T; Matsumoto I; Matsuo M J Inherit Metab Dis; 1982; 5(4):225-6. PubMed ID: 6820445 [TBL] [Abstract][Full Text] [Related]
9. [The neonatal form of propionic acidemia]. Figueras Aloy J; Ribes Rubio A; Vilaseca Busca MA; Lluch Mir M; Brines Godino P; Jiménez González R; Cruz Hernández M An Esp Pediatr; 1988 Dec; 29(6):459-62. PubMed ID: 3245641 [TBL] [Abstract][Full Text] [Related]
11. 1H-NMR studies of urine in propionic acidemia and methylmalonic acidemia. Kodama S; Sugiura M; Nakao H; Kobayashi K; Miyoshi M; Yoshii K; Komatsu M; Sakurai T Acta Paediatr Jpn; 1991 Apr; 33(2):139-45. PubMed ID: 1957637 [TBL] [Abstract][Full Text] [Related]
12. Hyperglycinemia and propionyl coA carboxylase deficiency and episodic severe illness without consistent ketosis. Wadlington WB; Kilroy A; Ando T; Sweetman L; Nyhan WL J Pediatr; 1975 May; 86(5):707-12. PubMed ID: 1133651 [TBL] [Abstract][Full Text] [Related]
13. Propionic acidemia without acidemia: a case report. Ramachandran R; Pietz J J Perinatol; 1995; 15(1):71-3. PubMed ID: 7650559 [TBL] [Abstract][Full Text] [Related]
14. [Propionic acidemia associated with hypertrophic pyloric stenosis and bouts of severe hyperglycemia (author's transl)]. Lehnert W; Junker A; Wehinger H; Zöberlein HG; Baumgartner R; Ropers HH Monatsschr Kinderheilkd; 1980 Nov; 128(11):720-3. PubMed ID: 6110180 [TBL] [Abstract][Full Text] [Related]
15. Comparison of cytosolic and mitochondrial enzyme alterations in the livers of propionic or methylmalonic acidemia: a reduction of cytochrome oxidase activity. Hayasaka K; Metoki K; Satoh T; Narisawa K; Tada K; Kawakami T; Matsuo N; Aoki T Tohoku J Exp Med; 1982 Jul; 137(3):329-34. PubMed ID: 6287671 [TBL] [Abstract][Full Text] [Related]
16. Isotope dilution analysis of methylcitric acid in amniotic fluid for the prenatal diagnosis of propionic and methylmalonic acidemia. Naylor G; Sweetman L; Nyhan WL; Hornbeck C; Griffiths J; Mörch L; Brandänge S Clin Chim Acta; 1980 Nov; 107(3):175-83. PubMed ID: 7002368 [TBL] [Abstract][Full Text] [Related]
17. Studies on the urinary acidic metabolites from three patients with methylmalonic aciduria. Kuhara T; Matsumoto I Biomed Mass Spectrom; 1980 Oct; 7(10):424-8. PubMed ID: 6111361 [TBL] [Abstract][Full Text] [Related]