181 related articles for article (PubMed ID: 6773584)
1. Specificity of galactosylceramidase activation by phosphatidylserine.
Hanada E; Suzuki K
Biochim Biophys Acta; 1980 Aug; 619(2):396-402. PubMed ID: 6773584
[TBL] [Abstract][Full Text] [Related]
2. Hydrolysis of galactosylceramide is catalyzed by two genetically distinct acid beta-galactosidases.
Kobayashi T; Shinnoh N; Goto I; Kuroiwa Y
J Biol Chem; 1985 Dec; 260(28):14982-7. PubMed ID: 3934152
[TBL] [Abstract][Full Text] [Related]
3. Galactosylceramide- and lactosylceramide-loading studies in cultured fibroblasts from normal individuals and patients with globoid cell leukodystrophy (Krabbe's disease) and GM1-gangliosidosis.
Kobayashi T; Shinnoh N; Goto I; Kuroiwa Y; Okawauchi M; Sugihara G; Tanaka M
Biochim Biophys Acta; 1985 Jul; 835(3):456-64. PubMed ID: 3926002
[TBL] [Abstract][Full Text] [Related]
4. Effect of bile salts on lactosylceramide beta-galactosidase activities in human brain, liver and cultured skin fibroblasts.
da Wenger ; Sattler M; Clark C
Biochim Biophys Acta; 1975 Dec; 409(3):297-303. PubMed ID: 812551
[TBL] [Abstract][Full Text] [Related]
5. Lactosylceramidase assays for diagnosis of globoid cell leukodystrophy and GM1-gangliosidosis.
Tanaka H; Suzuki K
Clin Chim Acta; 1977 Mar; 75(2):267-74. PubMed ID: 403037
[TBL] [Abstract][Full Text] [Related]
6. Hydrolysis of lactosylceramide by human galactosylceramidase and GM1-beta-galactosidase in a detergent-free system and its stimulation by sphingolipid activator proteins, sap-B and sap-C. Activator proteins stimulate lactosylceramide hydrolysis.
Zschoche A; Fürst W; Schwarzmann G; Sanhoff K
Eur J Biochem; 1994 May; 222(1):83-90. PubMed ID: 8200356
[TBL] [Abstract][Full Text] [Related]
7. Metabolism of galactosylceramide in the twitcher mouse, an animal model of human globoid cell leukodystrophy.
Kobayashi T; Shinnoh N; Kuroiwa Y
Biochim Biophys Acta; 1986 Nov; 879(2):215-20. PubMed ID: 3094585
[TBL] [Abstract][Full Text] [Related]
8. Lactosylceramide beta-galactosidase in human sphingolipidoses. Evidence for two genetically distinct enzymes.
Tanaka H; Suzuki K
J Biol Chem; 1975 Mar; 250(6):2324-32. PubMed ID: 803971
[TBL] [Abstract][Full Text] [Related]
9. Isoelectric focusing of galactosylceramide beta-galactosylceramide beta-galactosidase in cultured skin fibroblasts of patients with Krabbe's globoid-cell leucodystrophy.
Besley GT
Biochem Soc Trans; 1975; 3(2):241-4. PubMed ID: 1132549
[No Abstract] [Full Text] [Related]
10. Human brain cerebroside beta-galactosidase: deficiency of transgalactosidic activity in Krabbe's disease.
Carter TP; Beblowski DW; Savage MH; Kanfer JN
J Neurochem; 1980 Jan; 34(1):189-96. PubMed ID: 6778958
[TBL] [Abstract][Full Text] [Related]
11. Hydrolysis of galactosylsphingosine and lactosylsphingosine by beta-galactosidases in human brain and cultured fibroblasts.
Goda S; Kobayashi T; Goto I
Biochim Biophys Acta; 1987 Aug; 920(3):259-65. PubMed ID: 3111543
[TBL] [Abstract][Full Text] [Related]
12. Globoid cell leukodystrophy (Krabbe's disease). Metabolic studies with cultured fibroblasts.
Tanaka H; Suzuki K
J Neurol Sci; 1978 Oct; 38(3):409-19. PubMed ID: 731265
[TBL] [Abstract][Full Text] [Related]
13. Activation of human brain galactosylceramidase by phosphatidylserine.
Hanada E; Suzuki K
Biochim Biophys Acta; 1979 Dec; 575(3):410-20. PubMed ID: 42440
[TBL] [Abstract][Full Text] [Related]
14. The specificity of beta-galactosidase in the degradation of gangliosides.
Suzuki K; Tanaka H; Yamanaka T; Van Damme O
Adv Exp Med Biol; 1980; 125():307-18. PubMed ID: 6767344
[TBL] [Abstract][Full Text] [Related]
15. Krabbe's globoid cell leucodystrophy. Studies on galactosylceramide beta-galactosidase and non-specific beta-galactosidase of leucocytes, cultured skin fibroblasts, and amniotic fluid cells.
Besley GT; Bain AD
J Med Genet; 1976 Jun; 13(3):195-9. PubMed ID: 819652
[TBL] [Abstract][Full Text] [Related]
16. Chemical pathology of krabbe's disease. IV. Studies of galactosylceramide and lactosylceramide BETA-galactosidases in brain, white blood cells and aminotic fluid cells.
Svennerholm L; Häkansson G; Vanier MT
Acta Paediatr Scand; 1975 Jul; 64(4):649-56. PubMed ID: 1155085
[TBL] [Abstract][Full Text] [Related]
17. Clinical and biochemical heterogeneity of globoid cell leukodystrophy.
Farrell DF; Swedberg K
Ann Neurol; 1981 Oct; 10(4):364-8. PubMed ID: 7316489
[TBL] [Abstract][Full Text] [Related]
18. A protein activator of galactosylceramide beta-galactosidase.
Wenger DA; Sattler M; Roth S
Biochim Biophys Acta; 1982 Sep; 712(3):639-49. PubMed ID: 7126630
[TBL] [Abstract][Full Text] [Related]
19. Galactocerebrosidase activity in canine globoid leukodystrophy.
Fletcher TF; Suzuki K; Martin FB
Neurology; 1977 Aug; 27(8):758-66. PubMed ID: 560646
[TBL] [Abstract][Full Text] [Related]
20. Lactosylceramidases in canine globoid cell leukodystrophy.
Kurczynski TW; Fletcher TF; Suzuki K
J Neurochem; 1977 Jul; 29(1):37-41. PubMed ID: 886322
[No Abstract] [Full Text] [Related]
[Next] [New Search]