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2. Lactosylceramide beta-galactosidase in human sphingolipidoses. Evidence for two genetically distinct enzymes. Tanaka H; Suzuki K J Biol Chem; 1975 Mar; 250(6):2324-32. PubMed ID: 803971 [TBL] [Abstract][Full Text] [Related]
3. Human brain cerebroside beta-galactosidase: deficiency of transgalactosidic activity in Krabbe's disease. Carter TP; Beblowski DW; Savage MH; Kanfer JN J Neurochem; 1980 Jan; 34(1):189-96. PubMed ID: 6778958 [TBL] [Abstract][Full Text] [Related]
4. The use of natural and artifical substrates in the prenatal diagnosis of Krabbe's disease. Besley GT J Inherit Metab Dis; 1978; 1(3):115-8. PubMed ID: 116080 [TBL] [Abstract][Full Text] [Related]
5. [A study of various properties of beta-galactocerebrosidase from human chorion using synthetic fluorescent substrates]. Petushkova NA; Kozlova IK; Tsvetkova IV; Vidershaĭn GIa Biokhimiia; 1988 Sep; 53(9):1539-45. PubMed ID: 3203114 [TBL] [Abstract][Full Text] [Related]
7. Specificity of galactosylceramidase activation by phosphatidylserine. Hanada E; Suzuki K Biochim Biophys Acta; 1980 Aug; 619(2):396-402. PubMed ID: 6773584 [TBL] [Abstract][Full Text] [Related]
8. Use of a fluorogenic substrate, 6-hexadecanoylamino-4-methylumbelliferyl-beta-D-galactopyranoside, in the diagnosis of Krabbe disease. Grimm U; Zschiesche M; Widerschain G; Seidlitz G; Machill G J Inherit Metab Dis; 1991; 14(6):940-1. PubMed ID: 1779655 [No Abstract] [Full Text] [Related]
9. Characterization of 6-hexadecanoylamino-4-methylumbelliferyl-beta-D- galactopyranoside as fluorogenic substrate of galactocerebrosidase for the diagnosis of Krabbe disease. Wiederschain G; Raghavan S; Kolodny E Clin Chim Acta; 1992 Jan; 205(1-2):87-96. PubMed ID: 1521344 [TBL] [Abstract][Full Text] [Related]
10. Lactosylceramidase assays for diagnosis of globoid cell leukodystrophy and GM1-gangliosidosis. Tanaka H; Suzuki K Clin Chim Acta; 1977 Mar; 75(2):267-74. PubMed ID: 403037 [TBL] [Abstract][Full Text] [Related]
11. [Biochemical diagnosis of globoid cell leukodystrophy (Krabbe's disease)]. Tsvetkova IV; Zolotukhina TV; Rozenfel'd RA Vopr Med Khim; 1985; 31(2):128-30. PubMed ID: 2860752 [TBL] [Abstract][Full Text] [Related]
13. Metabolism of galactosylceramide in the twitcher mouse, an animal model of human globoid cell leukodystrophy. Kobayashi T; Shinnoh N; Kuroiwa Y Biochim Biophys Acta; 1986 Nov; 879(2):215-20. PubMed ID: 3094585 [TBL] [Abstract][Full Text] [Related]
14. A practical chromogenic procedure for the diagnosis of Krabbe's disease. Gal AE; Brady RO; Pentchev PG; Furbish FS; Suzuki K; Tanaka H; Schneider EL Clin Chim Acta; 1977 May; 77(1):53-9. PubMed ID: 17489 [TBL] [Abstract][Full Text] [Related]
15. [Determination of beta-galactosidase activity on nitrocellulose plates using 5-bromo-3-indolyl-beta-D-galactopyranoside and tetrazolium salts]. Markarian AN; Voznyĭ IaV; Dzantiev BB; Egorov AM Bioorg Khim; 1987 Feb; 13(2):263-5. PubMed ID: 3107576 [TBL] [Abstract][Full Text] [Related]
16. Use of mixed dispersion of fluorescent galactosylceramide and sodium dodecylsulfate for assaying galactosylceramide-beta-galactosidase and diagnosing Krabbe disease. Salvayre R; Gatt S Enzyme; 1985; 33(3):175-80. PubMed ID: 4054076 [TBL] [Abstract][Full Text] [Related]
17. Use of leukocytes in diagnosis of Krabbe disease and detection of carriers. Svennerholm L; Vanier MT; Häkansson G; Mänsson JE Clin Chim Acta; 1981 May; 112(3):333-42. PubMed ID: 7237832 [TBL] [Abstract][Full Text] [Related]
18. Globoid cell leukodystrophy: deficiency of lactosyl ceramide beta-galactosidase. Wenger DA; Sattler M; Hiatt W Proc Natl Acad Sci U S A; 1974 Mar; 71(3):854-7. PubMed ID: 4522795 [TBL] [Abstract][Full Text] [Related]
19. [A new fluorogenic substrate for human galactocerebroside-beta-D-galactosidase]. Vidershaĭn GIa; Kozlova IK; Il'ina GS Biokhimiia; 1985 Oct; 50(10):1665-7. PubMed ID: 3935176 [TBL] [Abstract][Full Text] [Related]
20. Additional deficiency of psychosine galactosidase in globoid cell leukodystrophy: an implication to enzyme replacement therapy. Miyatake T; Suzuki K Birth Defects Orig Artic Ser; 1973 Mar; 9(2):136-40. PubMed ID: 4611526 [No Abstract] [Full Text] [Related] [Next] [New Search]