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22. HPRTSardinia: a new point mutation causing HPRT deficiency without Lesch-Nyhan disease. Cossu A; Orrù S; Jacomelli G; Carcassi C; Contu L; Sestini S; Corradi MR; Pompucci G; Carcassi A; Micheli V Biochim Biophys Acta; 2006 Jan; 1762(1):29-33. PubMed ID: 16216473 [TBL] [Abstract][Full Text] [Related]
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30. Production of a model for Lesch-Nyhan syndrome in hypoxanthine phosphoribosyltransferase-deficient mice. Wu CL; Melton DW Nat Genet; 1993 Mar; 3(3):235-40. PubMed ID: 8485579 [TBL] [Abstract][Full Text] [Related]
31. Hypoxanthine-guanine phosphoribosyltransferase: characteristics of the mutant enzyme in erythrocytes from patients with the Lesch-Nyhan syndrome. Arnold WJ; Meade JC; Kelley WN J Clin Invest; 1972 Jul; 51(7):1805-12. PubMed ID: 4624352 [TBL] [Abstract][Full Text] [Related]
33. Molecular analysis of the mutations in five unrelated patients with the Lesch Nyhan syndrome. Marcus S; Christensen E; Malm G Hum Mutat; 1993; 2(6):473-7. PubMed ID: 8111415 [TBL] [Abstract][Full Text] [Related]
34. Hypoxanthine-guanine phosphoribosyltransferase in human lymphoblastoid cells: confirmation of four structural variants and demonstration of a new variant (HPRT Ann Arbor). Wilson JM; Baugher BW; Kelley WN Adv Exp Med Biol; 1984; 165 Pt B():33-8. PubMed ID: 6720433 [No Abstract] [Full Text] [Related]
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37. Functional analysis of brain dopamine systems in a genetic mouse model of Lesch-Nyhan syndrome. Jinnah HA; Langlais PJ; Friedmann T J Pharmacol Exp Ther; 1992 Nov; 263(2):596-607. PubMed ID: 1432691 [TBL] [Abstract][Full Text] [Related]
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