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3. Adenine phosphoribosyl transferase deficiency in association with sub-normal hypoxanthine phophoribosyl transferase in families of Lesch--Nyhan patients. Itiaba K; Melançon SB; Dallaire L; Crawhall JC Biochem Med; 1978 Apr; 19(2):252-9. PubMed ID: 656085 [No Abstract] [Full Text] [Related]
4. HGPRT-positive and HGPRT-negative erythrocytes in heterozygotes for HGPRT deficiency. Emmerson BT; Johnson LA; Gordon RB Adv Exp Med Biol; 1977; 76A():359-60. PubMed ID: 558715 [No Abstract] [Full Text] [Related]
5. Lesch-Nyhan syndrome: biochemical characterization of a case with attenuated behavioral manifestation. Fattal A; Spirer Z; Zoref-Shani E; Sperling O Enzyme; 1984; 31(1):55-60. PubMed ID: 6201351 [TBL] [Abstract][Full Text] [Related]
6. Prenatal diagnosis of Lesch-Nyhan syndrome and some characteristics of hypoxanthine-guanine phosphoribosyltransferase and adenine phosphoribosyltransferase in human tissues and cultivated cells. Shin-Buehring YS; Osang M; Wirtz A; Haas B; Rahm P; Schaub J Pediatr Res; 1980 Jun; 14(6):825-9. PubMed ID: 7402756 [TBL] [Abstract][Full Text] [Related]
7. Hypoxanthine-guanine phosphoribosyltransferase activity in individual erythrocytes: autoradiographic studies in heterozygotes. Emmerson BT; Gordon RB; Johnson LA Ciba Found Symp; 1977; (48):97-104. PubMed ID: 245995 [TBL] [Abstract][Full Text] [Related]
12. [A new form of the Lesch-Nyhan syndrome. A study of hypoxanthine-guanine-phosphoribosyl-transferase in fibroblasts. The in vitro and in vivo effect of adenine on enzyme activity]. Warter S; Bieth R Ann Biol Clin (Paris); 1982; 40(5):561-6. PubMed ID: 6186166 [TBL] [Abstract][Full Text] [Related]
13. HGPRT structural gene mutation in Lesch-Nyhan-syndrome as indicated by antigenic activity and reversion of the enzyme deficiency. Strauss M; Lübbe L; Geissler E Hum Genet; 1981; 57(2):185-8. PubMed ID: 7228031 [TBL] [Abstract][Full Text] [Related]
14. Two populations of heterozygote erythrocytes in moderate hypoxanthine guanine phosphoribosyltransferase deficiency. Johnson LA; Gordon RB; Emmerson BT Nature; 1976 Nov; 264(5582):172-4. PubMed ID: 995201 [No Abstract] [Full Text] [Related]
15. [Lesch-Nyhan syndrome: a new variant with hypoxanthine-guanine phosphoriboxyl transferase activity higher than the classical disease and detection of the heterozygote trait in the erythrocytes of the carrier]. Hernández Nieto L; Nyhan WL; Page T; Cubillo Ferreira G; Rodríguez Fernández M; González García T; Cabrera de León A; Santolaria Fernández FJ Med Clin (Barc); 1985 Jan; 84(2):68-71. PubMed ID: 3974350 [No Abstract] [Full Text] [Related]
16. Hypoxanthine-guanine phosphoribosyltransferase gene analysis for Japanese patients with Lesch-Nyhan syndrome. Shimizu N; Konomi H; Arima M; Aoki T Acta Paediatr Jpn; 1996 Feb; 38(1):36-40. PubMed ID: 8992857 [TBL] [Abstract][Full Text] [Related]
17. Clinical and biochemical observations on three cases of hypoxanthine-guanine phosphoribosyltransferase deficiency. Bunn DN; Moss IK; Nicholls A; Scott JT; Snaith ML; Watson MR Ann Rheum Dis; 1975 Jun; 34(3):249-55. PubMed ID: 1155984 [TBL] [Abstract][Full Text] [Related]
18. [Clinical spectrum of hypoxanthine-guanine phosphoribosyltransferase deficiency: study of 12 cases]. García Puig J; Mateos FA; Jiménez ML; Arcas J; Miranda ME; Oríz Vázquez J Med Clin (Barc); 1994 May; 102(18):681-7. PubMed ID: 8028417 [TBL] [Abstract][Full Text] [Related]
19. Novel mutation in the human HPRT1 gene and the Lesch-Nyhan disease. Nguyen KV; Naviaux RK; Nyhan WL Nucleosides Nucleotides Nucleic Acids; 2017 Nov; 36(11):704-711. PubMed ID: 29185864 [TBL] [Abstract][Full Text] [Related]